Q27.9
BillableCongenital malformation of peripheral vascular system, unsp
Congenital malformation of peripheral vascular system, unspecified
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Anomaly of artery or vein NOS
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(6)
Q27.0Congenital absence and hypoplasia of umbilical artery
Q27.1Congenital renal artery stenosis
Q27.2Other congenital malformations of renal artery
Q27.3Arteriovenous malformation (peripheral)
Q27.4Congenital phlebectasia
Q27.8Oth congenital malformations of peripheral vascular system
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(214)
SNOMED CT
- Venous anomaly of umbilical cord29057008
- Vascular anomaly of umbilical cord31481000
- Arterial anomaly of umbilical cord62023000
- Abnormal umbilical cord90009001
- Short cord156222001
- Short umbilical cord156222001
- Capillary fragility - hereditary191329002
- Hereditary vascular fragility191329002
- Capillary malformation234118009
- Congenital anomaly of capillary234118009
- Arterial malformation234119001
- Congenital abnormality of artery234119001
- Congenital anomaly of artery234119001
- Congenital arterial malformation234119001
- Venous malformation234124003
- Congenital anomaly of valve of vein234125002
- Venous valvular anomaly234125002
- Capillary-venous malformation234133001
- Venous-lymphatic malformation234134007
- Capillary-venous-lymphatic malformation234136009
- Dysplasia of lung253745002
- Congenital vascular hamartoma254206003
- Congenital vascular naevus254206003
- Congenital vascular nevus254206003
- Blue rubber bleb naevus254784002
- Blue rubber bleb naevus syndrome254784002
- Blue rubber bleb nevus254784002
- Blue rubber bleb nevus syndrome254784002
- Vascular disorder of inner ear277493007
- Vascular malformation of inner ear277495000
- Venous remnant280143008
- Congenital abnormality of vein297222002
- Congenital anomaly of vein297222002
- Combined vascular malformation400017009
- Mixed vascular malformation400017009
- Congenital vascular malformation of skin400042000
- Cutaneous vascular malformation400042000
- Congenital vascular anomaly400159008
- Congenital vascular malformation400159008
- VM - Vascular malformation400159008
- Vascular malformation400159008
- Four vessels in umbilical cord417426005
- Congenital anomaly of peripheral blood vessel430166008
- Peripheral vascular congenital anomaly430166008
- Congenital anomaly of blood vessel of upper limb432293006
- Congenital vascular anomaly of upper limb432293006
- Congenital abnormality of systemic vein448065006
- Congenital anomaly of blood vessel of extremity449870006
- Congenital anomaly of blood vessel of limb449870006
- Congenital anomaly of blood vessel of lower limb449871005
- Congenital abnormality of systemic artery461440001
- PHACE syndrome698765007
- Pascual Castroviejo syndrome type 2698765007
- Posterior fossa brain malformation, haemangioma, arterial anomaly, cardiac defect and aortic coarctation, and eye abnormality syndrome698765007
- Posterior fossa brain malformation, hemangioma, arterial anomaly, cardiac defect and aortic coarctation, and eye abnormality syndrome698765007
- Peripheral venous malformation703198009
- Infantile haemangioma of rare localisation703270004
- Infantile hemangioma of rare localization703270004
- Diffuse lymphatic malformation703298001
- Cutaneous capillary malformation703299009
- Cutaneous capillary vascular malformation703299009
- Microcephaly-capillary malformation syndrome703369003
- Capillary malformation-arteriovenous malformation syndrome703533007
- CLOVE syndrome719475006
- CLOVES syndrome719475006
- Congenital lipomatous overgrowth, vascular malformation, epidermal naevi, skeletal anomaly syndrome719475006
- Congenital lipomatous overgrowth, vascular malformation, epidermal nevi, skeletal anomaly syndrome719475006
- Angio-osteohypertrophic syndrome723991007
- Angioosteohypertrophic syndrome723991007
- Congenital venous malformation of skin724842007
- Intraosseous haemangioma764100007
