H90.5
BillableUnspecified sensorineural hearing loss
Unspecified sensorineural hearing loss
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Central hearing loss NOS
- Congenital deafness NOS
- Neural hearing loss NOS
- Perceptive hearing loss NOS
- Sensorineural deafness NOS
- Sensory hearing loss NOS
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
Related Codes(9)
H90.0Conductive hearing loss, bilateral
H90.1Conductive hear loss, uni w unrestricted hear cntra side
H90.2Conductive hearing loss, unspecified
H90.3Sensorineural hearing loss, bilateral
H90.4Sensorineural hear loss, uni w unrestricted hear cntra side
H90.6Mixed conductive and sensorineural hearing loss, bilateral
H90.7Mixed cndct/snrl hear loss, uni w unrestr hear cntra side
H90.8Mixed conductive and sensorineural hearing loss, unspecified
H90.ACndct/snrl hearing loss with restricted hear cntra side
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(996)
SNOMED CT
- Autosomal dominant KID (keratitis, ichthyosis, deafness) syndrome2625009
- Autosomal dominant keratitis, ichthyosis, deafness syndrome2625009
- Senter syndrome2625009
- Diabetes mellitus associated with genetic syndrome5969009
- Genetic syndromes of diabetes mellitus5969009
- 10p partial monosomy syndrome6002006
- Complete deafness8531006
- BADS syndrome10170007
- Black locks, oculocutaneous albinism, AND deafness of the sensorineural type10170007
- Hereditary sensory neuropathy11442006
- Posterior sensory radicular neuropathy11442006
- Thiamine-responsive megaloblastic anaemia12907000
- Thiamine-responsive megaloblastic anemia12907000
- Pili torti17170005
- Twisted hair17170005
- Eyes wide apart22006008
- Eyes widely set22006008
- Hypertelorism22006008
- Orbital hypertelorism22006008
- Orbital separation excessive22006008
- Congenital absence of proximal portion of limb22841008
- Phocomelia22841008
- Phocomelic dwarf22841008
- Congenital dilatation of colon24291004
- Congenital megacolon24291004
- OA - Ocular albinism26399002
- Ocular albinism26399002
- Deficient secretion of all pituitary hormones32390006
- Panhypopituitarism32390006
- Primary hypopituitarism32390006
- Simmond's disease32390006
- Simmonds' disease32390006
- Congenital pernicious anaemia34925000
- Congenital pernicious anemia34925000
- Megaloblastic anaemia due to inborn errors of metabolism34925000
- Megaloblastic anemia due to inborn errors of metabolism34925000
- Primary hypersomnia36124002
- Achalasia of cardia45564002
- Achalasia of esophagus45564002
- Achalasia of oesophagus45564002
- Cardiospasm45564002
- Lack of reflex relaxation of lower esophageal sphincter45564002
- Lack of reflex relaxation of lower oesophageal sphincter45564002
- End organ deafness56943007
- Retinitis pigmentosa-deafness syndrome57838006
- Usher syndrome57838006
- Usher's syndrome57838006
- Gingival fibromatosis58569000
- Duane retraction syndrome60318001
- Duane syndrome60318001
- Duane's retraction syndrome60318001
- Duane's syndrome60318001
- Eye retraction syndrome60318001
- Stilling-Turk-Duane syndrome60318001
- Gelineau's syndrome60380001
- Narcolepsy60380001
- Narcoleptic syndrome60380001
- Paroxysmal sleep60380001
- Neurosensory deafness60700002
- PD - Perceptive deafness60700002
- Perceptive deafness60700002
- Perceptive hearing loss60700002
- SND - Sensorineural deafness60700002
- SNHL - Sensorineural hearing loss60700002
- Sensorineural deafness60700002
- Sensorineural hearing loss60700002
- Sensory-neural deafness60700002
- Sensory-neural hearing loss60700002
- Sensorineural hearing loss of combined sites65680009
- Dejerine-Thomas syndrome67761004
- Déjérine-Thomas syndrome67761004
- OPCA - Olivopontocerebellar atrophy67761004
- Olivocerebellar atrophy67761004
- Olivopontocerebellar atrophy67761004
- Olivopontocerebellar degeneration67761004
- Thomas' syndrome67761004
- Bjornstad's syndrome67817003
- Björnstad syndrome67817003
- Deafness, pili torti, hypogonadism syndrome67817003
- Hearing loss, pili torti, hypogonadism syndrome67817003
- Pili torti-deafness syndrome67817003
- Central auditory dysfunction68467004
- Central deafness68467004
- Central hearing loss68467004
- DIDMOAD (diabetes insipidus, diabetes mellitus, optic atrophy, deafness) syndrome70694009
- DIDMOAD syndrome70694009
- Marquardt-Loriaux syndrome70694009
- Wolfram syndrome70694009
- Congenital humpback71311003
- Congenital hunchback71311003
- Congenital kyphosis71311003
- Macrodontia71485000
- Macrodontism71485000
- Megadontia71485000
- Megalodontia71485000
- Nerve conduction deafness73371001
- Nerve deafness73371001
- Neural hearing loss73371001
- Retrocochlear hearing loss73371001
- Micromelia74370006
- Micromelic dwarf74370006
- Micromelus74370006
- Nanomelia74370006
- Multiple malformation syndrome, moderate short stature, facial77701002
- Multiple malformation syndrome, moderate short stature, facial with or without genital features77701002
- Sudden hearing loss79471008
- Cochlear hearing loss85571008
- Inner ear hearing loss85571008
- Sensory hearing loss85571008
- Benign neoplasm of sacrococcygeal region92331005
- Gonadal dysgenesis with auditory dysfunction, autosomal recessive inheritance93466004
- Gonadal dysgenesis with sensorineural deafness, autosomal recessive inheritance93466004
- Perrault syndrome93466004
- Sensory neuropathy95662005
- Congenital hearing disorder95827002
- Congenital deafness95828007
- Hereditary fibrous enlargement of gingiva109620006
- Hereditary gingival fibromatosis109620006
- Duane syndrome, type 3128084001
- Duane's syndrome, type 3128084001
- CRB - Congenital retinal blindness193413001
- Congenital retinal blindness193413001
- Leber amaurosis193413001
- Leber congenital amaurosis193413001
- Leber's amaurosis193413001
- Combined perceptive hearing loss194426007
- Dentinogenesis imperfecta196286005
- Hereditary opalescent dentin196286005
- Congenital preauricular fistula204272007
- Fistula auris congenita204272007
- Preauricular fistula204272007
- Preauricular sinus204272007
- Anal atresia204712000
- Aproctia204712000
- Atresia ani204712000
- Congenital atresia of anus204712000
- Congenital imperforate anus204712000
- Imperforate anus204712000
- Chronic deafness232325008
