Q28.8
BillableOth congenital malformations of circulatory system
Other specified congenital malformations of circulatory system
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Congenital aneurysm, specified site NEC
- Spinal vessel anomaly
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(5)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(218)
SNOMED CT
- Absent pulmonary valve6996004
- Congenital absence of pulmonary valve6996004
- Congenital absence of pulmonic valve6996004
- Venous anomaly of umbilical cord29057008
- Heart disease in mother complicating pregnancy, childbirth AND/OR puerperium78381004
- Fallot's tetralogy86299006
- Subpulmonic stenosis, ventricular septal defect, overriding aorta, AND right ventricular hypertrophy86299006
- TOF - Tetralogy of Fallot86299006
- Tetralogy of Fallot86299006
- Absent ductus arteriosus92965002
- Congenital absence of ductus arteriosus92965002
- Hypoplasia of spinal vessel204490005
- Venous-lymphatic malformation234134007
- Ductus venosus abnormality253329001
- Venous duct abnormality253329001
- Patent ductus venosus253330006
- Closed ductus venosus253331005
- Congenital cardiovascular disorders during pregnancy, childbirth and the puerperium267207004
- Venous remnant280143008
- Congenital anomaly of cardiovascular structure of trunk363028003
- Congenital anomaly of lymphatic structure of trunk363031002
- Absent ductus venosus448635000
- Absent venous duct448635000
- Absent ductus venosus with direct connection of umbilical vein to right atrium449439007
- Absent venous duct with direct connection of umbilical vein to right atrium449439007
- Absent ductus venosus with direct connection of umbilical vein to renal vein449486006
- Absent venous duct with direct connection of umbilical vein to renal vein449486006
- Absent ductus venosus with direct connection of umbilical vein to inferior vena cava449527001
- Absent venous duct with direct connection of umbilical vein to inferior caval vein449527001
- Dural arteriovenous fistula of spinal cord449903008
- Type I arteriovenous malformation of spinal cord449903008
- Type I spinal dural AV fistula449903008
- Type I spinal dural arteriovenous fistula449903008
- Intramedullary glomus arteriovenous malformation of spinal cord449904002
- Type II arteriovenous malformation of spinal cord449904002
- Intramedullary and extramedullary arteriovenous malformation of spinal cord449905001
- Juvenile arteriovenous malformation of spinal cord449905001
- Type III arteriovenous malformation of spinal cord449905001
- Perimedullary arteriovenous fistula of spinal cord449906000
- Type IV arteriovenous malformation of spinal cord449906000
- Abnormality of arterial ligament460952008
- Abnormality of ligamentum arteriosum460952008
- Abnormal insertion of arterial ligament460953003
- Anomalous insertion of arterial ligament460953003
- Anomalous insertion of ligamentum arteriosum460953003
- Anomalous insertion of arterial ligament into distal left pulmonary artery460954009
- Anomalous insertion of ligamentum arteriosum into distal left pulmonary artery460954009
- Anomalous insertion of arterial ligament into pulmonary trunk460955005
- Anomalous insertion of ligamentum arteriosum into pulmonary trunk460955005
- Anomalous insertion of arterial ligament into right pulmonary artery460956006
- Anomalous insertion of ligamentum arteriosum into right pulmonary artery460956006
- Abnormal origin of arterial ligament460957002
- Anomalous origin of arterial ligament460957002
- Anomalous origin of ligamentum arteriosum460957002
- Anomalous origin of arterial ligament from aortic arch460958007
- Anomalous origin of ligamentum arteriosum from aortic arch460958007
- Anomalous origin of arterial ligament from ascending aorta460959004
- Anomalous origin of ligamentum arteriosum from ascending aorta460959004
- Anomalous origin of arterial ligament from distal descending aorta460960009
- Anomalous origin of ligamentum arteriosum from distal descending aorta460960009
- Anomalous origin of arterial ligament from right brachiocephalic artery460961008
- Anomalous origin of ligamentum arteriosum from right brachiocephalic artery460961008
- Anomalous origin of arterial ligament from left brachiocephalic artery460962001
- Anomalous origin of ligamentum arteriosum from left brachiocephalic artery460962001
- Anomalous origin of arterial ligament from right subclavian artery460963006
- Anomalous origin of ligamentum arteriosum from right subclavian artery460963006
- Anomalous origin of arterial ligament from left subclavian artery460964000
- Anomalous origin of ligamentum arteriosum from left subclavian artery460964000
- Anomalous origin of arterial ligament from right carotid artery460965004
- Anomalous origin of ligamentum arteriosum from right carotid artery460965004
- Anomalous origin of arterial ligament from left carotid artery460966003
- Anomalous origin of ligamentum arteriosum from left carotid artery460966003
- Right arterial ligament460967007
- Right ligamentum arteriosum460967007
- Anomalous origin of right arterial ligament from right aortic arch460968002