- Intraosseous hemangioma764100007
- Osseous venous malformation764100007
- Primary intraosseous venous malformation764100007
- Angio-osteohypotrophic syndrome765750001
- Angioosteohypotrophic syndrome765750001
- Phlebectatic osteohypoplastic angiodysplasia765750001
- Servelle Martorell syndrome765750001
- Congenital dysplasia of left lobe of lung co-occurrent with congenital vascular malformation767029004
- Congenital dysplasia of right lobe of lung co-occurrent with congenital vascular malformation767030009
- Agenesis of artery789097007
- DCMO - diffuse capillary malformation with overgrowth1293116008
- Diffuse capillary malformation with overgrowth1293116008
- Infantile haemangioma1293125002
- Infantile hemangioma1293125002
- Posterior cord syndrome due to vascular malformation1343512002
- Bilateral congenital anomaly of blood vessels of lower limbs15973261000119108
- Congenital anomaly of blood vessels of bilateral lower extremities15973261000119108
- Congenital anomaly of blood vessels of bilateral lower limbs15973261000119108
- Congenital anomaly of blood vessels of both lower limbs15973261000119108
- Bilateral congenital anomaly of blood vessels of upper limbs16007671000119109
- Congenital anomaly of blood vessels of bilateral upper extremities16007671000119109
- Congenital anomaly of blood vessels of bilateral upper limbs16007671000119109
- Congenital anomaly of blood vessels of both upper limbs16007671000119109
- Congenital anomaly of blood vessel of left lower extremity15973181000119106
- Congenital anomaly of blood vessel of left lower limb15973181000119106
- Congenital anomaly of blood vessel of left upper extremity16007591000119106
- Congenital anomaly of blood vessel of left upper limb16007591000119106
- Congenital anomaly of blood vessel of right lower extremity15973221000119103
- Congenital anomaly of blood vessel of right lower limb15973221000119103
- Congenital anomaly of blood vessel of right upper extremity16007631000119106
- Congenital anomaly of blood vessel of right upper limb16007631000119106
- Congenital anomaly of gastrointestinal vessel32201000119107
UMLS
Clinical Terms
- Posterior fossa brain malformation, haemangioma, arterial anomaly, cardiac defect and aortic coarctation, and eye abnormality syndrome
- Congenital anomaly of blood vessel of left lower limb
- Four vessels in umbilical cord
- Capillary-venous-lymphatic malformation
- Short umbilical cord
- Angioosteohypertrophic syndrome
- CLOVES syndrome
- Congenital anomaly of blood vessels of both lower limbs
- Intraosseous haemangioma
- Agenesis of artery
- Congenital anomaly of artery
- Congenital anomaly of blood vessel of right lower extremity
- Congenital vascular hamartoma
- Capillary fragility - hereditary
- Intraosseous hemangioma
- Infantile hemangioma of rare localization
- Combined vascular malformation
- Congenital lipomatous overgrowth, vascular malformation, epidermal naevi, skeletal anomaly syndrome
- Congenital vascular malformation of skin
- Congenital venous malformation of skin
- Congenital abnormality of systemic vein
- Congenital lipomatous overgrowth, vascular malformation, epidermal nevi, skeletal anomaly syndrome
- Congenital vascular nevus
- Congenital anomaly of blood vessels of bilateral upper extremities
- Congenital anomaly of peripheral blood vessel
- Servelle Martorell syndrome
- Angio-osteohypotrophic syndrome
- Arterial malformation
- Capillary-venous malformation
- Blue rubber bleb nevus syndrome
- Congenital dysplasia of right lobe of lung co-occurrent with congenital vascular malformation
- Peripheral venous malformation
- Venous valvular anomaly
- Osseous venous malformation
- Congenital anomaly of gastrointestinal vessel
- Venous malformation
- Capillary malformation-arteriovenous malformation syndrome
- Congenital anomaly of blood vessel of limb
- Congenital anomaly of blood vessel of right upper extremity
- Congenital anomaly of blood vessel of right lower limb
- Congenital abnormality of artery
- Pascual Castroviejo syndrome type 2
