N04.1
BillableNephrotic syndrome w focal and segmental glomerular lesions
Nephrotic syndrome with focal and segmental glomerular lesions
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Nephrotic syndrome with focal and segmental hyalinosis
- Nephrotic syndrome with focal and segmental sclerosis
- Nephrotic syndrome with focal glomerulonephritis
Includes
Conditions included under this code
- congenital nephrotic syndrome
- lipoid nephrosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
Code Also
A second code may be required; sequencing depends on circumstances
Related Codes(10)
N04.0Nephrotic syndrome with minor glomerular abnormality
N04.2Nephrotic syndrome w diffuse membranous glomerulonephritis
N04.3Nephrotic syndrome w diffuse mesangial prolif glomrlneph
N04.4Nephrotic syndrome w diffuse endocaplry prolif glomrlneph
N04.5Nephrotic syndrome w diffuse mesangiocapillary glomrlneph
N04.6Nephrotic syndrome with dense deposit disease
N04.7Nephrotic syndrome w diffuse crescentic glomerulonephritis
N04.8Nephrotic syndrome with other morphologic changes
N04.9Nephrotic syndrome with unspecified morphologic changes
N04.ANephrotic syndrome with C3 glomerulonephritis
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(23)
SNOMED CT
- Nephrotic syndrome, focal and segmental glomerular lesions197594005
- Congenital nephrotic syndrome with focal glomerulosclerosis236384008
- FSGS - Focal segmental glomerulosclerosis236403004
- Focal segmental glomerulosclerosis236403004
- Classical focal segmental glomerulosclerosis236404005
- Hyperfiltration focal segmental glomerulosclerosis236405006
UMLS
- Nephrotic syndrome w focal and segmental glomerular lesionsC0451720
- Nephrotic syndrome with focal and segmental glomerular lesionsC0451720
- Nephrotic syndrome, focal and segmental glomerular lesionsC0451720
- Nephrotic syndrome, focal and segmental glomerular lesions (disorder)C0451720
- Nephrotic syndrome with focal and segmental hyalinosisC2902887
- Nephrotic syndrome with focal and segmental sclerosisC2902888
- Nephrotic syndrome with focal glomerulonephritisC2902889
Clinical Terms
- Congenital nephrotic syndrome with focal glomerulosclerosis
- Nephrotic syndrome, focal and segmental glomerular lesions (disorder)
- Nephrotic syndrome, focal and segmental glomerular lesions
- Nephrotic syndrome with focal glomerulonephritis
- Classical focal segmental glomerulosclerosis
- Hyperfiltration focal segmental glomerulosclerosis
- Focal segmental glomerulosclerosis
- Nephrotic syndrome with focal and segmental sclerosis
- Nephrotic syndrome with focal and segmental hyalinosis
- FSGS - Focal segmental glomerulosclerosis
Frequently Asked Questions
What is the ICD-10 code for nephrotic syndrome w focal and segmental glomerular lesions?
The ICD-10-CM code for nephrotic syndrome w focal and segmental glomerular lesions is N04.1. The full clinical description is "Nephrotic syndrome with focal and segmental glomerular lesions". N04.1 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code N04.1 mean?
ICD-10-CM code N04.1 represents “Nephrotic syndrome with focal and segmental glomerular lesions”. It is classified under Chapter 14: Diseases of the Genitourinary System and is a billable/specific code that can be used on a claim.
Is N04.1 a billable code?
Yes, N04.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is N04.1 in?
N04.1 is in Chapter 14: Diseases of the Genitourinary System (codes N00-N99).
What codes cannot be used with N04.1?
N04.1 has Excludes1 notes indicating codes that cannot be used together with it, including: hypertensive chronic kidney disease (I12.-).
What SNOMED CT codes does N04.1 map to?
N04.1 maps to 5 SNOMED CT concepts: 236404005, 236384008, 236403004, 236405006, 197594005. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for N04.1?
N04.1 is linked to 4 UMLS Concept Unique Identifiers: C0451720, C2902887, C2902888, C2902889. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does N04.1 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like nephrotic syndrome w focal and segmental glomerular lesions affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of N04.1?
N04.1 maps to the ICD-11 code: GB41 (Nephrotic syndrome).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.