- Dominant sensorineural hearing loss232328005
- X-linked sensorineural hearing loss232329002
- Recessive sensorineural hearing loss232330007
- Postnatal acquired sensorineural hearing loss232332004
- SRNS - Steroid-resistant nephrotic syndrome236381000
- Steroid-resistant nephrotic syndrome236381000
- Steroid-unresponsive nephrotic syndrome236381000
- Albright's renal tubular acidosis236461000
- Classic distal renal tubular acidosis236461000
- Distal renal tubular acidosis236461000
- RTA (renal tubular acidosis) type I236461000
- Type I renal tubular acidosis236461000
- AR dRTA (autosomal recessive distal renal tubular acidosis) with deafness236532003
- Autosomal recessive distal renal tubular acidosis with deafness236532003
- Renal tubular acidosis with deafness236532003
- Renal tubular acidosis with progressive nerve deafness236532003
- Male infertility of chromosomal origin236791009
- Megaloblastic anaemia, thiamine-responsive, with diabetes mellitus and sensorineural deafness237617006
- Megaloblastic anemia, thiamine-responsive, with diabetes mellitus and sensorineural deafness237617006
- Rogers syndrome237617006
- Thiamine-responsive megaloblastic anaemia syndrome237617006
- Thiamine-responsive megaloblastic anemia syndrome237617006
- Ballinger-Wallace syndrome237619009
- Diabetes-deafness syndrome maternally transmitted237619009
- MIDD - maternally inherited diabetes and deafness237619009
- Maternally inherited diabetes and deafness237619009
- Maternally-inherited diabetes and hearing loss237619009
- Mitochondrial diabetes237619009
- Cutaneous syndrome with ichthyosis239057002
- Ichthyosis hystrix Rheydt type239059004
- KID syndrome239059004
- KID/HID syndrome239059004
- KIDS - Keratitis ichthyosis and deafness syndrome239059004
- Keratitis ichthyosis and deafness syndrome239059004
- Keratitis ichthyosis deafness syndrome239059004
- Keratitis, ichthyosis, deafness/hystrix-like ichthyosis deafness syndrome239059004
- Congenital calyceal diverticulum253875000
- Congenital nephritis276585000
- Dead ear - postoperative277424008
- Postoperative profound sensorineural hearing loss277424008
- 3-Methylglutaconic aciduria type 4297233004
- Lipoma of lower back307754008
- Premature canities387833009
- Premature graying387833009
- Premature grayness of hair387833009
- Premature greying387833009
- Premature greyness of hair387833009
- Autosomal dominant ichthyosis402770002
- Heritable disorder of neutrophil function402794002
- Autosomal recessive KID (keratitis, ichthyosis, deafness) syndrome403780007
- Autosomal recessive keratitis-ichthyosis-deafness syndrome403780007
- Congenital kyphoscoliosis405772002
- CHED-congenital hereditary endothelial dystrophy417651000
- Congenital hereditary endothelial dystrophy417651000
- Generalised dystonia425492002
- Generalized dystonia425492002
- Asymmetric hearing loss427772009
- Asymmetrical hearing loss427772009
- Autoimmune sensorineural hearing loss428470000
- Asymmetric sensorineural hearing loss428887009
- Asymmetrical sensorineural hearing loss428887009
- Calyceal diverticulum433036004
- Diverticulum of renal calyx433036004
- Acquired sensorineural hearing loss609125008
- Essential tremor609558009
- Hereditary essential tremor609559001
- Congenital prelingual deafness699238006
- Congenital achalasia of esophagus700283004
- Congenital achalasia of oesophagus700283004
- Congenital sensorineural deafness700453005
- Congenital sensorineural hearing loss700453005
- Dead ear700454004
- Profound sensorineural hearing loss700454004
- Chromosome 15q15.3 deletion syndrome700489002
- Deafness infertility syndrome700489002
- Sensorineural deafness and male infertility700489002
- Craniofacial deafness hand syndrome702362004
- Sommer Young Wee Frye syndrome702362004
- Deafness-dystonia syndrome702423009
- Deafness-dystonia-optic neuronopathy syndrome702423009
- Mohr-Tranebjaerg syndrome702423009
- Arts syndrome702441001
- Fatal X-linked ataxia with deafness and loss of vision702441001
- Lethal ataxia-deafness-optic atrophy702441001
- Globodontia707310009
- 3-methylglutaconic aciduria type IV with sensorineural deafness, encephalopathy and Leigh-like syndrome711409002
- 3-methylglutaconic aciduria with deafness, encephalopathy, Leigh-like syndrome711409002
- 3-methylglutaconic aciduria with hearing loss, encephalopathy, Leigh-like syndrome711409002
- MEGDEL syndrome711409002
- Sudden sensorineural hearing loss715239002
- Olivopontocerebellar atrophy and deafness715483009
- Olivopontocerebellar atrophy co-occurrent with sensorineural hearing loss715483009
- Phocomelia, ectrodactyly, deafness and sinus arrhythmia syndrome715506001
- Stoll Lévy Francfort syndrome715506001
- Deafness and oligodontia syndrome715527006
- Colobomatous microphthalmia715771008
- Microphthalmia with colobomatous cyst715771008
- Microphthalmos co-occurrent with congenital ocular coloboma715771008
- Cleft palate and cleft lip with deafness and sacral lipoma syndrome716007007
- Lowry Yong syndrome716007007
- Kawashima Tsuji syndrome716112005
- Microcephaly with deafness and intellectual disability syndrome716112005
- Deafness with cataract and skeletal anomaly syndrome716170005
- Nathalie syndrome716170005
- Short stature and deafness with neutrophil dysfunction and facial dysmorphism syndrome716192009
- Thong Douglas Ferrante syndrome716192009
- Chitty Hall Baraitser syndrome716238003
- Deafness with epiphyseal dysplasia and short stature syndrome716238003
- Hearing loss and salivary gland insensitivity to aldosterone syndrome716239006
- Tungland Bellman syndrome716239006
- Deafness with malformation of ear and facial palsy syndrome716243005
- Sellars Beighton syndrome716243005
- Deafness craniofacial syndrome716245003
- Ehlers-Danlos syndrome kyphoscoliotic type718211004
- Ehlers-Danlos syndrome type 6718211004
- Ehlers-Danlos syndrome type VI718211004
- Deafness and hypogonadism syndrome718714006
- Spondyloepiphyseal dysplasia MacDermot type718763005
- Spondyloepiphyseal dysplasia with myopia and sensorineural deafness syndrome718763005
- Congenital cataract with ataxia and deafness syndrome719102004
- Progressive sensorineural deafness and hypertrophic cardiomyopathy syndrome719272007