- Vascular malformation peripheral
- Venous anomaly of umbilical cord
- Congenital anomaly of capillary
- Bilateral congenital anomaly of blood vessels of lower limbs
- CLOVE syndrome
- Diffuse lymphatic malformation
- Blue rubber bleb naevus syndrome
- Peripheral vascular congenital anomaly
- Congenital anomaly of blood vessels of bilateral upper limbs
- Congenital arterial malformation
- Posterior cord syndrome due to vascular malformation
- Anomaly of artery or vein NOS
- Congenital anomaly of blood vessel of left upper limb
- Diffuse capillary malformation with overgrowth
- Congenital anomaly of blood vessel of right upper limb
- Congenital anomaly of blood vessels of both upper limbs
- Vascular disorder of inner ear
- Congenital anomaly of blood vessel of left lower extremity
- Congenital abnormality of systemic artery
- Congenital dysplasia of left lobe of lung co-occurrent with congenital vascular malformation
- Congenital abnormality of vein
- Blue rubber bleb nevus
- Arterial anomaly of umbilical cord
- Cutaneous capillary vascular malformation
- PHACE syndrome
- Posterior fossa brain malformation, hemangioma, arterial anomaly, cardiac defect and aortic coarctation, and eye abnormality syndrome
- Congenital vascular anomaly
- Congenital vascular malformation
- Abnormal umbilical cord
- Congenital anomaly of blood vessels of bilateral lower limbs
- Congenital vascular naevus
- Venous-lymphatic malformation
- Congenital anomaly of valve of vein
- Angio-osteohypertrophic syndrome
- Vascular malformation of inner ear
- Phlebectatic osteohypoplastic angiodysplasia
- Infantile haemangioma of rare localisation
- Vascular anomaly of umbilical cord
- Capillary malformation
- Primary intraosseous venous malformation
- Vascular malformation
- Cutaneous vascular malformation
- Congenital anomaly of the peripheral vascular system, unspecified site
- Congenital vascular anomaly of upper limb
- Bilateral congenital anomaly of blood vessels of upper limbs
- Congenital anomaly of blood vessel of left upper extremity
- Hereditary vascular fragility
- DCMO - diffuse capillary malformation with overgrowth
- Infantile hemangioma
- Congenital anomaly of blood vessel of upper limb
- Dysplasia of lung
- Congenital anomaly of vein
- Infantile haemangioma
- VM - Vascular malformation
- Congenital anomaly of blood vessels of bilateral lower extremities
- Cutaneous capillary malformation
- Mixed vascular malformation
- Venous remnant
- Short cord
- Congenital anomaly of blood vessel of extremity
- Microcephaly-capillary malformation syndrome
- Blue rubber bleb naevus
- Congenital anomaly of blood vessel of lower limb
- Angioosteohypotrophic syndrome
Frequently Asked Questions
What is the ICD-10 code for congenital malformation of peripheral vascular system, unsp?
The ICD-10-CM code for congenital malformation of peripheral vascular system, unsp is Q27.9. The full clinical description is "Congenital malformation of peripheral vascular system, unspecified". Q27.9 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q27.9 mean?
ICD-10-CM code Q27.9 represents “Congenital malformation of peripheral vascular system, unspecified”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q27.9 a billable code?
Yes, Q27.9 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q27.9 in?
Q27.9 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What SNOMED CT codes does Q27.9 map to?
Q27.9 maps to 55 SNOMED CT concepts: 90009001, 789097007, 723991007, 765750001, 62023000, and 50 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q27.9?
Q27.9 is linked to 2 UMLS Concept Unique Identifiers: C2910152, C0340797. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q27.9 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital malformation of peripheral vascular system, unsp affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q27.9?
Q27.9 maps to the ICD-11 code: LA90.Z (Structural developmental anomalies of the peripheral vascular system, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.