Q20.4
BillableDouble inlet ventricle
Double inlet ventricle
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Common ventricle
- Cor triloculare biatriatum
- Single ventricle
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(8)
Q20.0Common arterial trunk
Q20.1Double outlet right ventricle
Q20.2Double outlet left ventricle
Q20.3Discordant ventriculoarterial connection
Q20.5Discordant atrioventricular connection
Q20.6Isomerism of atrial appendages
Q20.8Oth congenital malform of cardiac chambers and connections
Q20.9Congenital malform of cardiac chambers and connections, unsp
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(219)
SNOMED CT
- Absence of interventricular septum45503006
- Common ventricle45503006
- Cor triloculare biatriatum45503006
- Single ventricle45503006
- Congenital absence of papillary muscle92974000
- Single right ventricle109425008
- Single left ventricle109426009
- Congenital cleft of cardiac valve123658006
- DIV - Double inlet ventricle253281003
- Double inlet ventricle253281003
- DIRV - Double inlet right ventricle253282005
- Double inlet right ventricle253282005
- DILV - Double inlet left ventricle253283000
- Double inlet left ventricle253283000
- DIIV - Double inlet indeterminate ventricle253284006
- Double inlet to ventricle of indeterminate morphology253284006
- Straddling tricuspid valve253379003
- Abnormality of right atrioventricular valve in double inlet ventricle253454000
- DIV - Abnormality of right atrioventricular valve in double inlet ventricle253454000
- Mucoid thickening of right atrioventricular valve253457007
- Right atrioventricular valve dysplasia253457007
- Right atrioventricular valve hypoplasia253458002
- Overriding right atrioventricular valve253460000
- Right atrioventricular valve stenosis253462008
- Straddling right atrioventricular valve253463003
- Absent right atrioventricular valve leaflets253465005
- Unguarded right atrioventricular valve orifice253465005
- Double orifice of right atrioventricular valve253467002
- Abnormality of right atrioventricular valve chordae tendinae253473001
- Abnormality of right atrioventricular valve chords253473001
- CT - Abnormality of right atrioventricular chordae tendinae253473001
- Abnormality of right atrioventricular valve papillary muscle253478005
- Congenital abnormality of right atrioventricular valve papillary muscle253478005
- Congenital parachute malformation of right atrioventricular valve253479002
- Parachute malformation of right atrioventricular valve253479002
- Abnormality of left atrioventricular valve in double inlet ventricle253483002
- DIV - Abnormality of left atrioventricular valve in double inlet ventricle253483002
- Imperforate left atrioventricular valve253484008
- Left atrioventricular valve atresia253484008
- Left atrioventricular valve dysplasia253486005
- Mucoid thickening of left atrioventricular valve253486005
- Left atrioventricular valve hypoplasia253487001
- Overriding left atrioventricular valve253489003
- Left atrioventricular valve stenosis253491006
- Straddling left atrioventricular valve253492004
- Left atrioventricular valve leaflet abnormality253493009
- Absent left atrioventricular valve leaflets253494003
- Unguarded left atrioventricular valve orifice253494003
- Double orifice of left atrioventricular valve253495002
- Ebstein anomaly of left atrioventricular valve253496001
- Ebstein's anomaly of left atrioventricular valve253496001
- Left atrioventricular valve prolapse253497005
- True cleft of left atrioventricular valve leaflet253498000
- Accessory tissue on left atrioventricular valve leaflet253499008
- Left atrioventricular valve leaflet dysplasia253500004
- Mucoid thickening of left atrioventricular valve leaflet253500004
- Abnormality of left atrioventricular valve chordae tendinae253501000
- Abnormality of left atrioventricular valve chords253501000
- CT - Abnormality of left atrioventricular chordae tendinae253501000
- Left atrioventricular valve chordae too short253502007
- Left atrioventricular valve chordae too long253503002
- Left atrioventricular valve chordae to outlet septum253504008
- Arcade abnormality of left atrioventricular valve chordae253505009
- Abnormality of left atrioventricular valve papillary muscle253506005
- Congenital abnormality of left atrioventricular valve papillary muscle253506005
- Congenital parachute malformation of left atrioventricular valve253507001
- Parachute malformation of left atrioventricular valve253507001
- Absent left atrioventricular valve papillary muscle253508006
- Congenital absence of left atrioventricular valve papillary muscle253508006
- Congenital fusion of left atrioventricular valve papillary muscles253509003
- Fused left atrioventricular valve papillary muscles253509003
- Congenital hypoplastic left atrioventricular valve papillary muscle253510008