- Progressive sensorineural hearing loss and hypertrophic cardiomyopathy syndrome719272007
- Autosomal recessive deafness onychodystrophy syndrome719800009
- DOOR syndrome719800009
- DOORS syndrome719800009
- Deafness, onychodystrophy, osteodystrophy, intellectual disability syndrome719800009
- CAPOS (cerebellar ataxia, areflexia, pes cavus, optic atrophy, sensorineural hearing loss) syndrome720634003
- Cerebellar ataxia, areflexia, pes cavus, optic atrophy, sensorineural hearing loss syndrome720634003
- Congenital hereditary endothelial dystrophy and perceptive deafness syndrome720749004
- Corneal dystrophy and perceptive deafness syndrome720749004
- Corneal dystrophy with progressive deafness720749004
- Harboyan syndrome720749004
- Ehlers-Danlos syndrome kyphoscoliotic and deafness type720859009
- Ehlers-Danlos syndrome kyphoscoliotic and hearing loss type720859009
- Ehlers-Danlos syndrome with progressive kyphoscoliosis, myopathy, and deafness720859009
- Kyphoscoliotic Ehlers-Danlos syndrome due to FKBP22 deficiency720859009
- Deafness, genital anomaly, metacarpal and metatarsal synostosis syndrome721086004
- Pfeiffer Kapferer syndrome721086004
- Dentinogenesis imperfecta, short stature, hearing loss, intellectual disability syndrome721089006
- Developmental malformation, deafness, dystonia syndrome721092005
- EAST (epilepsy, ataxia, sensorineural deafness, and tubulopathy) syndrome721207002
- SESAME (seizures, sensorineural deafness, ataxia, mental retardation, electrolyte imbalance) syndrome721207002
- SESAME syndrome721207002
- Seizure, sensorineural deafness, ataxia, intellectual disability, electrolyte imbalance syndrome721207002
- Hirschsprung disease with deafness and polydactyly syndrome721221000
- Santos Mateus Leal syndrome721221000
- Ocular albinism with late-onset sensorineural deafness722054007
- Severe X-linked intellectual disability Gustavson type722213009
- Albinism with deafness syndrome722285005
- Autosomal dominant cerebellar ataxia, deafness and narcolepsy syndrome722293005
- Congenital cataract with deafness and hypogonadism syndrome722378009
- Schaap Taylor Baraitser syndrome722378009
- Gingival fibromatosis with progressive deafness syndrome722449007
- Jones syndrome722449007
- Distal renal tubular acidosis co-occurrent with sensorineural deafness722468005
- Congenital atrophy of optic nerve722990003
- Congenital optic atrophy722990003
- Neuropathy with hearing impairment723497003
- Peripheral neuropathy with sensorineural hearing impairment syndrome723497003
- Sensorineural hearing loss, early graying, essential tremor syndrome723721007
- Sensorineural hearing loss, early greying, essential tremor syndrome723721007
- Sensorineural deafness with dilated cardiomyopathy syndrome723993005
- Retinitis pigmentosa, deafness, mental retardation, hypogonadism syndrome724001005
- Retinitis pigmentosa, intellectual disability, deafness, hypogenitalism syndrome724001005
- Braun Bayer syndrome724092009
- Nephrosis, deafness, urinary tract, digital malformation syndrome724092009
- Maternally inherited cardiomyopathy and deafness724173009
- Maternally inherited cardiomyopathy and hearing loss syndrome724173009
- Barakat syndrome724282009
- HDR (hypoparathyroidism, sensorineural deafness, renal disease) syndrome724282009
- HDR syndrome724282009
- Hypoparathyroidism, deafness, renal disease syndrome724282009
- Neutropenia, monocytopenia, deafness syndrome725137007
- Deletion of part of chromosome 10726380001
- Deletion of part of chromosome 11726381002
- Ectodermal dysplasia and sensorineural deafness syndrome732953008
- Deafness, vitiligo, achalasia syndrome733069009
- Profound acquired hearing loss737050003
- Congenital conductive hearing loss737344003
- Charcot-Marie-Tooth disease, deafness, intellectual disability syndrome763136000
- Hereditary motor and sensory neuropathy with deafness, intellectual disability and absent sensory large myelinated fibers763136000
- Hereditary motor and sensory neuropathy with deafness, intellectual disability and absent sensory large myelinated fibres763136000
- Deafness, encephaloneuropathy, obesity, valvulopathy syndrome763688008
- Hearing loss, encephaloneuropathy, obesity, valvulopathy syndrome763688008
- Keipert syndrome763774001
- Nasodigitoacoustic syndrome763774001
- Deafness, nephritis, anorectal malformation syndrome766249007
- Lowe Kohn Cohen syndrome766249007
- Epiphyseal dysplasia, hearing loss, dysmorphism syndrome766870005
- Finucane Kurtz Scott syndrome766870005
- Severe motor and intellectual disabilities, sensorineural deafness, dystonia syndrome770751003
- Sinoatrial node dysfunction and deafness770784003
- Oculootodental syndrome770944002
- Non-acquired combined pituitary hormone deficiency, deafness, rigid cervical spine syndrome771308008
- Non-acquired combined pituitary hormone deficiency, sensorineural hearing loss, spine abnormalities syndrome771308008
- Congenital cataract, progressive muscular hypotonia, deafness, developmental delay syndrome773398005
- Congenital cataract, progressive muscular hypotonia, hearing loss, developmental delay syndrome773398005
- MDP (mandibular hypoplasia, deafness, progeroid) syndrome773406003
- Mandibular hypoplasia, deafness, progeroid syndrome773406003
- Mandibular hypoplasia, hearing loss, progeroid syndrome773406003
- Aphonia, deafness, retinal dystrophy, bifid halluces, intellectual disability syndrome773583007
- Aphonia, deafness, retinal dystrophy, duplicated halluces, intellectual disability syndrome773583007
- Aphonia, hearing loss, retinal dystrophy, duplicated halluces, intellectual disability syndrome773583007
- Nephrotic syndrome, deafness, pretibial epidermolysis bullosa syndrome773647007
- Nephrotic syndrome, hearing loss, pretibial epidermolysis bullosa syndrome773647007
- Congenital cataract, deafness, severe developmental delay syndrome773648002
- Congenital cataract, hearing loss, severe developmental delay syndrome773648002
- Lethal neurodegenerative disorder due to copper transport defect773648002
- Hypogonadotropic hypogonadism, severe microcephaly, sensorineural deafness, dysmorphism syndrome773665006
- Hypogonadotropic hypogonadism, severe microcephaly, sensorineural hearing loss, dysmorphism syndrome773665006
