Q01.2
BillableOccipital encephalocele
Occipital encephalocele
Coding Notes
Includes
Conditions included under this code
- Arnold-Chiari syndrome, type III
- encephalocystocele
- encephalomyelocele
- hydroencephalocele
- hydromeningocele, cranial
- meningocele, cerebral
- meningoencephalocele
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(4)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(51)
SNOMED CT
- Occipital encephalocele42376006
- Brain stem herniation63986002
- Herniation of brainstem63986002
- Arnold-Chiari syndrome253184003
- Chiari malformation253184003
- Arnold Chiari type 3253186001
- Chiari malformation type III253186001
- Occipital meningocele445468002
- Knobloch syndrome703542000
- Retinal detachment and occipital encephalocele703542000
- Retinal detachment and occipital encephalocoele703542000
- Lethal occipital encephalocele, skeletal dysplasia syndrome773672007
UMLS
- Brain tissue sticks out through back of skullC0014067
- ENCEPH OCCIPITALC0014067
- Encephalocele, OccipitalC0014067
- Encephalocele, occipitalC0014067
- Encephaloceles, OccipitalC0014067
- NotoencephaloceleC0014067
- NotoencephalocelesC0014067
- OCCIPITAL ENCEPHC0014067
- Occipital EncephaloceleC0014067
- Occipital EncephalocelesC0014067
- Occipital encephaloceleC0014067
- Occipital encephalocele (disorder)C0014067
- Occipital meningoencephaloceleC0014067
- Posterior encephaloceleC0014067
- encephalocele occipitalC0014067
- occipital encephaloceleC0014067
Clinical Terms
- encephalocele occipital
- Brain stem herniation
- Retinal detachment and occipital encephalocele
- ENCEPH OCCIPITAL
- Arnold-Chiari syndrome
- Retinal detachment and occipital encephalocoele
- Occipital Encephaloceles
- Herniation of brainstem
- Occipital meningocele
- Chiari malformation
- OCCIPITAL ENCEPH
- Posterior encephalocele
- Lethal occipital encephalocele, skeletal dysplasia syndrome
- Chiari malformation type III
- Knobloch syndrome
- Arnold Chiari type 3
- Encephaloceles, Occipital
- Occipital encephalocele (disorder)
- Notoencephaloceles
- Encephalocele, occipital
- Brain tissue sticks out through back of skull
- Notoencephalocele
- Occipital meningoencephalocele
Frequently Asked Questions
What is the ICD-10 code for occipital encephalocele?
The ICD-10-CM code for occipital encephalocele is Q01.2. The full clinical description is "Occipital encephalocele". Q01.2 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q01.2 mean?
ICD-10-CM code Q01.2 represents “Occipital encephalocele”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q01.2 a billable code?
Yes, Q01.2 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q01.2 in?
Q01.2 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q01.2?
Q01.2 has Excludes1 notes indicating codes that cannot be used together with it, including: Meckel-Gruber syndrome (Q61.9).
What SNOMED CT codes does Q01.2 map to?
Q01.2 maps to 7 SNOMED CT concepts: 253186001, 253184003, 63986002, 703542000, 773672007, and 2 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q01.2?
Q01.2 is linked to 1 UMLS Concept Unique Identifier: C0014067. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q01.2 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like occipital encephalocele affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q01.2?
Q01.2 maps to the ICD-11 code: LA01 (Cephalocele).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.