- Hypoplastic left atrioventricular valve papillary muscle253510008
- Functional single ventricle443379009
- Common atrioventricular orifice in double inlet ventricle445294008
- Right atrioventricular valvar leaflets absent in double inlet ventricle (unguarded orifice)445330003
- Right atrioventricular valve leaflets absent in double inlet ventricle (unguarded orifice)445330003
- Two atrioventricular valves in double inlet ventricle446667008
- Functionally univentricular heart446916007
- Solitary ventricle of indeterminate morphology447283008
- Congenital abnormality of left atrioventricular valve in double inlet ventricle448947009
- Congenital abnormality of right atrioventricular valve leaflet in double inlet ventricle449031001
- Congenital abnormality of right atrioventricular valve papillary muscle in double inlet ventricle449032008
- Hypoplasia of right atrioventricular valve annulus in double inlet ventricle449040002
- Ebstein anomaly of left atrioventricular valve in functionally univentricular heart449086000
- Ebstein's anomaly of left atrioventricular valve in functionally univentricular heart449086000
- Congenital abnormality of left atrioventricular valve chordae tendinae in double inlet ventricle449098005
- Left atrioventricular valvar stenosis in double inlet ventricle449099002
- Left atrioventricular valve stenosis in double inlet ventricle449099002
- Double orifice of right atrioventricular valve in double inlet ventricle449111002
- Hypoplasia of left atrioventricular valve annulus in double inlet ventricle449228007
- Congenital abnormality of right atrioventricular valve chordae tendinae in double inlet ventricle449315003
- Congenital abnormality of right atrioventricular valve in double inlet ventricle449316002
- Congenital anomaly of left-sided atrioventricular valve in double inlet ventricle871583003
- Congenital anomaly of right-sided atrioventricular valve in double inlet ventricle871585005
- Double inlet to solitary ventricle of indeterminate morphology871659004
UMLS
- Absence of interventricular septumC0152424
- Common Ventricle DisorderC0152424
- Common ventricleC0152424
- Common ventricle (disorder)C0152424
- Complex Single VentricleC0152424
- Complex Single VentriclesC0152424
- Cor triloculare biatriatumC0152424
- Single ventricleC0152424
- Univentricular HeartC0152424
- Univentricular HeartsC0152424
- Univentricular heartC0152424
- Ventricle, Complex SingleC0152424
- cor triloculare biatriatumC0152424
- single ventricleC0152424
- univentricular heartC0152424
- ventricle commonC0152424
- DIV - Double inlet ventricleC0344620
- Double inlet ventricleC0344620
- Double inlet ventricle (disorder)C0344620
Clinical Terms
- Single ventricle
- Hypoplastic left atrioventricular valve papillary muscle
- Imperforate left atrioventricular valve
- DIRV - Double inlet right ventricle
- Straddling left atrioventricular valve
- Congenital absence of papillary muscle
- Unguarded right atrioventricular valve orifice
- Congenital abnormality of right atrioventricular valve papillary muscle
- Congenital abnormality of right atrioventricular valve chordae tendinae in double inlet ventricle
- Abnormality of left atrioventricular valve papillary muscle
- Right atrioventricular valve hypoplasia
- Common atrioventricular orifice in double inlet ventricle
- Left atrioventricular valve chordae too long
- Univentricular heart
- Two atrioventricular valves in double inlet ventricle
- Complex Single Ventricle
- Congenital hypoplastic left atrioventricular valve papillary muscle
- Left atrioventricular valvar stenosis in double inlet ventricle
- Left atrioventricular valve atresia
- DIV - Abnormality of left atrioventricular valve in double inlet ventricle
- Absent left atrioventricular valve leaflets
- Parachute malformation of right atrioventricular valve
- Right atrioventricular valve leaflets absent in double inlet ventricle (unguarded orifice)
- Left atrioventricular valve hypoplasia
- CT - Abnormality of left atrioventricular chordae tendinae
- Congenital abnormality of left atrioventricular valve chordae tendinae in double inlet ventricle
- Ventricle, Complex Single
- Arcade abnormality of left atrioventricular valve chordae
- CT - Abnormality of right atrioventricular chordae tendinae
- Congenital abnormality of left atrioventricular valve papillary muscle
- Congenital parachute malformation of left atrioventricular valve
- Congenital fusion of left atrioventricular valve papillary muscles
- Left atrioventricular valve chordae to outlet septum
- Left atrioventricular valve chordae too short
- Single left ventricle
- Common ventricle
- Right atrioventricular valve stenosis
- True cleft of left atrioventricular valve leaflet
- Univentricular Hearts
- Double inlet to ventricle of indeterminate morphology