- HPPD (hypertelorism, preauricular sinus, punctual pits, deafness) syndrome773667003
- Hypertelorism, preauricular sinus, punctual pits, deafness syndrome773667003
- Hypertelorism, preauricular sinus, punctual pits, hearing loss syndrome773667003
- Deafness with onychodystrophy syndrome773735007
- Gemignani syndrome782690007
- Spinocerebellar ataxia, amyotrophy, deafness syndrome782690007
- Renal caliceal diverticuli and deafness syndrome782942003
- Hypotrichosis and deafness syndrome783555001
- Familial steroid-resistant nephrotic syndrome with sensorineural deafness783614008
- Oligodontia787414001
- Selective tooth agenesis787414001
- Auditory synaptopathy788873009
- Diabetes, hypogonadism, deafness, intellectual disability syndrome816067005
- Woodhouse Sakati syndrome816067005
- Congenital corneal dystrophy1003408005
- Congenital dystrophy of cornea1003408005
- Neural hearing loss of left ear1010229008
- Neural hearing loss of right ear1010230003
- Retinitis pigmentosa-deafness syndrome type 31010610007
- Usher syndrome type 31010610007
- Sensorineural hearing loss of right ear1119386008
- Sensorineural hearing loss of left ear1119387004
- Late congenital syphilitic sensorineural deafness1142112002
- Sensorineural deafness due to late congenital syphilis1142112002
- DIAPH1-related sensorineural deafness, thrombocytopenia syndrome1172604004
- DIAPH1-related sensorineural hearing loss-thrombocytopenia syndrome1172604004
- Diaphanous related formin 1 related sensorineural hearing loss, thrombocytopenia syndrome1172604004
- Retinitis pigmentosa, deafness, premature ageing, short stature, facial dysmorphism syndrome1172605003
- Retinitis pigmentosa, deafness, premature aging, short stature, facial dysmorphism syndrome1172605003
- Retinitis pigmentosa, hearing loss, premature ageing, short stature, facial dysmorphism syndrome1172605003
- Retinitis pigmentosa, hearing loss, premature aging, short stature, facial dysmorphism syndrome1172605003
- Maternal perinatal sensorineural hearing loss1179361001
- Neonatal sensorineural hearing loss1179362008
- Hereditary growth hormone deficiency1186807002
- Non-syndromic mitochondrial sensorineural deafness1187512003
- Autosomal dominant deafness with onychodystrophy syndrome1208614008
- Autosomal dominant hearing loss, onychodystrophy syndrome1208614008
- DDOD (dominant deafness onychodystrophy) syndrome1208614008
- CAGSSS - cataract, growth hormone deficiency, sensory neuropathy, sensorineural hearing loss, skeletal dysplasia syndrome1220595008
- Cataract, growth hormone deficiency, sensory neuropathy, sensorineural hearing loss, skeletal dysplasia syndrome1220595008
- PCNA-related progressive neurodegenerative photosensitivity syndrome1228871002
- Proliferating cell nuclear antigen-related progressive neurodegenerative photosensitivity syndrome1228871002
- Autosomal dominant myopia, midfacial retrusion, sensorineural deafness, rhizomelic dysplasia syndrome1229999001
- Autosomal dominant myopia, midfacial retrusion, sensorineural hearing loss, rhizomelic dysplasia syndrome1229999001
- Duane retraction syndrome with congenital deafness1230014007
- Duane retraction syndrome with congenital hearing loss1230014007
- Profound hearing loss1230412003
- Lichtenstein Knorr syndrome1237413006
- Progressive autosomal recessive ataxia, deafness syndrome1237413006
- Progressive autosomal recessive cerebellar ataxia, sensorineural hearing loss syndrome1237413006
- SCAR19 - spinocerebellar ataxia, autosomal recessive 191237413006
- Microcephaly, intellectual disability, sensorineural deafness, epilepsy, abnormal muscle tone syndrome1254651003
- Microcephaly, intellectual disability, sensorineural hearing loss, epilepsy, abnormal muscle tone syndrome1254651003
- Syndromic sensorineural deafness due to COXPD (combined oxidative phosphorylation defect)1260133007
- Syndromic sensorineural deafness due to combined oxidative phosphorylation defect1260133007
- Syndromic sensorineural hearing loss due to COXPD (combined oxidative phosphorylation defect)1260133007
- High frequency sensorineural hearing loss1268415009
- High tone sensorineural hearing loss1268415009
- Low frequency sensorineural hearing loss1268466004
- Low tone sensorineural hearing loss1268466004
- Liberfarb syndrome1284851009
- Short stature, skeletal dysplasia, retinal degeneration, intellectual disability, sensorineural hearing loss syndrome1284851009
- WFS1 - Wolfram syndrome-11285518004
- Wolfram syndrome type 11285518004
- Wolfram syndrome type I1285518004
- WFS2 - Wolfram syndrome-21285519007
- Wolfram syndrome type 21285519007
- Wolfram syndrome type II1285519007
- Adult-onset progressive leucoencephalopathy, early-onset deafness1299152003
- Adult-onset progressive leucoencephalopathy, early-onset hearing loss1299152003
- Adult-onset progressive leukoencephalopathy, early-onset deafness1299152003
- Adult-onset progressive leukoencephalopathy, early-onset hearing loss1299152003
- COMMAD (coloboma, osteopetrosis, microphthalmia, macrocephaly, albinism, deafness) syndrome1332382002
- COMMAD syndrome1332382002
- Coloboma, osteopetrosis, microphthalmia, macrocephaly, albinism, deafness syndrome1332382002
- SHILCA syndrome1356736002
- Spondyloepiphyseal dysplasia, sensorineural hearing loss, intellectual disability, Leber congenital amaurosis syndrome1356736002
- Body height below reference range1363478003
- Bilateral optic atrophy of eyes15632891000119109
- Optic atrophy of bilateral eyes15632891000119109
- Optic atrophy of both eyes15632891000119109
- Congenital osteodystrophy5731000119108
- High frequency sensorineural hearing loss in right ear1091541000119108
- Sensorineural hearing loss in left ear23631000119109
- Sensorineural hearing loss in right ear23641000119100
UMLS
- Central Hearing LossC0018776
- Central deafnessC0018776
- Central hearing lossC0018776
- Central hearing loss (disorder)C0018776
- Central hearing loss NOSC0018776
- Deafness, centralC0018776
- Hearing Loss, CentralC0018776
- central hearing lossC0018776
- Cochlear Hearing LossC1691779
- Cochlear hearing lossC1691779
- Hearing Loss, CochlearC1691779
- Inner ear hearing lossC1691779
- Sensory Hearing LossC1691779