- Anomalous origin of right ligamentum arteriosum from right aortic arch460968002
- Anomalous origin of right arterial ligament from left aortic arch460969005
- Anomalous origin of right ligamentum arteriosum from left aortic arch460969005
- Cardiovascular abnormality due to anomalous origin of coronary artery from pulmonary artery461088006
- Cardiovascular abnormality due to bilateral arterial ducts461098000
- Cardiovascular abnormality due to bilateral ductus arteriosus461098000
- Cardiovascular abnormality due to anomalous origin of arterial duct461100000
- Cardiovascular abnormality due to anomalous origin of ductus arteriosus461100000
- Cardiovascular abnormality due to anomalous origin of coronary artery orifice461338005
- Cardiovascular abnormality due to anomalous origin of coronary artery ostium461338005
- Anomalous origin of arterial ligament from right aortic arch461399000
- Anomalous origin of ligamentum arteriosum from right aortic arch461399000
- Anomalous origin of arterial ligament from aortic diverticulum461400007
- Anomalous origin of ligamentum arteriosum from aortic diverticulum461400007
- Anomalous origin of arterial ligament from unknown site461401006
- Anomalous origin of ligamentum arteriosum from unknown site461401006
- Congenital atresia of aortic arch461557000
- Atresia of aortic arch with fibrous cord461562004
- Atresia of aortic arch with fibrous cord between subclavian artery and common carotid artery461572001
- Type B atresia of aortic arch with fibrous cord between subclavian artery and common carotid artery461572001
- Atresia of aortic arch with fibrous cord between left common carotid artery and right common carotid artery461577007
- Type C atresia of aortic arch with fibrous cord between left common carotid artery and right common carotid artery461577007
- Anomalous origin of arterial ligament from retroesophageal aortic diverticulum473005004
- Anomalous origin of ligamentum arteriosum from retroesophageal aortic diverticulum473005004
- Dural arteriovenous fistula703166003
- Congenital anomaly of great vessel762250009
- Absence of pulmonary valve, Fallot tetralogy, absence of ductus arteriosus syndrome766976003
- Pulmonary valve agenesis, tetralogy of Fallot, absence of ductus arteriosus syndrome766976003
- Agenesis of artery789097007
UMLS
Clinical Terms
- Type C atresia of aortic arch with fibrous cord between left common carotid artery and right common carotid artery
- Congenital absence of ductus arteriosus
- Anomalous origin of arterial ligament
- Type I arteriovenous malformation of spinal cord
- Anomalous origin of arterial ligament from aortic arch
- Anomalous origin of ligamentum arteriosum
- Hypoplasia of spinal vessel
- Abnormality of ligamentum arteriosum
- Agenesis of artery
- Absent ductus venosus
- Anomalous origin of arterial ligament from retroesophageal aortic diverticulum
- Anomalous insertion of ligamentum arteriosum into distal left pulmonary artery
- Anomalous origin of ligamentum arteriosum from distal descending aorta
- Cardiovascular abnormality due to bilateral ductus arteriosus
- Anomalous insertion of arterial ligament into distal left pulmonary artery
- Anomalous origin of right ligamentum arteriosum from right aortic arch
- Anomalous origin of ligamentum arteriosum from left carotid artery
- Absent ductus venosus with direct connection of umbilical vein to right atrium
- Anomalous origin of ligamentum arteriosum from ascending aorta
- Type III arteriovenous malformation of spinal cord
- Absent ductus arteriosus
- Type IV arteriovenous malformation of spinal cord
- Anomalous insertion of arterial ligament into right pulmonary artery
- Type B atresia of aortic arch with fibrous cord between subclavian artery and common carotid artery
- Atresia of aortic arch with fibrous cord between left common carotid artery and right common carotid artery
- Congenital cardiovascular disorders during pregnancy, childbirth and the puerperium
- Abnormal insertion of arterial ligament
- Venous anomaly of umbilical cord
- Dural arteriovenous fistula
- Anomalous origin of arterial ligament from unknown site
- Cardiovascular abnormality due to anomalous origin of coronary artery orifice
- Anomalous origin of arterial ligament from right subclavian artery
- Anomalous origin of ligamentum arteriosum from retroesophageal aortic diverticulum
- Anomalous origin of ligamentum arteriosum from right brachiocephalic artery
- Patent ductus venosus
- Subpulmonic stenosis, ventricular septal defect, overriding aorta, AND right ventricular hypertrophy
- Anomalous origin of ligamentum arteriosum from left brachiocephalic artery
- Absent ductus venosus with direct connection of umbilical vein to inferior vena cava
- Intramedullary and extramedullary arteriovenous malformation of spinal cord
- Type I spinal dural arteriovenous fistula
- Abnormal origin of arterial ligament
- Venous duct abnormality
- Congenital anomaly of great vessel
- Intramedullary glomus arteriovenous malformation of spinal cord
- Spinal vessel congenital anomaly
- Congenital absence of pulmonary valve
