M31.4
BillableAortic arch syndrome [Takayasu]
Aortic arch syndrome [Takayasu]
Coding Notes
Includes
Conditions included under this code
- autoimmune disease NOS
- collagen (vascular) disease NOS
- systemic autoimmune disease
- systemic collagen (vascular) disease
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- autoimmune disease, single organ or single cell-type -code to relevant condition category
Excludes 2
Conditions not included here, but the patient may have both
- •arthropathic psoriasisL40.5
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •compartment syndrome (traumatic)A-)T79
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
Related Codes(9)
M31.0Hypersensitivity angiitis
M31.1Thrombotic microangiopathy
M31.2Lethal midline granuloma
M31.3Wegener's granulomatosis
M31.5Giant cell arteritis with polymyalgia rheumatica
M31.6Other giant cell arteritis
M31.7Microscopic polyangiitis
M31.8Other specified necrotizing vasculopathies
M31.9Necrotizing vasculopathy, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(115)
SNOMED CT
- Acquired aortoarteritis359789008
- Aortic arch arteritis359789008
- Aortic arch syndrome359789008
- Aortitis syndrome359789008
- Atypical coarctation359789008
- Idiopathic medial aortopathy AND arteriopathy359789008
- Martorell syndrome359789008
- Nonspecific aortoarteritis359789008
- Nonspecific arteritis359789008
- Occlusive thromboarteriopathy359789008
- Primary arteritis359789008
- Pulseless disease359789008
- Raeder-Harbitz syndrome359789008
- Reverse coarctation359789008
- Sclerosing aortitis AND arteritis359789008
- Takayasu disease359789008
- Takayasu's arteriopathy359789008
- Takayasu's arteritis359789008
- Takayasu's disease359789008
- Young female arteritis359789008
- Primary systemic arteritis407529009
- Cerebrovascular abnormality due to Takayasu disease838309004
UMLS
- AORTIC ARCH SYNDROMEC0039263
- Acquired aortoarteritisC0039263
- Aortic arch arteritisC0039263
- Aortic arch syndrome [Takayasu]C0039263
- Arteritides, Young FemaleC0039263
- Arteritis, TakayasuC0039263
- Arteritis, Takayasu'sC0039263
- Arteritis, TakayasusC0039263
- Arteritis, Young FemaleC0039263
- Atypical coarctationC0039263
- Disease, TakayasuC0039263
- Female Arteritides, YoungC0039263
- Female Arteritis, YoungC0039263
- Idiopathic medial aortopathy AND arteriopathyC0039263
- Martorell syndromeC0039263
- Nonspecific aortoarteritisC0039263
- Nonspecific arteritisC0039263
- Occlusive thromboarteriopathyC0039263
- PULSELESS DISC0039263
- PULSELESS DISEASEC0039263
- Primary arteritisC0039263
- Pulseless DiseaseC0039263
- Pulseless diseaseC0039263
- Raeder-Harbitz syndromeC0039263
- Reverse coarctationC0039263
- Sclerosing aortitis AND arteritisC0039263
- TAKAYASU ARTERITISC0039263
- Takayasu ArteritisC0039263
- Takayasu DiseaseC0039263
- Takayasu SyndromeC0039263
- Takayasu diseaseC0039263
- Takayasu's ArteritisC0039263
- Takayasu's arteriopathyC0039263
- Takayasu's arteritisC0039263
- Takayasu's diseaseC0039263
- Takayasu's disease (disorder)C0039263
- Takayasus ArteritisC0039263
- YOUNG FEMALE ARTERITISC0039263
- Young Female ArteritidesC0039263
- Young Female ArteritisC0039263
- Young female arteritisC0039263
- aortic arch arteritisC0039263
- aortic arch syndromeC0039263
- arteritis takayasuC0039263
- arteritis takayasu'sC0039263
- arteritis takayasus'sC0039263
- middle aortic syndromeC0039263
- takayasu arteritisC0039263
- takayasu diseaseC0039263
- takayasu syndromeC0039263
- takayasu's arteritisC0039263
- takayasu's diseaseC0039263
- takayasus arteritisC0039263
Clinical Terms
- takayasu syndrome
- Arteritis, Young Female
- Young Female Arteritis
- Takayasu's arteriopathy
- Takayasu Disease
- Pulseless disease
- Arteritides, Young Female
- Primary arteritis
- Arteritis, Takayasu's
- Raeder-Harbitz syndrome
- PULSELESS DIS
- Female Arteritides, Young
- takayasus arteritis
- middle aortic syndrome
- Acquired aortoarteritis
- Martorell syndrome
- Primary systemic arteritis
- arteritis takayasu's
- Aortitis syndrome
- Takayasu's disease
- aortic arch syndrome
- TAKAYASU ARTERITIS
- arteritis takayasus's
- Takayasu's arteritis
- Disease, Takayasu
- Female Arteritis, Young
- Young Female Arteritides
- Idiopathic medial aortopathy AND arteriopathy
- Occlusive thromboarteriopathy
- Nonspecific arteritis
- Atypical coarctation
- Aortic arch arteritis
- Nonspecific aortoarteritis
- Sclerosing aortitis AND arteritis
- arteritis takayasu
- Takayasu's disease (disorder)
- Reverse coarctation
- Arteritis, Takayasus
- Arteritis, Takayasu
- Cerebrovascular abnormality due to Takayasu disease
Frequently Asked Questions
What is the ICD-10 code for aortic arch syndrome [takayasu]?
The ICD-10-CM code for aortic arch syndrome [takayasu] is M31.4. The full clinical description is "Aortic arch syndrome [Takayasu]". M31.4 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code M31.4 mean?
ICD-10-CM code M31.4 represents “Aortic arch syndrome [Takayasu]”. It is classified under Chapter 13: Diseases of the Musculoskeletal System and Connective Tissue and is a billable/specific code that can be used on a claim.
Is M31.4 a billable code?
Yes, M31.4 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is M31.4 in?
M31.4 is in Chapter 13: Diseases of the Musculoskeletal System and Connective Tissue (codes M00-M99).
What codes cannot be used with M31.4?
M31.4 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease, single organ or single cell-type -code to relevant condition category.
What SNOMED CT codes does M31.4 map to?
M31.4 maps to 3 SNOMED CT concepts: 359789008, 838309004, 407529009. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for M31.4?
M31.4 is linked to 1 UMLS Concept Unique Identifier: C0039263. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does M31.4 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like aortic arch syndrome [takayasu] affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of M31.4?
M31.4 maps to the ICD-11 code: 4A44.1 (Aortic arch syndrome).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.