- Sensory hearing lossC1691779
- Sensory hearing loss (disorder)C1691779
- Sensory hearing loss NOSC1691779
- Cochlear nerve deafnessC0155550
- Deafness nerveC0155550
- Deafness nerve typeC0155550
- Hearing Loss, RetrocochlearC0155550
- Nerve conduction deafnessC0155550
- Nerve deafnessC0155550
- Neural deafnessC0155550
- Neural hearing lossC0155550
- Neural hearing loss (disorder)C0155550
- Neural hearing loss NOSC0155550
- Retrocochlear Hearing LossC0155550
- Retrocochlear hearing lossC0155550
- nerve conduction deafnessC0155550
- nerve deafnessC0155550
- neural deafnessC0155550
- neural hearing lossC0155550
- Congenital deafnessC0339789
- Congenital deafness (disorder)C0339789
- Congenital deafness NOSC0339789
- Congenital hearing lossC0339789
- Deafness congenitalC0339789
- Deafness, congenitalC0339789
- Hearing loss, congenitalC0339789
- Hereditary deafnessC0339789
- congenital deafnessC0339789
- congenital hearing lossC0339789
- hereditary deafnessC0339789
- Deafness NeurosensoryC0018784
- Deafness, NeurosensoryC0018784
- Deafness, SensoryneuralC0018784
- Deafness, sensorineuralC0018784
- Deafnesses, NeurosensoryC0018784
- Deafnesses, SensoryneuralC0018784
- Hearing Loss, SensorineuralC0018784
- Hearing impairment, sensorineuralC0018784
- Hearing loss, perceptiveC0018784
- Hearing loss, sensorineuralC0018784
- Neuro sensory deafnessC0018784
- Neurosensory DeafnessC0018784
- Neurosensory DeafnessesC0018784
- Neurosensory deafnessC0018784
- PD - Perceptive deafnessC0018784
- Perceptive deafnessC0018784
- Perceptive hearing lossC0018784
- Perceptive hearing loss NOSC0018784
- SND - Sensorineural deafnessC0018784
- SNHL - Sensorineural hearing lossC0018784
- Sensorineural DeafnessC0018784
- Sensorineural Hearing LossC0018784
- Sensorineural deafnessC0018784
- Sensorineural deafness NOSC0018784
- Sensorineural hearing impairmentC0018784
- Sensorineural hearing lossC0018784
- Sensorineural hearing loss (disorder)C0018784
- Sensorineural hearing loss, unspecifiedC0018784
- Sensory-neural deafnessC0018784
- Sensory-neural hearing lossC0018784
- Sensoryneural DeafnessC0018784
- Sensoryneural DeafnessesC0018784
- Unspecified sensorineural hearing lossC0018784
- hearing loss sensori neuralC0018784
- hearing loss sensorineuralC0018784
- inner ear hearing lossC0018784
- perceptive deafnessC0018784
- sensorineural deafnessC0018784
- sensorineural hearing lossC0018784
- sensorineural hearing lossesC0018784
- sensory hearing lossC0018784
- sensory neuro deafnessC0018784
Clinical Terms
- Cutaneous syndrome with ichthyosis
- Congenital conductive hearing loss
- Genetic syndromes of diabetes mellitus
- Complete deafness
- OPCA - Olivopontocerebellar atrophy
- Steroid-resistant nephrotic syndrome
- Congenital hereditary endothelial dystrophy and perceptive deafness syndrome
- nerve conduction deafness
- Progressive sensorineural deafness and hypertrophic cardiomyopathy syndrome
- Asymmetrical sensorineural hearing loss
- Ehlers-Danlos syndrome with progressive kyphoscoliosis, myopathy, and deafness
- Maternal perinatal sensorineural hearing loss
- Retinitis pigmentosa, deafness, premature aging, short stature, facial dysmorphism syndrome
- Micromelic dwarf
- KIDS - Keratitis ichthyosis and deafness syndrome
- Aproctia
- Diabetes-deafness syndrome maternally transmitted
- Ichthyosis hystrix Rheydt type
- Sensory neuropathy
- Proliferating cell nuclear antigen-related progressive neurodegenerative photosensitivity syndrome
- Essential tremor
- Simmonds' disease
- Deafness, pili torti, hypogonadism syndrome
- Mandibular hypoplasia, deafness, progeroid syndrome
- Selective tooth agenesis
- Autosomal dominant KID (keratitis, ichthyosis, deafness) syndrome
- Bilateral optic atrophy of eyes
- CAGSSS - cataract, growth hormone deficiency, sensory neuropathy, sensorineural hearing loss, skeletal dysplasia syndrome
- inner ear hearing loss
- 3-methylglutaconic aciduria with hearing loss, encephalopathy, Leigh-like syndrome
- Optic atrophy of both eyes
- Asymmetric hearing loss
- Sensorineural hearing loss of combined sites
- Central hearing loss
- Non-syndromic mitochondrial sensorineural deafness
- Achalasia of cardia
- Premature grayness of hair
- Premature canities
- Sensorineural hearing impairment
- Deafness Neurosensory
- Sensory hearing loss
- Sensory hearing loss (disorder)
- hearing loss sensorineural
- CAPOS (cerebellar ataxia, areflexia, pes cavus, optic atrophy, sensorineural hearing loss) syndrome
- MEGDEL syndrome
- Congenital hearing disorder
- Craniofacial deafness hand syndrome
- PD - Perceptive deafness
- Hypogonadotropic hypogonadism, severe microcephaly, sensorineural deafness, dysmorphism syndrome
- Hearing Loss, Central
- Paroxysmal sleep
- Hearing loss, pili torti, hypogonadism syndrome
- Ocular albinism with late-onset sensorineural deafness
- Deafness with malformation of ear and facial palsy syndrome
- Macrodontia
- Combined perceptive hearing loss
- Short stature, skeletal dysplasia, retinal degeneration, intellectual disability, sensorineural hearing loss syndrome
- Sensorineural hearing loss, unspecified
- Achalasia of oesophagus
- Microcephaly with deafness and intellectual disability syndrome
- Keratitis ichthyosis deafness syndrome
- Congenital corneal dystrophy
- Deafness-dystonia-optic neuronopathy syndrome
- Non-acquired combined pituitary hormone deficiency, sensorineural hearing loss, spine abnormalities syndrome
- Retrocochlear Hearing Loss
- High frequency sensorineural hearing loss
- Progressive autosomal recessive ataxia, deafness syndrome
- Arts syndrome
- Keratitis, ichthyosis, deafness/hystrix-like ichthyosis deafness syndrome
- Jones syndrome
- Hereditary sensory neuropathy
- Deafness-dystonia syndrome
- HDR syndrome
- Posterior sensory radicular neuropathy
- Deafness and oligodontia syndrome
- Spondyloepiphyseal dysplasia, sensorineural hearing loss, intellectual disability, Leber congenital amaurosis syndrome
- Hearing loss, perceptive
- Maternally-inherited diabetes and hearing loss
- Renal tubular acidosis with deafness
- Colobomatous microphthalmia
- Hypoparathyroidism, deafness, renal disease syndrome
- Congenital kyphosis
- Sensoryneural Deafnesses
- Spinocerebellar ataxia, amyotrophy, deafness syndrome