- Absent ductus venosus with direct connection of umbilical vein to renal vein
- Perimedullary arteriovenous fistula of spinal cord
- Absent venous duct
- Absence of pulmonary valve, Fallot tetralogy, absence of ductus arteriosus syndrome
- Anomalous origin of ligamentum arteriosum from right carotid artery
- Congenital anomaly of cardiovascular structure of trunk
- Anomalous insertion of arterial ligament
- Congenital aneurysm, specified site NEC
- Right ligamentum arteriosum
- Anomalous insertion of arterial ligament into pulmonary trunk
- Anomalous insertion of ligamentum arteriosum
- Cardiovascular abnormality due to anomalous origin of ductus arteriosus
- Anomalous insertion of ligamentum arteriosum into right pulmonary artery
- Anomalous origin of ligamentum arteriosum from aortic diverticulum
- Anomalous origin of arterial ligament from distal descending aorta
- Ductus venosus abnormality
- Venous-lymphatic malformation
- Right arterial ligament
- Tetralogy of Fallot
- Anomalous origin of ligamentum arteriosum from aortic arch
- Type I spinal dural AV fistula
- Cardiovascular abnormality due to anomalous origin of arterial duct
- Anomalous origin of arterial ligament from right carotid artery
- TOF - Tetralogy of Fallot
- Cardiovascular abnormality due to anomalous origin of coronary artery from pulmonary artery
- Cardiovascular abnormality due to bilateral arterial ducts
- Absent venous duct with direct connection of umbilical vein to right atrium
- Spinal vessel anomaly
- Fallot's tetralogy
- Dural arteriovenous fistula of spinal cord
- Anomalous origin of ligamentum arteriosum from right subclavian artery
- Atresia of aortic arch with fibrous cord between subclavian artery and common carotid artery
- Anomalous origin of arterial ligament from aortic diverticulum
- Anomalous origin of right arterial ligament from right aortic arch
- Absent pulmonary valve
- Anomalous origin of ligamentum arteriosum from left subclavian artery
- Anomalous origin of arterial ligament from left subclavian artery
- Anomalous origin of ligamentum arteriosum from right aortic arch
- Anomalous insertion of ligamentum arteriosum into pulmonary trunk
- Type II arteriovenous malformation of spinal cord
- Absent venous duct with direct connection of umbilical vein to inferior caval vein
- Congenital anomaly of lymphatic structure of trunk
- Abnormality of arterial ligament
- Anomalous origin of arterial ligament from left carotid artery
- Atresia of aortic arch with fibrous cord
- Congenital atresia of aortic arch
- Anomalous origin of arterial ligament from left brachiocephalic artery
- Heart disease in mother complicating pregnancy, childbirth AND/OR puerperium
- Congenital spinal vessel anomaly NOS
- Absent venous duct with direct connection of umbilical vein to renal vein
- Juvenile arteriovenous malformation of spinal cord
- Pulmonary valve agenesis, tetralogy of Fallot, absence of ductus arteriosus syndrome
- Anomalous origin of arterial ligament from right aortic arch
- Anomalous origin of right ligamentum arteriosum from left aortic arch
- Closed ductus venosus
- Venous remnant
- Anomalous origin of ligamentum arteriosum from unknown site
- Anomalous origin of arterial ligament from ascending aorta
- Cardiovascular abnormality due to anomalous origin of coronary artery ostium
- Anomalous origin of arterial ligament from right brachiocephalic artery
- Congenital absence of pulmonic valve
- Anomalous origin of right arterial ligament from left aortic arch
Frequently Asked Questions
What is the ICD-10 code for oth congenital malformations of circulatory system?
The ICD-10-CM code for oth congenital malformations of circulatory system is Q28.8. The full clinical description is "Other specified congenital malformations of circulatory system". Q28.8 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q28.8 mean?
ICD-10-CM code Q28.8 represents “Other specified congenital malformations of circulatory system”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q28.8 a billable code?
Yes, Q28.8 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q28.8 in?
Q28.8 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q28.8?
Q28.8 has Excludes1 notes indicating codes that cannot be used together with it, including: congenital aneurysm NOS (Q27.8); congenital coronary aneurysm (Q24.5); ruptured cerebral arteriovenous malformation (I60.8); and 1 more.
What SNOMED CT codes does Q28.8 map to?
Q28.8 maps to 56 SNOMED CT concepts: 460953003, 460957002, 460952008, 766976003, 92965002, and 51 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q28.8?
Q28.8 is linked to 3 UMLS Concept Unique Identifiers: C2910159, C0375522, C0478008. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q28.8 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like oth congenital malformations of circulatory system affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q28.8?
Q28.8 maps to the ICD-11 code: LA9Z (Structural developmental anomalies of the circulatory system, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.