- DILV - Double inlet left ventricle
- cor triloculare biatriatum
- Double inlet right ventricle
- Congenital absence of left atrioventricular valve papillary muscle
- Functionally univentricular heart
- Mucoid thickening of left atrioventricular valve leaflet
- Left atrioventricular valve leaflet dysplasia
- Ebstein's anomaly of left atrioventricular valve in functionally univentricular heart
- Congenital anomaly of left-sided atrioventricular valve in double inlet ventricle
- Accessory tissue on left atrioventricular valve leaflet
- Congenital cleft of cardiac valve
- Complex Single Ventricles
- Absent left atrioventricular valve papillary muscle
- Mucoid thickening of right atrioventricular valve
- Single right ventricle
- Abnormality of left atrioventricular valve chordae tendinae
- Ebstein's anomaly of left atrioventricular valve
- Right atrioventricular valvar leaflets absent in double inlet ventricle (unguarded orifice)
- Double inlet to solitary ventricle of indeterminate morphology
- Straddling right atrioventricular valve
- Abnormality of right atrioventricular valve chords
- DIV - Abnormality of right atrioventricular valve in double inlet ventricle
- Parachute malformation of left atrioventricular valve
- Overriding right atrioventricular valve
- Double inlet left ventricle
- Congenital anomaly of right-sided atrioventricular valve in double inlet ventricle
- Double orifice of left atrioventricular valve
- Left atrioventricular valve prolapse
- Double orifice of right atrioventricular valve in double inlet ventricle
- Left atrioventricular valve dysplasia
- Right atrioventricular valve dysplasia
- Absence of interventricular septum
- Double inlet ventricle (disorder)
- Common Ventricle Disorder
- Congenital abnormality of left atrioventricular valve in double inlet ventricle
- Common ventricle (disorder)
- Abnormality of right atrioventricular valve papillary muscle
- Congenital abnormality of right atrioventricular valve papillary muscle in double inlet ventricle
- Left atrioventricular valve leaflet abnormality
- Absent right atrioventricular valve leaflets
- Congenital abnormality of right atrioventricular valve in double inlet ventricle
- Ebstein anomaly of left atrioventricular valve
- Abnormality of left atrioventricular valve chords
- Abnormality of right atrioventricular valve in double inlet ventricle
- ventricle common
- Fused left atrioventricular valve papillary muscles
- Congenital parachute malformation of right atrioventricular valve
- Functional single ventricle
- Left atrioventricular valve stenosis in double inlet ventricle
- DIIV - Double inlet indeterminate ventricle
- Mucoid thickening of left atrioventricular valve
- Solitary ventricle of indeterminate morphology
- Double orifice of right atrioventricular valve
- Left atrioventricular valve stenosis
- Overriding left atrioventricular valve
- Ebstein anomaly of left atrioventricular valve in functionally univentricular heart
- Straddling tricuspid valve
- Congenital abnormality of right atrioventricular valve leaflet in double inlet ventricle
- DIV - Double inlet ventricle
- Hypoplasia of left atrioventricular valve annulus in double inlet ventricle
- Abnormality of right atrioventricular valve chordae tendinae
- Abnormality of left atrioventricular valve in double inlet ventricle
- Unguarded left atrioventricular valve orifice
- Hypoplasia of right atrioventricular valve annulus in double inlet ventricle
Frequently Asked Questions
What is the ICD-10 code for double inlet ventricle?
The ICD-10-CM code for double inlet ventricle is Q20.4. The full clinical description is "Double inlet ventricle". Q20.4 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q20.4 mean?
ICD-10-CM code Q20.4 represents “Double inlet ventricle”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q20.4 a billable code?
Yes, Q20.4 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q20.4 in?
Q20.4 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q20.4?
Q20.4 has Excludes1 notes indicating codes that cannot be used together with it, including: dextrocardia with situs inversus (Q89.3); mirror-image atrial arrangement with situs inversus (Q89.3).
What SNOMED CT codes does Q20.4 map to?
Q20.4 maps to 66 SNOMED CT concepts: 253501000, 253483002, 253506005, 253473001, 253454000, and 61 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q20.4?
Q20.4 is linked to 2 UMLS Concept Unique Identifiers: C0152424, C0344620. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q20.4 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like double inlet ventricle affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q20.4?
Q20.4 maps to the ICD-11 code: LA89.0 (Double inlet atrioventricular connection).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.