- Ehlers-Danlos syndrome type 6
- Sellars Beighton syndrome
- Stoll Lévy Francfort syndrome
- Braun Bayer syndrome
- Sensory-neural deafness
- Sommer Young Wee Frye syndrome
- Hereditary gingival fibromatosis
- Congenital deafness
- Hypertelorism, preauricular sinus, punctual pits, deafness syndrome
- Congenital cataract, deafness, severe developmental delay syndrome
- Kyphoscoliotic Ehlers-Danlos syndrome due to FKBP22 deficiency
- Liberfarb syndrome
- Deafness and hypogonadism syndrome
- Type I renal tubular acidosis
- Hereditary motor and sensory neuropathy with deafness, intellectual disability and absent sensory large myelinated fibers
- Lethal neurodegenerative disorder due to copper transport defect
- Cerebellar ataxia, areflexia, pes cavus, optic atrophy, sensorineural hearing loss syndrome
- Retinitis pigmentosa, intellectual disability, deafness, hypogenitalism syndrome
- Central deafness
- Sensorineural Hearing Loss
- Gonadal dysgenesis with auditory dysfunction, autosomal recessive inheritance
- Seizure, sensorineural deafness, ataxia, intellectual disability, electrolyte imbalance syndrome
- DOORS syndrome
- COMMAD syndrome
- Duane's retraction syndrome
- Deafness, central
- Pfeiffer Kapferer syndrome
- Cataract, growth hormone deficiency, sensory neuropathy, sensorineural hearing loss, skeletal dysplasia syndrome
- Benign neoplasm of sacrococcygeal region
- Nephrotic syndrome, hearing loss, pretibial epidermolysis bullosa syndrome
- KID/HID syndrome
- Chromosome 15q15.3 deletion syndrome
- Thong Douglas Ferrante syndrome
- Congenital calyceal diverticulum
- Deafness nerve type
- Asymmetrical hearing loss
- Gelineau's syndrome
- Nanomelia
- Premature graying
- Deafness, congenital
- Mandibular hypoplasia, hearing loss, progeroid syndrome
- CHED-congenital hereditary endothelial dystrophy
- Deafness, sensorineural
- Progressive autosomal recessive cerebellar ataxia, sensorineural hearing loss syndrome
- Olivopontocerebellar atrophy co-occurrent with sensorineural hearing loss
- High tone sensorineural hearing loss
- sensorineural deafness
- Senter syndrome
- Dejerine-Thomas syndrome
- Deafness, encephaloneuropathy, obesity, valvulopathy syndrome
- Bjornstad's syndrome
- Orbital separation excessive
- Phocomelia, ectrodactyly, deafness and sinus arrhythmia syndrome
- Hearing loss and salivary gland insensitivity to aldosterone syndrome
- Marquardt-Loriaux syndrome
- Albright's renal tubular acidosis
- Barakat syndrome
- Leber's amaurosis
- 3-methylglutaconic aciduria type IV with sensorineural deafness, encephalopathy and Leigh-like syndrome
- Olivopontocerebellar atrophy
- Nathalie syndrome
- Perceptive hearing loss
- Duane's syndrome
- COMMAD (coloboma, osteopetrosis, microphthalmia, macrocephaly, albinism, deafness) syndrome
- Gemignani syndrome
- Autosomal dominant hearing loss, onychodystrophy syndrome
- 3-methylglutaconic aciduria with deafness, encephalopathy, Leigh-like syndrome
- Perceptive hearing loss NOS
- 10p partial monosomy syndrome
- Sensorineural deafness NOS
- Schaap Taylor Baraitser syndrome
- Multiple malformation syndrome, moderate short stature, facial with or without genital features
- SCAR19 - spinocerebellar ataxia, autosomal recessive 19
- Nephrosis, deafness, urinary tract, digital malformation syndrome
- Thomas' syndrome
- Deafness with onychodystrophy syndrome
- Keipert syndrome
- neural hearing loss
- Congenital cataract, hearing loss, severe developmental delay syndrome
- Deafness, onychodystrophy, osteodystrophy, intellectual disability syndrome
- Gonadal dysgenesis with sensorineural deafness, autosomal recessive inheritance
- KID syndrome
- Autosomal recessive KID (keratitis, ichthyosis, deafness) syndrome
- Wolfram syndrome type 1
- Deafness, nephritis, anorectal malformation syndrome
- perceptive deafness
- Congenital cataract with deafness and hypogonadism syndrome
- Sensorineural hearing loss of right ear
- Deafness infertility syndrome
- EAST (epilepsy, ataxia, sensorineural deafness, and tubulopathy) syndrome
- DIAPH1-related sensorineural deafness, thrombocytopenia syndrome
- Congenital atresia of anus
- WFS2 - Wolfram syndrome-2
- Cochlear hearing loss
- Congenital nephritis
- Syndromic sensorineural deafness due to combined oxidative phosphorylation defect
- Chitty Hall Baraitser syndrome
- Neural hearing loss of left ear
- Retinitis pigmentosa-deafness syndrome type 3
- Severe motor and intellectual disabilities, sensorineural deafness, dystonia syndrome
- Wolfram syndrome
- Deafness nerve
- Cleft palate and cleft lip with deafness and sacral lipoma syndrome
- Neural hearing loss of right ear
- Sensorineural deafness and male infertility
- Body height below reference range
- Congenital retinal blindness
- Hypertelorism
- SNHL - Sensorineural hearing loss
- Adult-onset progressive leucoencephalopathy, early-onset deafness
- Central hearing loss (disorder)
- Deafness, vitiligo, achalasia syndrome
- Thiamine-responsive megaloblastic anaemia syndrome
- Usher's syndrome
- Ehlers-Danlos syndrome kyphoscoliotic and hearing loss type
- Congenital sensorineural deafness
- Sensory-neural hearing loss
- hereditary deafness
- Retinitis pigmentosa, hearing loss, premature ageing, short stature, facial dysmorphism syndrome
- Dead ear - postoperative
- Acquired sensorineural hearing loss
- Generalised dystonia
- Lichtenstein Knorr syndrome
- Congenital imperforate anus
- Cardiospasm
- Diverticulum of renal calyx
- High frequency sensorineural hearing loss in right ear
- Congenital cataract, progressive muscular hypotonia, hearing loss, developmental delay syndrome
- Leber congenital amaurosis
- Central hearing loss NOS
- Gingival fibromatosis with progressive deafness syndrome
- Aphonia, deafness, retinal dystrophy, bifid halluces, intellectual disability syndrome
- nerve deafness
- Keratitis ichthyosis and deafness syndrome
- Renal tubular acidosis with progressive nerve deafness
- Sensory hearing loss NOS
- Sensoryneural Deafness
- Neonatal sensorineural hearing loss
- X-linked sensorineural hearing loss
- Congenital achalasia of esophagus
- Hypertelorism, preauricular sinus, punctual pits, hearing loss syndrome
- Harboyan syndrome
