N25.1
BillableNephrogenic diabetes insipidus
Nephrogenic diabetes insipidus
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •disorders of kidney and ureter with urolithiasisN20-N23
Related Codes(3)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(114)
SNOMED CT
- Secondary AVP (arginine vasopressin)-related polyuria13196008
- Secondary arginine vasopressin-related polyuria13196008
- Secondary diabetes insipidus13196008
- Secondary vasopressin-related polyuria13196008
- Acquired AVP (arginine vasopressin) resistance81475007
- Acquired AVP-R (arginine vasopressin resistance)81475007
- Acquired nephrogenic diabetes insipidus81475007
- Acquired vasopressin resistance81475007
- AVP-R - arginine vasopressin resistance111395007
- Arginine vasopressin resistance111395007
- NDI - Nephrogenic diabetes insipidus111395007
- Nephrogenic diabetes insipidus111395007
- Vasopressin resistance111395007
- Arginine vasopressin resistance, intracranial calcification, short stature, facial dysmorphism syndrome716200002
- Nephrogenic diabetes insipidus and intracranial calcification syndrome716200002
- Schofer Beetz Bohl syndrome716200002
- Autosomal hereditary AVP-R (arginine vasopressin resistance)1296897006
- Autosomal hereditary arginine vasopressin resistance1296897006
- Autosomal hereditary vasopressin resistance1296897006
- Hereditary nephrogenic diabetes insipidus1296897006
- Hereditary AVP-R (arginine vasopressin resistance)1296898001
- Hereditary arginine vasopressin resistance1296898001
- Hereditary vasopressin resistance1296898001
- Autosomal dominant hereditary AVP-R (arginine vasopressin resistance)1296908006
- Autosomal dominant hereditary arginine vasopressin resistance1296908006
- Autosomal dominant hereditary vasopressin resistance1296908006
- Autosomal dominant vasopressin resistance1296908006
- Autosomal recessive hereditary AVP-R (arginine vasopressin resistance)1296909003
- Autosomal recessive hereditary arginine vasopressin resistance1296909003
- Autosomal recessive hereditary vasopressin resistance1296909003
- Autosomal recessive vasopressin resistance1296909003
- X-linked hereditary AVP-R (arginine vasopressin resistance)1296910008
- X-linked hereditary arginine vasopressin resistance1296910008
- X-linked hereditary vasopressin resistance1296910008
- Hereditary AVP (arginine vasopressin)-related polyuria1296911007
- Hereditary arginine vasopressin-related polyuria1296911007
- Hereditary vasopressin-related polyuria1296911007
- Secondary AVP-R (arginine vasopressin resistance)1296921004
- Secondary arginine vasopressin resistance1296921004
- Secondary vasopressin resistance1296921004
- Partial AVP (arginine vasopressin)-related polyuria68061000119109
- Partial arginine vasopressin-related polyuria68061000119109
- Partial diabetes insipidus68061000119109
- Partial vasopressin-related polyuria68061000119109
- Partial AVP-R (arginine vasopressin resistance)368961000119107
- Partial arginine vasopressin resistance368961000119107
- Partial nephrogenic diabetes insipidus368961000119107
- Partial vasopressin resistance368961000119107
UMLS
- AVP-R - arginine vasopressin resistanceC0162283
- Arginine vasopressin resistanceC0162283
- Arginine vasopressin resistance (disorder)C0162283
- Diabetes Insipidus, NephrogenicC0162283
- Diabetes insipidus nephrogenicC0162283
- Diabetes insipidus, nephrogenicC0162283
- NDIC0162283
- NDI - Nephrogenic diabetes insipidusC0162283
- Nephrogenic Diabetes InsipidusC0162283
- Nephrogenic diabetes insipidusC0162283
- Vasopressin resistanceC0162283
- diabete insipidus nephrogenicC0162283
- diabetes insipidus nephrogenicC0162283
- nephrogenic diabetes insipidusC0162283
Clinical Terms
- Partial arginine vasopressin-related polyuria
- Acquired vasopressin resistance
- AVP-R - arginine vasopressin resistance
