M30.0
BillablePolyarteritis nodosa
Polyarteritis nodosa
Coding Notes
Includes
Conditions included under this code
- autoimmune disease NOS
- collagen (vascular) disease NOS
- systemic autoimmune disease
- systemic collagen (vascular) disease
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- autoimmune disease, single organ or single cell-type -code to relevant condition category
- •microscopic polyarteritisM31.7
Excludes 2
Conditions not included here, but the patient may have both
- •arthropathic psoriasisL40.5
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •compartment syndrome (traumatic)A-)T79
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
Related Codes(4)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(73)
SNOMED CT
- Polyarteritis20258000
- Benign cutaneous periarteritis nodosa58144006
- Periarteritis76805007
- PAN - Polyarteritis nodosa155441006
- Periarteritis nodosa155441006
- Polyarteritis nodosa155441006
- Neuropathy in vasculitis and connective tissue disease193177003
- Polyneuropathy in collagen vascular disease193177003
- Polyneuropathy in polyarteritis nodosa193179000
- Myopathy due to polyarteritis nodosa193249002
- Nephrotic syndrome in polyarteritis nodosa197607004
- Polyarteritis nodosa with single organ involvement239925001
- Cutaneous livedo with nodules239926000
- Cutaneous polyarteritis nodosa239926000
- Nodular livedo239926000
- Polyarteritis nodosa with multi-organ involvement239927009
- Primary systemic arteritis407529009
- Retinal vasculitis due to polyarteritis nodosa416703007
- Medium sized vessel vasculitis724598001
- Medium vessel vasculitis724598001
- Vasculitis of medium sized vessel724598001
- Dementia due to polyarteritis nodosa1259663006
- Vasculitis due to systemic disease1268295005
UMLS
- Classic polyarteritis nodosaC0031036
- Classical Polyarteritis NodosaC0031036
- Kussmaul's diseaseC0031036
- PANC0031036
- PAN - Polyarteritis nodosaC0031036
- Panarteritis NodosaC0031036
- Panarteritis nodosaC0031036
- Periarteritis NodosaC0031036
- Periarteritis nodosaC0031036
- Polyarteritis NodosaC0031036
- Polyarteritis nodosaC0031036
- Polyarteritis nodosa (disorder)C0031036
- Polyarteritis nodosumC0031036
- kussmaul diseaseC0031036
- nodosa polyarteritisC0031036
- panarteritis nodosaC0031036
- periarteritis nodosaC0031036
- polyarteritis nodosaC0031036
- polyarteritis nodosumC0031036
Clinical Terms
- Vasculitis of medium sized vessel
- Myopathy due to polyarteritis nodosa
- Polyarteritis nodosa with multi-organ involvement
- Dementia due to polyarteritis nodosa
- Retinal vasculitis due to polyarteritis nodosa
- Polyarteritis nodosum
- Polyarteritis nodosa (disorder)
- Nephrotic syndrome in polyarteritis nodosa
- Nodular livedo
- Periarteritis
- kussmaul disease
- PAN - Polyarteritis nodosa
- Polyneuropathy in polyarteritis nodosa
- panarteritis nodosa
- Neuropathy in vasculitis and connective tissue disease
- Primary systemic arteritis
- Polyneuropathy in collagen vascular disease
- Kussmaul's disease
- periarteritis nodosa
- Classic polyarteritis nodosa
- Medium sized vessel vasculitis
- Vasculitis due to systemic disease
- Medium vessel vasculitis
- nodosa polyarteritis
- Classical Polyarteritis Nodosa
- Polyarteritis
- Cutaneous livedo with nodules
- Polyarteritis nodosa with single organ involvement
- Benign cutaneous periarteritis nodosa
- Cutaneous polyarteritis nodosa
- PAN
Frequently Asked Questions
What is the ICD-10 code for polyarteritis nodosa?
The ICD-10-CM code for polyarteritis nodosa is M30.0. The full clinical description is "Polyarteritis nodosa". M30.0 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code M30.0 mean?
ICD-10-CM code M30.0 represents “Polyarteritis nodosa”. It is classified under Chapter 13: Diseases of the Musculoskeletal System and Connective Tissue and is a billable/specific code that can be used on a claim.
Is M30.0 a billable code?
Yes, M30.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is M30.0 in?
M30.0 is in Chapter 13: Diseases of the Musculoskeletal System and Connective Tissue (codes M00-M99).
What codes cannot be used with M30.0?
M30.0 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease, single organ or single cell-type -code to relevant condition category; microscopic polyarteritis (M31.7).
What SNOMED CT codes does M30.0 map to?
M30.0 maps to 16 SNOMED CT concepts: 58144006, 239926000, 1259663006, 724598001, 193249002, and 11 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for M30.0?
M30.0 is linked to 1 UMLS Concept Unique Identifier: C0031036. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does M30.0 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like polyarteritis nodosa affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of M30.0?
M30.0 maps to the ICD-11 code: 4A44.4 (Polyarteritis nodosa).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.