- Diaphanous related formin 1 related sensorineural hearing loss, thrombocytopenia syndrome
- Congenital osteodystrophy
- Neurosensory deafness
- Primary hypersomnia
- Central auditory dysfunction
- Charcot-Marie-Tooth disease, deafness, intellectual disability syndrome
- Gingival fibromatosis
- Low frequency sensorineural hearing loss
- End organ deafness
- Hypogonadotropic hypogonadism, severe microcephaly, sensorineural hearing loss, dysmorphism syndrome
- Duane retraction syndrome with congenital hearing loss
- Premature greyness of hair
- Retinitis pigmentosa, deafness, mental retardation, hypogonadism syndrome
- Ehlers-Danlos syndrome kyphoscoliotic type
- Retinitis pigmentosa, hearing loss, premature aging, short stature, facial dysmorphism syndrome
- Perrault syndrome
- Autosomal dominant deafness with onychodystrophy syndrome
- Wolfram syndrome type I
- Finucane Kurtz Scott syndrome
- Hypotrichosis and deafness syndrome
- Micromelus
- Congenital preauricular fistula
- Duane retraction syndrome
- RTA (renal tubular acidosis) type I
- Hereditary fibrous enlargement of gingiva
- Björnstad syndrome
- Peripheral neuropathy with sensorineural hearing impairment syndrome
- Hearing loss, encephaloneuropathy, obesity, valvulopathy syndrome
- Atresia ani
- Distal renal tubular acidosis co-occurrent with sensorineural deafness
- Profound hearing loss
- Neurosensory Deafnesses
- Corneal dystrophy with progressive deafness
- Narcolepsy
- Usher syndrome
- Aphonia, deafness, retinal dystrophy, duplicated halluces, intellectual disability syndrome
- Congenital hearing loss
- Microcephaly, intellectual disability, sensorineural hearing loss, epilepsy, abnormal muscle tone syndrome
- WFS1 - Wolfram syndrome-1
- Albinism with deafness syndrome
- Megaloblastic anemia, thiamine-responsive, with diabetes mellitus and sensorineural deafness
- Lack of reflex relaxation of lower oesophageal sphincter
- MIDD - maternally inherited diabetes and deafness
- Microcephaly, intellectual disability, sensorineural deafness, epilepsy, abnormal muscle tone syndrome
- Renal caliceal diverticuli and deafness syndrome
- Deafness congenital
- Ballinger-Wallace syndrome
- Congenital deafness NOS
- Lowe Kohn Cohen syndrome
- Postoperative profound sensorineural hearing loss
- Corneal dystrophy and perceptive deafness syndrome
- Eyes wide apart
- neural deafness
- Deafness, Neurosensory
- Black locks, oculocutaneous albinism, AND deafness of the sensorineural type
- Congenital megacolon
- Hearing Loss, Retrocochlear
- Congenital kyphoscoliosis
- Hereditary essential tremor
- sensorineural hearing losses
- Classic distal renal tubular acidosis
- Congenital sensorineural hearing loss
- HDR (hypoparathyroidism, sensorineural deafness, renal disease) syndrome
- Duane syndrome
- DIDMOAD (diabetes insipidus, diabetes mellitus, optic atrophy, deafness) syndrome
- Spondyloepiphyseal dysplasia MacDermot type
- Megalodontia
- Deafness craniofacial syndrome
- Congenital pernicious anaemia
- Asymmetric sensorineural hearing loss
- Wolfram syndrome type 2
- Adult-onset progressive leukoencephalopathy, early-onset hearing loss
- Orbital hypertelorism
- Globodontia
- Calyceal diverticulum
- Sudden hearing loss
- SND - Sensorineural deafness
- Dentinogenesis imperfecta
- Deafness, genital anomaly, metacarpal and metatarsal synostosis syndrome
- Sensorineural hearing loss, early graying, essential tremor syndrome
- Hearing loss, congenital
- Wolfram syndrome type II
- Deletion of part of chromosome 11
- Autoimmune sensorineural hearing loss
- Male infertility of chromosomal origin
- 3-Methylglutaconic aciduria type 4
- Severe X-linked intellectual disability Gustavson type
- Congenital prelingual deafness
- Fistula auris congenita
- Sensorineural hearing loss in left ear
- Spondyloepiphyseal dysplasia with myopia and sensorineural deafness syndrome
- Congenital hunchback
- DDOD (dominant deafness onychodystrophy) syndrome
- Adult-onset progressive leucoencephalopathy, early-onset hearing loss
- Congenital deafness (disorder)
- Autosomal dominant cerebellar ataxia, deafness and narcolepsy syndrome
- MDP (mandibular hypoplasia, deafness, progeroid) syndrome
- Sensorineural deafness due to late congenital syphilis
- Stilling-Turk-Duane syndrome
- Olivopontocerebellar atrophy and deafness
- Panhypopituitarism
- Diabetes, hypogonadism, deafness, intellectual disability syndrome
- Thiamine-responsive megaloblastic anemia
- Heritable disorder of neutrophil function
- PCNA-related progressive neurodegenerative photosensitivity syndrome
- Preauricular fistula
- Deafnesses, Sensoryneural
- Neuro sensory deafness
- Micromelia
- Maternally inherited cardiomyopathy and hearing loss syndrome
- Generalized dystonia
- Premature greying
- SRNS - Steroid-resistant nephrotic syndrome
- Hearing impairment, sensorineural
- Dominant sensorineural hearing loss
- Santos Mateus Leal syndrome
- Sensorineural hearing loss, early greying, essential tremor syndrome
- HPPD (hypertelorism, preauricular sinus, punctual pits, deafness) syndrome
- Duane syndrome, type 3
- Megaloblastic anaemia, thiamine-responsive, with diabetes mellitus and sensorineural deafness
- Deafness with epiphyseal dysplasia and short stature syndrome
- Epiphyseal dysplasia, hearing loss, dysmorphism syndrome
- Preauricular sinus
- Autosomal recessive deafness onychodystrophy syndrome
- Congenital pernicious anemia
- Hereditary growth hormone deficiency
- OA - Ocular albinism
- Duane retraction syndrome with congenital deafness
- Sinoatrial node dysfunction and deafness
- Deafness with cataract and skeletal anomaly syndrome
- Hearing Loss, Sensorineural
- Recessive sensorineural hearing loss
- Phocomelic dwarf
- Olivopontocerebellar degeneration
- Duane's syndrome, type 3
- Hereditary motor and sensory neuropathy with deafness, intellectual disability and absent sensory large myelinated fibres
- Neuropathy with hearing impairment
- Congenital absence of proximal portion of limb
- Déjérine-Thomas syndrome
- Retinitis pigmentosa-deafness syndrome
- Neural hearing loss (disorder)
- Multiple malformation syndrome, moderate short stature, facial
- Syndromic sensorineural hearing loss due to COXPD (combined oxidative phosphorylation defect)
