J84.01
BillableAlveolar proteinosis
Alveolar proteinosis
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •smoke inhalationT59.81
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •lung diseases due to external agentsJ60-J70
Use Additional Code
Additional codes that should follow this code
Code Also
A second code may be required; sequencing depends on circumstances
- , if applicable, associated condition
Related Codes(3)
Also Known As / Clinical Terms(74)
SNOMED CT
- Alveolar proteinosis10501004
- PAP - Pulmonary alveolar proteinosis10501004
- Pulmonary alveolar lipoproteinosis10501004
- Pulmonary alveolar proteinosis10501004
- Proteinosis59714007
- Hypogammaglobulinaemia119250001
- Hypogammaglobulinemia119250001
- Congenital pulmonary alveolar proteinosis707442002
- Autoimmune pulmonary alveolar proteinosis707443007
- Secondary pulmonary alveolar proteinosis707510005
- 2'-5'-oligoadenylate synthetase 1-related infantile-onset pulmonary alveolar proteinosis, hypogammaglobulinaemia1197476009
- 2'-5'-oligoadenylate synthetase 1-related infantile-onset pulmonary alveolar proteinosis, hypogammaglobulinemia1197476009
- Infantile-onset pulmonary alveolar proteinosis, hypogammaglobulinaemia1197476009
- Infantile-onset pulmonary alveolar proteinosis, hypogammaglobulinemia1197476009
- OAS1-related infantile-onset pulmonary alveolar proteinosis, hypogammaglobulinaemia1197476009
- OAS1-related infantile-onset pulmonary alveolar proteinosis, hypogammaglobulinemia1197476009
- Hereditary pulmonary alveolar proteinosis with hepatic involvement1228876007
- Interstitial lung and liver disease1228876007
- Pulmonary alveolar proteinosis Reunion island type1228876007
- Severe early-onset pulmonary alveolar proteinosis due to MARS deficiency1228876007
- Severe early-onset pulmonary alveolar proteinosis due to methionyl-transfer ribonucleic acid synthetase 1 deficiency1228876007
UMLS
- ALVEOLAR PROTEINOSES PULMC0034050
- ALVEOLAR PROTEINOSIS PULMC0034050
- Alveolar Proteinoses, PulmonaryC0034050
- Alveolar Proteinosis, PulmonaryC0034050
- Alveolar proteinosisC0034050
- PAP - Pulmonary alveolar proteinosisC0034050
- PROTEINOSES PULM ALVEOLARC0034050
- PROTEINOSIS PULM ALVEOLARC0034050
- PULM ALVEOLAR PROTEINOSESC0034050
- PULM ALVEOLAR PROTEINOSISC0034050
- Proteinoses, Pulmonary AlveolarC0034050
- Proteinosis, Pulmonary AlveolarC0034050
- Pulmonary Alveolar ProteinosesC0034050
- Pulmonary Alveolar ProteinosisC0034050
- Pulmonary alveolar lipoproteinosisC0034050
- Pulmonary alveolar proteinosisC0034050
- Pulmonary alveolar proteinosis (disorder)C0034050
- alveolar proteinosisC0034050
- proteinosis alveolarC0034050
- pulmonary alveolar proteinosisC0034050
Clinical Terms
- Secondary pulmonary alveolar proteinosis
- Proteinosis, Pulmonary Alveolar
- 2'-5'-oligoadenylate synthetase 1-related infantile-onset pulmonary alveolar proteinosis, hypogammaglobulinaemia
- Pulmonary alveolar proteinosis (disorder)
- pulmonary alveolar proteinosis
- Congenital pulmonary alveolar proteinosis
- proteinosis alveolar
- Pulmonary alveolar proteinosis Reunion island type
- Interstitial lung and liver disease
- Hereditary pulmonary alveolar proteinosis with hepatic involvement
- Proteinosis
- 2'-5'-oligoadenylate synthetase 1-related infantile-onset pulmonary alveolar proteinosis, hypogammaglobulinemia
- OAS1-related infantile-onset pulmonary alveolar proteinosis, hypogammaglobulinemia
- Alveolar Proteinosis, Pulmonary
- Severe early-onset pulmonary alveolar proteinosis due to MARS deficiency
- Infantile-onset pulmonary alveolar proteinosis, hypogammaglobulinaemia
- Pulmonary alveolar lipoproteinosis
- OAS1-related infantile-onset pulmonary alveolar proteinosis, hypogammaglobulinaemia
- PULM ALVEOLAR PROTEINOSES
- Hypogammaglobulinemia
- ALVEOLAR PROTEINOSES PULM
- Autoimmune pulmonary alveolar proteinosis
- Infantile-onset pulmonary alveolar proteinosis, hypogammaglobulinemia
- Pulmonary Alveolar Proteinoses
- PAP - Pulmonary alveolar proteinosis
- Severe early-onset pulmonary alveolar proteinosis due to methionyl-transfer ribonucleic acid synthetase 1 deficiency
- PROTEINOSES PULM ALVEOLAR
- PULM ALVEOLAR PROTEINOSIS
- Proteinoses, Pulmonary Alveolar
- PROTEINOSIS PULM ALVEOLAR
- Hypogammaglobulinaemia
- ALVEOLAR PROTEINOSIS PULM
- Alveolar Proteinoses, Pulmonary
Frequently Asked Questions
What is the ICD-10 code for alveolar proteinosis?
The ICD-10-CM code for alveolar proteinosis is J84.01. The full clinical description is "Alveolar proteinosis". J84.01 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code J84.01 mean?
ICD-10-CM code J84.01 represents “Alveolar proteinosis”. It is classified under Chapter 10: Diseases of the Respiratory System and is a billable/specific code that can be used on a claim.
Is J84.01 a billable code?
Yes, J84.01 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is J84.01 in?
J84.01 is in Chapter 10: Diseases of the Respiratory System (codes J00-J99).
What codes cannot be used with J84.01?
J84.01 has Excludes1 notes indicating codes that cannot be used together with it, including: drug-induced interstitial lung disorders (J70.2-J70.4); interstitial emphysema (J98.2).
Are additional codes required with J84.01?
Yes, when using J84.01, also report: code, where applicable, to identify:; exposure to environmental tobacco smoke (Z77.22); exposure to tobacco smoke in the perinatal period (P96.81); history of tobacco dependence (Z87.891); occupational exposure to environmental tobacco smoke (Z57.31); tobacco dependence (F17.-); tobacco use (Z72.0).
What SNOMED CT codes does J84.01 map to?
J84.01 maps to 8 SNOMED CT concepts: 1197476009, 10501004, 707443007, 707442002, 1228876007, and 3 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for J84.01?
J84.01 is linked to 1 UMLS Concept Unique Identifier: C0034050. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does J84.01 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like alveolar proteinosis affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of J84.01?
There is no direct ICD-11 mapping available for J84.01 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.