Q20.4

Billable

Double inlet ventricle

Double inlet ventricle

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Common ventricle
  • Cor triloculare biatriatum
  • Single ventricle

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(8)
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

Also Known As / Clinical Terms(219)

SNOMED CT

Clinical Terms

  • Single ventricle
  • Hypoplastic left atrioventricular valve papillary muscle
  • Imperforate left atrioventricular valve
  • DIRV - Double inlet right ventricle
  • Straddling left atrioventricular valve
  • Congenital absence of papillary muscle
  • Unguarded right atrioventricular valve orifice
  • Congenital abnormality of right atrioventricular valve papillary muscle
  • Congenital abnormality of right atrioventricular valve chordae tendinae in double inlet ventricle
  • Abnormality of left atrioventricular valve papillary muscle
  • Right atrioventricular valve hypoplasia
  • Common atrioventricular orifice in double inlet ventricle
  • Left atrioventricular valve chordae too long
  • Univentricular heart
  • Two atrioventricular valves in double inlet ventricle
  • Complex Single Ventricle
  • Congenital hypoplastic left atrioventricular valve papillary muscle
  • Left atrioventricular valvar stenosis in double inlet ventricle
  • Left atrioventricular valve atresia
  • DIV - Abnormality of left atrioventricular valve in double inlet ventricle
  • Absent left atrioventricular valve leaflets
  • Parachute malformation of right atrioventricular valve
  • Right atrioventricular valve leaflets absent in double inlet ventricle (unguarded orifice)
  • Left atrioventricular valve hypoplasia
  • CT - Abnormality of left atrioventricular chordae tendinae
  • Congenital abnormality of left atrioventricular valve chordae tendinae in double inlet ventricle
  • Ventricle, Complex Single
  • Arcade abnormality of left atrioventricular valve chordae
  • CT - Abnormality of right atrioventricular chordae tendinae
  • Congenital abnormality of left atrioventricular valve papillary muscle
  • Congenital parachute malformation of left atrioventricular valve
  • Congenital fusion of left atrioventricular valve papillary muscles
  • Left atrioventricular valve chordae to outlet septum
  • Left atrioventricular valve chordae too short
  • Single left ventricle
  • Common ventricle
  • Right atrioventricular valve stenosis
  • True cleft of left atrioventricular valve leaflet
  • Univentricular Hearts
  • Double inlet to ventricle of indeterminate morphology
  • DILV - Double inlet left ventricle
  • cor triloculare biatriatum
  • Double inlet right ventricle
  • Congenital absence of left atrioventricular valve papillary muscle
  • Functionally univentricular heart
  • Mucoid thickening of left atrioventricular valve leaflet
  • Left atrioventricular valve leaflet dysplasia
  • Ebstein's anomaly of left atrioventricular valve in functionally univentricular heart
  • Congenital anomaly of left-sided atrioventricular valve in double inlet ventricle
  • Accessory tissue on left atrioventricular valve leaflet
  • Congenital cleft of cardiac valve
  • Complex Single Ventricles
  • Absent left atrioventricular valve papillary muscle
  • Mucoid thickening of right atrioventricular valve
  • Single right ventricle
  • Abnormality of left atrioventricular valve chordae tendinae
  • Ebstein's anomaly of left atrioventricular valve
  • Right atrioventricular valvar leaflets absent in double inlet ventricle (unguarded orifice)
  • Double inlet to solitary ventricle of indeterminate morphology
  • Straddling right atrioventricular valve
  • Abnormality of right atrioventricular valve chords
  • DIV - Abnormality of right atrioventricular valve in double inlet ventricle
  • Parachute malformation of left atrioventricular valve
  • Overriding right atrioventricular valve
  • Double inlet left ventricle
  • Congenital anomaly of right-sided atrioventricular valve in double inlet ventricle
  • Double orifice of left atrioventricular valve
  • Left atrioventricular valve prolapse
  • Double orifice of right atrioventricular valve in double inlet ventricle
  • Left atrioventricular valve dysplasia
  • Right atrioventricular valve dysplasia
  • Absence of interventricular septum
  • Double inlet ventricle (disorder)
  • Common Ventricle Disorder
  • Congenital abnormality of left atrioventricular valve in double inlet ventricle
  • Common ventricle (disorder)
  • Abnormality of right atrioventricular valve papillary muscle
  • Congenital abnormality of right atrioventricular valve papillary muscle in double inlet ventricle
  • Left atrioventricular valve leaflet abnormality
  • Absent right atrioventricular valve leaflets
  • Congenital abnormality of right atrioventricular valve in double inlet ventricle
  • Ebstein anomaly of left atrioventricular valve
  • Abnormality of left atrioventricular valve chords
  • Abnormality of right atrioventricular valve in double inlet ventricle
  • ventricle common
  • Fused left atrioventricular valve papillary muscles
  • Congenital parachute malformation of right atrioventricular valve
  • Functional single ventricle
  • Left atrioventricular valve stenosis in double inlet ventricle
  • DIIV - Double inlet indeterminate ventricle
  • Mucoid thickening of left atrioventricular valve
  • Solitary ventricle of indeterminate morphology
  • Double orifice of right atrioventricular valve
  • Left atrioventricular valve stenosis
  • Overriding left atrioventricular valve
  • Ebstein anomaly of left atrioventricular valve in functionally univentricular heart
  • Straddling tricuspid valve
  • Congenital abnormality of right atrioventricular valve leaflet in double inlet ventricle
  • DIV - Double inlet ventricle
  • Hypoplasia of left atrioventricular valve annulus in double inlet ventricle
  • Abnormality of right atrioventricular valve chordae tendinae
  • Abnormality of left atrioventricular valve in double inlet ventricle
  • Unguarded left atrioventricular valve orifice
  • Hypoplasia of right atrioventricular valve annulus in double inlet ventricle
Frequently Asked Questions
What is the ICD-10 code for double inlet ventricle?

The ICD-10-CM code for double inlet ventricle is Q20.4. The full clinical description is "Double inlet ventricle". Q20.4 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code Q20.4 mean?

ICD-10-CM code Q20.4 represents “Double inlet ventricle”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.

Is Q20.4 a billable code?

Yes, Q20.4 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is Q20.4 in?

Q20.4 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).

What codes cannot be used with Q20.4?

Q20.4 has Excludes1 notes indicating codes that cannot be used together with it, including: dextrocardia with situs inversus (Q89.3); mirror-image atrial arrangement with situs inversus (Q89.3).

What SNOMED CT codes does Q20.4 map to?

Q20.4 maps to 66 SNOMED CT concepts: 253501000, 253483002, 253506005, 253473001, 253454000, and 61 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for Q20.4?

Q20.4 is linked to 2 UMLS Concept Unique Identifiers: C0152424, C0344620. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does Q20.4 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like double inlet ventricle affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of Q20.4?

Q20.4 maps to the ICD-11 code: LA89.0 (Double inlet atrioventricular connection).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.