- Congenital cataract with ataxia and deafness syndrome
- Coloboma, osteopetrosis, microphthalmia, macrocephaly, albinism, deafness syndrome
- Non-acquired combined pituitary hormone deficiency, deafness, rigid cervical spine syndrome
- Oculootodental syndrome
- Usher syndrome type 3
- Congenital cataract, progressive muscular hypotonia, deafness, developmental delay syndrome
- Short stature and deafness with neutrophil dysfunction and facial dysmorphism syndrome
- Congenital achalasia of oesophagus
- Dead ear
- Lethal ataxia-deafness-optic atrophy
- Progressive sensorineural hearing loss and hypertrophic cardiomyopathy syndrome
- Congenital atrophy of optic nerve
- Dentinogenesis imperfecta, short stature, hearing loss, intellectual disability syndrome
- Autosomal dominant keratitis, ichthyosis, deafness syndrome
- Chronic deafness
- Maternally inherited cardiomyopathy and deafness
- Retinitis pigmentosa, deafness, premature ageing, short stature, facial dysmorphism syndrome
- Microphthalmia with colobomatous cyst
- Deafness, Sensoryneural
- Lipoma of lower back
- Pili torti-deafness syndrome
- Lack of reflex relaxation of lower esophageal sphincter
- sensory neuro deafness
- Olivocerebellar atrophy
- Twisted hair
- Diabetes mellitus associated with genetic syndrome
- Deafnesses, Neurosensory
- Congenital humpback
- Postnatal acquired sensorineural hearing loss
- Familial steroid-resistant nephrotic syndrome with sensorineural deafness
- Low tone sensorineural hearing loss
- Deletion of part of chromosome 10
- DIAPH1-related sensorineural hearing loss-thrombocytopenia syndrome
- SHILCA syndrome
- Thiamine-responsive megaloblastic anaemia
- CRB - Congenital retinal blindness
- Megaloblastic anaemia due to inborn errors of metabolism
- Oligodontia
- Sudden sensorineural hearing loss
- AR dRTA (autosomal recessive distal renal tubular acidosis) with deafness
- Fatal X-linked ataxia with deafness and loss of vision
- Sensorineural deafness with dilated cardiomyopathy syndrome
- Autosomal dominant myopia, midfacial retrusion, sensorineural hearing loss, rhizomelic dysplasia syndrome
- Megaloblastic anemia due to inborn errors of metabolism
- Profound acquired hearing loss
- Auditory synaptopathy
- Simmond's disease
- Syndromic sensorineural deafness due to COXPD (combined oxidative phosphorylation defect)
- Ocular albinism
- Thiamine-responsive megaloblastic anemia syndrome
- Rogers syndrome
- Megadontia
- Optic atrophy of bilateral eyes
- BADS syndrome
- Adult-onset progressive leukoencephalopathy, early-onset deafness
- SESAME syndrome
- Distal renal tubular acidosis
- Achalasia of esophagus
- Developmental malformation, deafness, dystonia syndrome
- Ectodermal dysplasia and sensorineural deafness syndrome
- Eyes widely set
- DOOR syndrome
- Steroid-unresponsive nephrotic syndrome
- Profound sensorineural hearing loss
- Lowry Yong syndrome
- Hereditary opalescent dentin
- Imperforate anus
- Deficient secretion of all pituitary hormones
- Autosomal recessive keratitis-ichthyosis-deafness syndrome
- Late congenital syphilitic sensorineural deafness
- Nephrotic syndrome, deafness, pretibial epidermolysis bullosa syndrome
- Hearing Loss, Cochlear
- Maternally inherited diabetes and deafness
- Sensorineural hearing loss in right ear
- Narcoleptic syndrome
- Autosomal recessive distal renal tubular acidosis with deafness
- Sensorineural hearing loss (disorder)
- Sensorineural hearing loss of left ear
- Macrodontism
- Leber amaurosis
- Congenital optic atrophy
- Neutropenia, monocytopenia, deafness syndrome
- Phocomelia
- Primary hypopituitarism
- Tungland Bellman syndrome
- Neural hearing loss NOS
- Nasodigitoacoustic syndrome
- Autosomal dominant myopia, midfacial retrusion, sensorineural deafness, rhizomelic dysplasia syndrome
- Aphonia, hearing loss, retinal dystrophy, duplicated halluces, intellectual disability syndrome
- Kawashima Tsuji syndrome
- Mitochondrial diabetes
- DIDMOAD syndrome
- hearing loss sensori neural
- Congenital hereditary endothelial dystrophy
- Microphthalmos co-occurrent with congenital ocular coloboma
- Anal atresia
- Eye retraction syndrome
- Ehlers-Danlos syndrome kyphoscoliotic and deafness type
- Autosomal dominant ichthyosis
- SESAME (seizures, sensorineural deafness, ataxia, mental retardation, electrolyte imbalance) syndrome
- Cochlear nerve deafness
- Congenital dystrophy of cornea
- Hirschsprung disease with deafness and polydactyly syndrome
- Woodhouse Sakati syndrome
- Ehlers-Danlos syndrome type VI
- Mohr-Tranebjaerg syndrome
- Pili torti
- Congenital dilatation of colon
Frequently Asked Questions
What is the ICD-10 code for unspecified sensorineural hearing loss?
The ICD-10-CM code for unspecified sensorineural hearing loss is H90.5. The full clinical description is "Unspecified sensorineural hearing loss". H90.5 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code H90.5 mean?
ICD-10-CM code H90.5 represents “Unspecified sensorineural hearing loss”. It is classified under Chapter 8: Diseases of the Ear and Mastoid Process and is a billable/specific code that can be used on a claim.
Is H90.5 a billable code?
Yes, H90.5 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is H90.5 in?
H90.5 is in Chapter 8: Diseases of the Ear and Mastoid Process (codes H60-H95).
What codes cannot be used with H90.5?
H90.5 has Excludes1 notes indicating codes that cannot be used together with it, including: deaf nonspeaking NEC (H91.3); deafness NOS (H91.9-); hearing loss NOS (H91.9-); and 5 more.
What SNOMED CT codes does H90.5 map to?
H90.5 maps to 197 SNOMED CT concepts: 6002006, 297233004, 711409002, 236532003, 45564002, and 192 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for H90.5?
H90.5 is linked to 5 UMLS Concept Unique Identifiers: C0018776, C1691779, C0155550, C0339789, C0018784. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does H90.5 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like unspecified sensorineural hearing loss affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of H90.5?
H90.5 maps to the ICD-11 code: AB51.Z (Acquired hearing impairment, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.