I67.5
BillableMoyamoya disease
Moyamoya disease
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •systemic connective tissue disordersM30-M36
- •transient cerebral ischemic attacks and related syndromesG45
- •sequelae of the listed conditionsI69.8
Use Additional Code
Additional codes that should follow this code
Related Codes(9)
I67.0Dissection of cerebral arteries, nonruptured
I67.1Cerebral aneurysm, nonruptured
I67.2Cerebral atherosclerosis
I67.3Progressive vascular leukoencephalopathy
I67.4Hypertensive encephalopathy
I67.6Nonpyogenic thrombosis of intracranial venous system
I67.7Cerebral arteritis, not elsewhere classified
I67.8Other specified cerebrovascular diseases
I67.9Cerebrovascular disease, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(78)
SNOMED CT
- Achalasia of cardia45564002
- Achalasia of esophagus45564002
- Achalasia of oesophagus45564002
- Cardiospasm45564002
- Lack of reflex relaxation of lower esophageal sphincter45564002
- Lack of reflex relaxation of lower oesophageal sphincter45564002
- Moyamoya disease69116000
- Congenital stenosis of carotid artery93396008
- ICA - Internal carotid artery stenosis233964008
- Internal carotid artery stenosis233964008
- Moyamoya disease with early onset achalasia718551002
- Moyamoya angiopathy, short stature, facial dysmorphism, hypergonadotropic hypogonadism syndrome724097003
- Moyamoya disease, short stature, facial dysmorphism, hypergonadotropic hypogonadism724097003
- Secondary moyamoya disease1208841001
- Intracranial carotid artery stenosis450440061000119108
- Stenosis of intracranial carotid artery450440061000119108
UMLS
- CEREBROVASCULAR MOYAMOYA DISC0026654
- Cerebrovascular Moyamoya DiseaseC0026654
- Cerebrovascular moyamoya diseaseC0026654
- Disease, Moya-MoyaC0026654
- MOYA MOYA DISC0026654
- MOYAMOYA DISC0026654
- Moya Moya DiseaseC0026654
- Moya-Moya DiseaseC0026654
- Moya-moya diseaseC0026654
- MoyamoyaC0026654
- Moyamoya DiseaseC0026654
- Moyamoya SyndromeC0026654
- Moyamoya diseaseC0026654
- Moyamoya disease (disorder)C0026654
- Moyamoya syndromeC0026654
- Progressive Intracranial Occlusive Arteropathy (Moyamoya)C0026654
- Progressive intracranial arterial occlusionC0026654
- Progressive intracranial arterial occlusion (disorder)C0026654
- Progressive intracranial occlusive arteropathyC0026654
- Spontaneous occlusion of the Circle of WillisC0026654
- Spontaneous occlusion of the circle of WillisC0026654
- disease moya moyaC0026654
- disease moyamoyaC0026654
- moya diseaseC0026654
- moya moya diseaseC0026654
- moya-moya diseaseC0026654
- moyamoyaC0026654
- moyamoya diseaseC0026654
- moyamoya syndromeC0026654
Clinical Terms
- Cardiospasm
- Moyamoya disease, short stature, facial dysmorphism, hypergonadotropic hypogonadism
- Intracranial carotid artery stenosis
- Moya-moya disease
- Moyamoya Syndrome
- disease moyamoya
- CEREBROVASCULAR MOYAMOYA DIS
- Disease, Moya-Moya
- disease moya moya
- Achalasia of cardia
- moya moya disease
- Moyamoya disease with early onset achalasia
- moyamoya
- MOYA MOYA DIS
- moya disease
- MOYAMOYA DIS
- Stenosis of intracranial carotid artery
- Spontaneous occlusion of the Circle of Willis
- Moyamoya disease (disorder)
- Moyamoya angiopathy, short stature, facial dysmorphism, hypergonadotropic hypogonadism syndrome
- Progressive intracranial occlusive arteropathy
- Secondary moyamoya disease
- Congenital stenosis of carotid artery
- Lack of reflex relaxation of lower esophageal sphincter
- Achalasia of oesophagus
- Lack of reflex relaxation of lower oesophageal sphincter
- ICA - Internal carotid artery stenosis
- Achalasia of esophagus
- Progressive intracranial arterial occlusion
- Cerebrovascular moyamoya disease
- Internal carotid artery stenosis
- Progressive Intracranial Occlusive Arteropathy (Moyamoya)
- Progressive intracranial arterial occlusion (disorder)
Frequently Asked Questions
What is the ICD-10 code for moyamoya disease?
The ICD-10-CM code for moyamoya disease is I67.5. The full clinical description is "Moyamoya disease". I67.5 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code I67.5 mean?
ICD-10-CM code I67.5 represents “Moyamoya disease”. It is classified under Chapter 9: Diseases of the Circulatory System and is a billable/specific code that can be used on a claim.
Is I67.5 a billable code?
Yes, I67.5 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is I67.5 in?
I67.5 is in Chapter 9: Diseases of the Circulatory System (codes I00-I99).
What codes cannot be used with I67.5?
I67.5 has Excludes1 notes indicating codes that cannot be used together with it, including: traumatic intracranial hemorrhage (S06.-); Occlusion and stenosis of cerebral artery causing cerebral infarction (I63.3-I63.5-); Occlusion and stenosis of precerebral artery causing cerebral infarction (I63.2-).
Are additional codes required with I67.5?
Yes, when using I67.5, also report: presence of:; alcohol abuse and dependence (F10.-); exposure to environmental tobacco smoke (Z77.22); history of tobacco dependence (Z87.891); hypertension (I10-I1A); occupational exposure to environmental tobacco smoke (Z57.31); tobacco dependence (F17.-); tobacco use (Z72.0).
What SNOMED CT codes does I67.5 map to?
I67.5 maps to 8 SNOMED CT concepts: 45564002, 93396008, 233964008, 450440061000119108, 724097003, and 3 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for I67.5?
I67.5 is linked to 1 UMLS Concept Unique Identifier: C0026654. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does I67.5 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like moyamoya disease affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of I67.5?
I67.5 maps to the ICD-11 code: 8B22.B (Moyamoya syndrome).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.