Growth delay with hydrocephalus and lung hypoplasia syndrome
congenital hydrocephaly
hydrocephalus in newborn
Hypoplasia of corpus callosum, intellectual disability, adducted thumbs, spasticity, hydrocephalus syndrome
Congenital abnormality of sclera
Hydrocephaly
CSF - Cerebrospinal rhinorrhoea
Kyphosis of thoracic spine
Cerebrospinal fluid rhinorrhea due to hydrocephalus
Beemer lethal malformation syndrome
Thoracic dysplasia and hydrocephalus syndrome
Vertebral abnormality, anal atresia, cardiac abnormality, tracheo-esophageal fistula, renal anomaly, limb defect syndrome with hydrocephalus
Portwine naevus
Congenital elevation of scapula
Truncal obesity
X-linked hydrocephalus
Nova syndrome
Congenital hydrocephalus, low insertion of umbilicus syndrome
Leak of cranial cerebrospinal fluid due to hydrocephalus
Palmer Pagon syndrome
Daish Hardman Lamont syndrome
Port-wine stain of skin
Cerebrospinal fluid rhinorrhoea due to hydrocephalus
Sprengel's deformity
Port-wine naevi, mega cisterna magna, hydrocephalus syndrome
Hydrocephalus, costovertebral dysplasia, Sprengel anomaly syndrome
Naevus flammeus
Central obesity
Hypoplasia of corpus callosum and mental retardation with adducted thumbs and spasticity and hydrocephalus syndrome
Congenital hydrencephaly
Obesity of face and trunk, sparing limbs
Congenital humpback
EFE - Endocardial fibroelastosis
Port-wine nevus
Hydrocephaly, tall stature, joint laxity syndrome
Hydrocephalus congenital
Hydrocephalus
Aqueduct of Sylvius anomaly
External hydrocephalus
Agenesis of cerebellum and hydrocephalus syndrome
CSF - Cerebrospinal rhinorrhea
Port-wine naevus
Total agenesis of cerebellum
Blue sclera
Congenital anomaly of the meninges
Endocardial fibroelastosis
X-linked hydrocephalus syndrome
Port-wine nevi, mega cisterna magna, hydrocephalus syndrome
Congenital hydrencephalus
Port wine stain of skin
Bickers-Adams syndrome
Hypoplasia of corpus callosum
CONGEN HYDROCEPHALUS
Cerebellum agenesis with hydrocephaly
MPPH (megalencephaly, polymicrogyria, polydactyly, hydrocephalus) syndrome
Elastomyofibrosis
Hydrocephalus with endocardial fibroelastosis and cataract syndrome
Congenital malformation of the meninges
Hydrocephalus, congenital
Agenesis of cerebellum
VACTERL syndrome with hydrocephalus
Portwine nevus
Primary hydrocephalus
Congenital hypoplasia of cerebral white matter
Congenital absence of cerebellum
Hydrocephalus with obesity and hypogonadism syndrome
Hydrocephalus, cardiac malformation, dense bone syndrome
Congenital dilatation of cerebral ventricles
PWS - Port-wine stain
Primary hydrocephaly
Undescended shoulder
Fibroelastosis cordis
Cranial cerebrospinal fluid fistula
Dandy-Walker malformation
Vertebral abnormality, anal atresia, cardiac abnormality, tracheo-oesophageal fistula, renal anomaly, limb defect syndrome with hydrocephalus
Cerebrospinal fluid rhinorrhoea
Congenital hunchback
HEC (hydrocephalus, endocardial fibroelastosis, cataract) syndrome
Congenital kyphosis
Centripetal obesity
Congenital stenosis of aqueduct of Sylvius
Dandy-Walker deformity
Game Friedman Paradice syndrome
Kyphosis of dorsal spine
Cerebrospinal rhinorrhea
Abnormal blue sclerae
Macroencephaly
MPPH syndrome
Congenital hydrocephalus (disorder)
Beemer Ertbruggen syndrome
L1 syndrome
Braddock Jones Superneau syndrome
Internal hydrocephalus
Craniosynostosis with Dandy-Walker malformation and hydrocephalus syndrome
Ferlini Ragno Calzolari syndrome
Hemispheric cerebral hypoplasia
Cerebrospinal rhinorrhoea
Arrested hydrocephalus
Congenital obstructive hydrocephalus
Cerebrospinal fluid rhinorrhea
Hydrocephalus, tall stature, joint laxity syndrome
Congenital endocardial fibroelastosis
Cranial cerebrospinal fluid leak
Port-wine stain
HEC syndrome
Kyphosis deformity of thoracic spine
Waaler Aarskog syndrome
Hydrocephalus associated with congenital aqueduct stenosis
Cranial cerebrospinal fluid leak due to hydrocephalus
Hydrocephalus, blue sclera, nephropathy syndrome
Android fat distribution
Fat body with thin limbs
Congenital deformity of lumbosacral region
Mega cisterna magna
Megalencephaly
Congenital hypoplasia of cerebral hemisphere
Daentl Townsend Siegel syndrome
Congenital kyphosis of thoracic spine
Dandy-Walker syndrome
Obstructive hydrocephalus
CRASH syndrome
Nevus flammeus
Leak of cranial cerebrospinal fluid
Port-wine birthmark
Megalencephaly, polymicrogyria, postaxial polydactyly, hydrocephalus syndrome
Cerebral degeneration due to congenital hydrocephalus
Sengers Hamel Otten syndrome
Congenital anomaly of sclera

Frequently Asked Questions

What is the ICD-10 code for congenital hydrocephalus, unspecified?

The ICD-10-CM code for congenital hydrocephalus, unspecified is Q03.9. The full clinical description is "Congenital hydrocephalus, unspecified". Q03.9 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code Q03.9 mean?

ICD-10-CM code Q03.9 represents “Congenital hydrocephalus, unspecified”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.

Is Q03.9 a billable code?

Yes, Q03.9 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is Q03.9 in?

Q03.9 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).

What codes cannot be used with Q03.9?

Q03.9 has Excludes1 notes indicating codes that cannot be used together with it, including: Arnold-Chiari syndrome, type II (Q07.0-); acquired hydrocephalus (G91.-); hydrocephalus due to congenital toxoplasmosis (P37.1); and 1 more.

What SNOMED CT codes does Q03.9 map to?

Q03.9 maps to 50 SNOMED CT concepts: 204164000, 253172000, 715990006, 248311001, 25397008, and 45 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for Q03.9?

Q03.9 is linked to 1 UMLS Concept Unique Identifier: C0020256. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does Q03.9 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital hydrocephalus, unspecified affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of Q03.9?

Q03.9 maps to the ICD-11 code: LA04.Z (Congenital hydrocephalus, unspecified).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.