Q00.0
BillableAnencephaly
Anencephaly
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Acephaly
- Acrania
- Amyelencephaly
- Hemianencephaly
- Hemicephaly
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(2)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(152)
SNOMED CT
- Congenital absence of cerebrum11701009
- Hemicephalia11701009
- Hemicephalus11701009
- Hemicephaly11701009
- Holoacardius acephalus35577008
- Absence of head AND hands63340009
- Acephalocheiria63340009
- Acephalochiria63340009
- Amyelencephalus75076004
- Amyelencephaly75076004
- Hemianencephaly85641006
- Anencephalus89369001
- Anencephaly89369001
- Congenital absence of brain89369001
- Acephalia91848009
- Acephalus91848009
- Acephaly91848009
- Congenital absence of head91848009
- Acrania203923004
- Acardia205834002
- Acephalobrachius205835001
- Incomplete anencephaly359824007
- Holoanencephaly417658006
- Brain aplasia, congenital702611008
- Congenital brain aplasia702611008
- Anencephaly without rachischisis717939009
- Acheiria of left hand16090091000119100
- Congenital absence of left hand16090091000119100
- Acheiria of right hand1078261000119107
- Congenital absence of right hand1078261000119107
UMLS
- ABSENCE OF BRAIN CONGENC0002902
- ANPHC0002902
- Absence of Brain, CongenitalC0002902
- AnencephaliaC0002902
- AnencephaliasC0002902
- AnencephalusC0002902
- Anencephalus (disorder)C0002902
- AnencephalyC0002902
- Brain Congenital AbsenceC0002902
- CONGEN ABSENCE OF BRAINC0002902
- Congenital Absence of BrainC0002902
- Congenital absence of brainC0002902
- Embryonic anencephalyC0002902
- Fetal anencephalyC0002902
- Fetal anencephaly (disorder)C0002902
- Foetal anencephalyC0002902
- anencephaliaC0002902
- anencephalusC0002902
- anencephalyC0002902
- brain aplasiaC0002902
- AcephaliaC0685896
- AcephalusC0685896
- AcephalyC0685896
- Acephaly (disorder)C0685896
- Congenital absence of headC0685896
- acephaliC0685896
- acephalusC0685896
- acephalyC0685896
- AcraniaC0702169
- Acrania (disorder)C0702169
- AcraniasC0702169
- acraniaC0702169
- acraniusC0702169
- AmyelencephalusC0266672
- Amyelencephalus (disorder)C0266672
- AmyelencephalyC0266672
- Brain aplasia, congenitalC0266672
- Congenital brain aplasiaC0266672
- Congenital brain aplasia (disorder)C0266672
- Anencephalies, PartialC0302356
- Anencephaly, HemicranialC0302356
- Anencephaly, IncompleteC0302356
- Anencephaly, PartialC0302356
- HemianencephalyC0302356
- Hemianencephaly (disorder)C0302356
- HemicraniaC0302356
- Hemicranial AnencephalyC0302356
- Incomplete AnencephalyC0302356
- Incomplete anencephalyC0302356
- Incomplete anencephaly (disorder)C0302356
- Partial AnencephaliesC0302356
- Partial AnencephalyC0302356
- hemianencephalyC0302356
- hemicraniaC0302356
- Congenital absence of cerebrumC0266452
- HemicephaliaC0266452
- HemicephalusC0266452
- HemicephalyC0266452
- Hemicephaly (disorder)C0266452
- hemicephaliaC0266452
- hemicephalusC0266452
- hemicephalyC0266452
Clinical Terms
- Hemianencephaly (disorder)
- Acranias
- Amyelencephalus (disorder)
- Anencephalus (disorder)
- acranius
- Congenital absence of right hand
- hemicephalus
- ABSENCE OF BRAIN CONGEN
- Congenital Absence of Brain
- Brain aplasia, congenital
- Acephaly (disorder)
- Incomplete anencephaly
- Anencephaly, Partial
- Acephalocheiria
- Acephalobrachius
- Incomplete anencephaly (disorder)
- Congenital absence of left hand
- Anencephalies, Partial
- Acephalia
- acrania
- Anencephaly, Hemicranial
- acephalus
- Acephaly
- Partial Anencephaly
- anencephalia
- Hemicephaly
- CONGEN ABSENCE OF BRAIN
- Fetal anencephaly (disorder)
- Anencephalias
- Congenital brain aplasia
- Acephalochiria
- Embryonic anencephaly
- Hemicrania
- Amyelencephaly
- Anencephaly, Incomplete
- Congenital brain aplasia (disorder)
- Amyelencephalus
- Fetal anencephaly
- Hemicranial Anencephaly
- Holoacardius acephalus
- ANPH
- Absence of Brain, Congenital
- hemianencephaly
- Acrania (disorder)
- brain aplasia
- Hemicephaly (disorder)
- Brain Congenital Absence
- Acardia
- Absence of head AND hands
- Acheiria of right hand
- Anencephalus
- Congenital absence of head
- Foetal anencephaly
- Congenital absence of cerebrum
- Hemicephalia
- Holoanencephaly
- acephali
- Partial Anencephalies
- Anencephaly without rachischisis
- Acheiria of left hand
Frequently Asked Questions
What is the ICD-10 code for anencephaly?
The ICD-10-CM code for anencephaly is Q00.0. The full clinical description is "Anencephaly". Q00.0 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q00.0 mean?
ICD-10-CM code Q00.0 represents “Anencephaly”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q00.0 a billable code?
Yes, Q00.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q00.0 in?
Q00.0 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What SNOMED CT codes does Q00.0 map to?
Q00.0 maps to 16 SNOMED CT concepts: 63340009, 205834002, 91848009, 205835001, 16090091000119100, and 11 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q00.0?
Q00.0 is linked to 6 UMLS Concept Unique Identifiers: C0002902, C0685896, C0702169, C0266672, C0302356, and 1 more. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q00.0 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like anencephaly affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q00.0?
Q00.0 maps to the ICD-11 code: LA00.0Z (Anencephaly, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.