AutoICD API

I78.0

Billable

Hereditary hemorrhagic telangiectasia

Hereditary hemorrhagic telangiectasia

Status

Billable / Specific

Block

I70-I79

Parent Code

I78

ICD-11 Mapping

1 equivalent

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Rendu-Osler-Weber disease

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(3)
I78.1

Nevus, non-neoplastic

BillableI78.8

Other diseases of capillaries

BillableI78.9

Disease of capillaries, unspecified

Billable
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

LA90.00Hereditary haemorrhagic telangiectasiaequivalentPrimary
Also Known As / Clinical Terms(158)

SNOMED CT

UMLS

Clinical Terms

  • Hereditary benign telangiectasia
  • Conjunctival telangiectasis
  • Epilepsy telangiectasia syndrome
  • osler rendu weber
  • osler weber rendu
  • Juvenile polyposis of intestine
  • rendu osler weber
  • Telangiectasia, Hereditary Hemorrhagic, of Rendu, Osler, and Weber
  • OSLER-RENDU-WEBER DISEASE
  • JP-HHT (juvenile polyposis with hereditary hemorrhagic telangiectasia) syndrome
  • Weber Osler Syndrome
  • rendu osler weber syndrome
  • Familial cutaneous telangiectasia and oropharyngeal cancer predisposition syndrome
  • osler weber rendu disease
  • Rendu Osler Weber Disease
  • Rendu-Osler-Weber syndrome
  • osler-weber-rendu disease
  • Hereditary haemorrhagic telangiectasia
  • osler-rendu-weber syndrome
  • HLTRS (hypotrichosis, lymphoedema, telangiectasia, renal defect) syndrome
  • Vascular abnormality of conjunctiva
  • Osler hemorrhagic telangiectasia syndrome (disorder)
  • rendu osler disease
  • Osler Rendu Weber Disease
  • Hereditary hemorrhagic telangiectasia of gingiva
  • JP-HHT (juvenile polyposis with hereditary haemorrhagic telangiectasia) syndrome
  • Osler haemorrhagic telangiectasia syndrome
  • hht
  • Hereditary haemorrhagic telangiectasia of gingiva
  • Hereditary dysplasia of blood vessel
  • Osler Rendu Disease
  • Shortened little finger
  • osler's disease
  • Osler Weber Rendu Syndrome
  • rendu weber osler disease
  • Osler hemorrhagic telangiectasia syndrome
  • Juvenile polyposis syndrome with hereditary hemorrhagic telangiectasia
  • Hemorrhagic Telangiectasia, Hereditary
  • Hypotrichosis, lymphedema, telangiectasia, renal defect syndrome
  • Conjunctival vascular abnormality
  • osler rendu syndrome weber
  • HHT - Hereditary hemorrhagic telangiectasia
  • rendu-osler-weber disease
  • Retention polyps of large bowel
  • Weber-Osler Disease
  • Juvenile polyps of large bowel
  • Weber-Osler Syndrome
  • Juvenile polyposis syndrome
  • Telangiectasia, Hereditary Hemorrahagic, of Rendu, Osler
  • OSLER RENDU DIS
  • HHT - Hereditary haemorrhagic telangiectasia
  • Abnormally short little finger
  • HLTRS (hypotrichosis, lymphedema, telangiectasia, renal defect) syndrome
  • Osler-Rendu Disease
  • Telangiectasia, Hereditary Hemorrhagic
  • ORW DISEASE
  • Osler Disease
  • Hypotrichosis, lymphoedema, telangiectasia, renal defect syndrome
  • disease osler weber rendu
  • Juvenile polyposis syndrome with hereditary haemorrhagic telangiectasia
  • rendu weber osler
  • disease rendu-osler-weber
  • Osler-Weber-Rendu syndrome
  • Weber Osler Disease
  • OSLER RENDU WEBER DIS
  • osler rendus syndrome weber
Frequently Asked Questions
What is the ICD-10 code for hereditary hemorrhagic telangiectasia?

The ICD-10-CM code for hereditary hemorrhagic telangiectasia is I78.0. The full clinical description is "Hereditary hemorrhagic telangiectasia". I78.0 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code I78.0 mean?

ICD-10-CM code I78.0 represents “Hereditary hemorrhagic telangiectasia”. It is classified under Chapter 9: Diseases of the Circulatory System and is a billable/specific code that can be used on a claim.

Is I78.0 a billable code?

Yes, I78.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is I78.0 in?

I78.0 is in Chapter 9: Diseases of the Circulatory System (codes I00-I99).

What SNOMED CT codes does I78.0 map to?

I78.0 maps to 12 SNOMED CT concepts: 897328006, 231870008, 74100001, 733032006, 782823001, and 7 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for I78.0?

I78.0 is linked to 1 UMLS Concept Unique Identifier: C0039445. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does I78.0 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like hereditary hemorrhagic telangiectasia affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of I78.0?

I78.0 maps to the ICD-11 code: LA90.00 (Hereditary haemorrhagic telangiectasia).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.