- Partial AVP-R (arginine vasopressin resistance)
- Partial AVP (arginine vasopressin)-related polyuria
- Acquired nephrogenic diabetes insipidus
- Autosomal dominant vasopressin resistance
- Acquired AVP (arginine vasopressin) resistance
- Arginine vasopressin resistance, intracranial calcification, short stature, facial dysmorphism syndrome
- Autosomal recessive hereditary vasopressin resistance
- Vasopressin resistance
- X-linked hereditary vasopressin resistance
- X-linked hereditary arginine vasopressin resistance
- Autosomal hereditary arginine vasopressin resistance
- Partial diabetes insipidus
- Autosomal hereditary AVP-R (arginine vasopressin resistance)
- Autosomal dominant hereditary arginine vasopressin resistance
- NDI
- Acquired AVP-R (arginine vasopressin resistance)
- Hereditary arginine vasopressin-related polyuria
- Secondary AVP (arginine vasopressin)-related polyuria
- Hereditary arginine vasopressin resistance
- Partial vasopressin resistance
- Hereditary nephrogenic diabetes insipidus
- Partial nephrogenic diabetes insipidus
- NDI - Nephrogenic diabetes insipidus
- Partial arginine vasopressin resistance
- Autosomal dominant hereditary vasopressin resistance
- diabete insipidus nephrogenic
- Secondary vasopressin-related polyuria
- Autosomal recessive vasopressin resistance
- Hereditary vasopressin resistance
- Arginine vasopressin resistance
- Nephrogenic diabetes insipidus and intracranial calcification syndrome
- Arginine vasopressin resistance (disorder)
- Secondary arginine vasopressin resistance
- Schofer Beetz Bohl syndrome
- Hereditary AVP (arginine vasopressin)-related polyuria
- Secondary vasopressin resistance
- Diabetes insipidus nephrogenic
- Autosomal dominant hereditary AVP-R (arginine vasopressin resistance)
- Hereditary vasopressin-related polyuria
- Secondary diabetes insipidus
- Secondary AVP-R (arginine vasopressin resistance)
- Autosomal recessive hereditary arginine vasopressin resistance
- Diabetes Insipidus, Nephrogenic
- Autosomal hereditary vasopressin resistance
- Partial vasopressin-related polyuria
- Hereditary AVP-R (arginine vasopressin resistance)
- Secondary arginine vasopressin-related polyuria
- Autosomal recessive hereditary AVP-R (arginine vasopressin resistance)
- X-linked hereditary AVP-R (arginine vasopressin resistance)
Frequently Asked Questions
What is the ICD-10 code for nephrogenic diabetes insipidus?
The ICD-10-CM code for nephrogenic diabetes insipidus is N25.1. The full clinical description is "Nephrogenic diabetes insipidus". N25.1 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code N25.1 mean?
ICD-10-CM code N25.1 represents “Nephrogenic diabetes insipidus”. It is classified under Chapter 14: Diseases of the Genitourinary System and is a billable/specific code that can be used on a claim.
Is N25.1 a billable code?
Yes, N25.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is N25.1 in?
N25.1 is in Chapter 14: Diseases of the Genitourinary System (codes N00-N99).
What codes cannot be used with N25.1?
N25.1 has Excludes1 notes indicating codes that cannot be used together with it, including: diabetes insipidus NOS (E23.2).
What SNOMED CT codes does N25.1 map to?
N25.1 maps to 13 SNOMED CT concepts: 111395007, 81475007, 716200002, 1296908006, 1296897006, and 8 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for N25.1?
N25.1 is linked to 1 UMLS Concept Unique Identifier: C0162283. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does N25.1 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like nephrogenic diabetes insipidus affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of N25.1?
N25.1 maps to the ICD-11 code: GB90.4A (Nephrogenic diabetes insipidus).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.