L40.1
BillableGeneralized pustular psoriasis
Generalized pustular psoriasis
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Impetigo herpetiformis
- Von Zumbusch's disease
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •lipomelanotic reticulosisI89.8
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •systemic connective tissue disordersM30-M36
- •viral wartsB07
Related Codes(7)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(88)
SNOMED CT
- Generalised pustular psoriasis, exanthematous type28840001
- Generalized pustular psoriasis, exanthematous type28840001
- Vesicular eruption79893008
- Vesicular rash79893008
- Localised pustular psoriasis81271001
- Localized pustular psoriasis81271001
- Discoid psoriasis200965009
- Nummular psoriasis200965009
- Plaque psoriasis200965009
- Pustular psoriasis200973000
- Acute generalised pustular psoriasis238612002
- Acute generalized pustular psoriasis238612002
- Generalised pustular psoriasis238612002
- Generalised pustular psoriasis of von Zumbusch238612002
- Generalized pustular psoriasis238612002
- Generalized pustular psoriasis of von Zumbusch238612002
- Generalised pustular psoriasis of pregnancy238613007
- Generalized pustular psoriasis of pregnancy238613007
- Impetigo herpetiformis238613007
- Infantile pustular psoriasis238616004
- Circinate and annular pustular psoriasis238617008
- Exanthematous disorder238812004
- Bullous eruption271759003
- Acute generalised pustular psoriasis de novo402326008
- Acute generalized pustular psoriasis de novo402326008
- Acute generalised pustular flare of preexisting plaque psoriasis402327004
- Acute generalized pustular flare of preexisting plaque psoriasis402327004
- Acute blistering eruption of skin721542002
- Acute blistering skin eruption721542002
- Acute pustular eruption of skin1251376007
- Acute pustular skin eruption1251376007
- Acute pustular skin rash1251376007
- Plaque psoriasis with pustules1254867007
- Exacerbation of psoriasis1296646001
UMLS
- Acute generalised pustular psoriasisC0343055
- Acute generalized pustular psoriasisC0343055
- GPPC0343055
- Generalised pustular psoriasisC0343055
- Generalised pustular psoriasis of von ZumbuschC0343055
- Generalized Pustular PsoriasisC0343055
- Generalized pustular psoriasisC0343055
- Generalized pustular psoriasis (disorder)C0343055
- Generalized pustular psoriasis of von ZumbuschC0343055
- Pustular psoriasis, generalizedC0343055
- Von Zumbusch psoriasisC0343055
- generalized psoriasis pustularC0343055
- generalized pustular psoriasisC0343055
- Impetigo herpetiformisC1314968
- Von Zumbusch's diseaseC2888177
Clinical Terms
- Generalised pustular psoriasis of pregnancy
- Discoid psoriasis
- Acute pustular skin rash
- Generalized pustular psoriasis of pregnancy
- Circinate and annular pustular psoriasis
- Plaque psoriasis
- Acute pustular eruption of skin
- Von Zumbusch's disease
- generalized psoriasis pustular
- Acute generalised pustular flare of preexisting plaque psoriasis
- Generalised pustular psoriasis
- Bullous eruption
- Acute pustular skin eruption
- Generalized pustular psoriasis (disorder)
- Impetigo herpetiformis
- Generalized pustular psoriasis of von Zumbusch
- Exanthematous disorder
- Localised pustular psoriasis
- Acute generalised pustular psoriasis
- Infantile pustular psoriasis
- Acute generalised pustular psoriasis de novo
- Acute generalized pustular flare of preexisting plaque psoriasis
- Pustular psoriasis
- Acute generalized pustular psoriasis
- Vesicular eruption
- Generalised pustular psoriasis, exanthematous type
- Plaque psoriasis with pustules
- Pustular psoriasis, generalized
- Exacerbation of psoriasis
- Acute generalized pustular psoriasis de novo
- Localized pustular psoriasis
- GPP
- Generalized pustular psoriasis, exanthematous type
- Von Zumbusch psoriasis
- Nummular psoriasis
- Generalised pustular psoriasis of von Zumbusch
- Acute blistering skin eruption
- Acute blistering eruption of skin
- Vesicular rash
Frequently Asked Questions
What is the ICD-10 code for generalized pustular psoriasis?
The ICD-10-CM code for generalized pustular psoriasis is L40.1. The full clinical description is "Generalized pustular psoriasis". L40.1 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code L40.1 mean?
ICD-10-CM code L40.1 represents “Generalized pustular psoriasis”. It is classified under Chapter 12: Diseases of the Skin and Subcutaneous Tissue and is a billable/specific code that can be used on a claim.
Is L40.1 a billable code?
Yes, L40.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is L40.1 in?
L40.1 is in Chapter 12: Diseases of the Skin and Subcutaneous Tissue (codes L00-L99).
What SNOMED CT codes does L40.1 map to?
L40.1 maps to 17 SNOMED CT concepts: 721542002, 402327004, 238612002, 402326008, 1251376007, and 12 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for L40.1?
L40.1 is linked to 3 UMLS Concept Unique Identifiers: C0343055, C1314968, C2888177. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does L40.1 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like generalized pustular psoriasis affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of L40.1?
L40.1 maps to the ICD-11 code: EA90.40 (Generalised pustular psoriasis).
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.