L44.0
BillablePityriasis rubra pilaris
Pityriasis rubra pilaris
Coding Notes
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •lipomelanotic reticulosisI89.8
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •systemic connective tissue disordersM30-M36
- •viral wartsB07
Related Codes(6)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(75)
SNOMED CT
- Devergie's disease3755001
- Lichen ruber acuminatus3755001
- PRP - Pityriasis rubra pilaris3755001
- Pityriasis rubra pilaris3755001
- Classical adult pityriasis rubra pilaris238618003
- PRP - Classical adult pityriasis rubra pilaris238618003
- PRP - Type I pityriasis rubra pilaris238618003
- Type I pityriasis rubra pilaris238618003
- Atypical adult pityriasis rubra pilaris238619006
- PRP - Atypical adult pityriasis rubra pilaris238619006
- PRP - Type II pityriasis rubra pilaris238619006
- Type II pityriasis rubra pilaris238619006
- Classical juvenile pityriasis rubra pilaris238620000
- PRP - Classical juvenile pityriasis rubra pilaris238620000
- PRP - Type III pityriasis rubra pilaris238620000
- Type III pityriasis rubra pilaris238620000
- Circumscribed juvenile pityriasis rubra pilaris238621001
- PRP - Circumscribed juvenile pityriasis rubra pilaris238621001
- PRP - Type IV pityriasis rubra pilaris238621001
- Type IV pityriasis rubra pilaris238621001
- Atypical juvenile pityriasis rubra pilaris238622008
- PRP - Atypical juvenile pityriasis rubra pilaris238622008
- PRP - Type V pityriasis rubra pilaris238622008
- Type V pityriasis rubra pilaris238622008
- Nail dystrophy due to pityriasis rubra pilaris402340009
- Pityriasis rubra pilaris due to HIV infection1142046003
- Pityriasis rubra pilaris due to human immunodeficiency virus infection1142046003
- Disorder of skin due to human immunodeficiency virus infection1148863007
- Skin disease due to human immunodeficiency virus infection1148863007
- Adult pityriasis rubra pilaris1254885000
- Juvenile pityriasis rubra pilaris1254920007
UMLS
- Devergie's diseaseC0032027
- Lichen ruber acuminatusC0032027
- PITYRIASIS RUBRA PILARISC0032027
- PRPC0032027
- PRP - Pityriasis rubra pilarisC0032027
- Pityriasis Rubra PilarisC0032027
- Pityriasis rubra pilarisC0032027
- Pityriasis rubra pilaris (disorder)C0032027
- devergie's diseaseC0032027
- pityriasis pilaris rubraC0032027
- pityriasis rubra pilarisC0032027
Clinical Terms
- pityriasis pilaris rubra
- PRP - Classical adult pityriasis rubra pilaris
- Pityriasis rubra pilaris (disorder)
- Classical adult pityriasis rubra pilaris
- Skin disease due to human immunodeficiency virus infection
- PRP - Type I pityriasis rubra pilaris
- PRP - Type V pityriasis rubra pilaris
- PRP - Atypical adult pityriasis rubra pilaris
- PRP - Type IV pityriasis rubra pilaris
- Type II pityriasis rubra pilaris
- PRP - Pityriasis rubra pilaris
- Classical juvenile pityriasis rubra pilaris
- Type IV pityriasis rubra pilaris
- PRP
- PRP - Type II pityriasis rubra pilaris
- Disorder of skin due to human immunodeficiency virus infection
- Type V pityriasis rubra pilaris
- Devergie's disease
- Atypical adult pityriasis rubra pilaris
- PRP - Atypical juvenile pityriasis rubra pilaris
- Pityriasis rubra pilaris due to human immunodeficiency virus infection
- Nail dystrophy due to pityriasis rubra pilaris
- Circumscribed juvenile pityriasis rubra pilaris
- PRP - Classical juvenile pityriasis rubra pilaris
- PRP - Type III pityriasis rubra pilaris
- Pityriasis rubra pilaris due to HIV infection
- Juvenile pityriasis rubra pilaris
- Atypical juvenile pityriasis rubra pilaris
- PRP - Circumscribed juvenile pityriasis rubra pilaris
- Type III pityriasis rubra pilaris
- Lichen ruber acuminatus
- Adult pityriasis rubra pilaris
- Type I pityriasis rubra pilaris
Frequently Asked Questions
What is the ICD-10 code for pityriasis rubra pilaris?
The ICD-10-CM code for pityriasis rubra pilaris is L44.0. The full clinical description is "Pityriasis rubra pilaris". L44.0 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code L44.0 mean?
ICD-10-CM code L44.0 represents “Pityriasis rubra pilaris”. It is classified under Chapter 12: Diseases of the Skin and Subcutaneous Tissue and is a billable/specific code that can be used on a claim.
Is L44.0 a billable code?
Yes, L44.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is L44.0 in?
L44.0 is in Chapter 12: Diseases of the Skin and Subcutaneous Tissue (codes L00-L99).
What SNOMED CT codes does L44.0 map to?
L44.0 maps to 11 SNOMED CT concepts: 1254885000, 238619006, 238622008, 238621001, 238618003, and 6 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for L44.0?
L44.0 is linked to 1 UMLS Concept Unique Identifier: C0032027. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does L44.0 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like pityriasis rubra pilaris affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of L44.0?
L44.0 maps to the ICD-11 code: EA94 (Pityriasis rubra pilaris).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.