H35.54
BillableDystrophies primarily w the retinal pigment epithelium
Dystrophies primarily involving the retinal pigment epithelium
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Vitelliform retinal dystrophy
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •diabetes mellitus related eye conditions, , ,E09.3, E10.3, E11.3, E13.3
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury (trauma) of eye and orbitS05
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •syphilis related eye disorders, , ,A50.01, A50.3, A51.43, A52.71
- •diabetic retinal disorders, , , ,E08.311-E08.359, E09.311-E09.359, E10.311-E10.359, E11.311-E11.359, E13.311-E13.359
Related Codes(4)
Also Known As / Clinical Terms(80)
SNOMED CT
- Cone-rod retinal dystrophy80328002
- Progressive cone-rod dystrophy80328002
- AOFMD - adult-onset foveomacular dystrophy232049001
- AVMD - adult vitelliform macular dystrophy232049001
- Adult vitelliform macular dystrophy232049001
- Adult-onset foveomacular dystrophy232049001
- Adult-onset vitelliform macular dystrophy232049001
- Gass disease232049001
- Pseudo-Best disease232049001
- Pseudo-vitelliform macular dystrophy232049001
- Pattern dystrophy of macula232051002
- Retinal vitelliform deposits247140007
- Macular vitelliform deposits247155003
- Hereditary retinal dystrophy primarily involving retinal pigment epithelium698847000
- Inherited retinal dystrophy primarily involving retinal pigment epithelium698847000
- Amelogenesis imperfecta co-occurrent with cone rod dystrophy707608003
- Jalili syndrome707608003
- Spondylometaphyseal dysplasia with cone-rod dystrophy syndrome719205008
- Multifocal pattern dystrophy of retinal pigment epithelium simulating fundus flavimaculatus723408004
- Multifocal pattern dystrophy simulating Stargardt disease723408004
- Multifocal pattern dystrophy simulating fundus flavimaculatus723408004
- Reticular dystrophy of retinal pigment epithelium723502001
- BMD - Best macular dystrophy763387005
- BVMD - Best vitelliform macular dystrophy763387005
- Best disease763387005
- Best vitelliform macular dystrophy763387005
- Early-onset vitelliform macular dystrophy763387005
- Juvenile-onset vitelliform macular dystrophy763387005
- Polymorphic vitelline macular degeneration763387005
- Vitelliform macular dystrophy type 2763387005
- Biallelic RPE65 mutation associated retinal dystrophy764969006
- Biallelic RPE65, retinoid isomerohydrolase mutation associated retinal dystrophy764969006
- Fundus pulverulentus770437002
- MCRPE - Martinique crinkled retinal pigment epitheliopathy1187639002
- MDPT3 - patterned macular dystrophy 31187639002
- Martinique crinkled retinal pigment epitheliopathy1187639002
- Patterned macular dystrophy 31187639002
- Retinal pigment epithelial dystrophy342581000119102
UMLS
Clinical Terms
- Vitelliform retinal dystrophy
- Pseudo-vitelliform macular dystrophy
- MDPT3 - patterned macular dystrophy 3
- Best disease
- Polymorphic vitelline macular degeneration
- Reticular dystrophy of retinal pigment epithelium
- Progressive cone-rod dystrophy
- Biallelic RPE65, retinoid isomerohydrolase mutation associated retinal dystrophy
- Macular vitelliform deposits
- Amelogenesis imperfecta co-occurrent with cone rod dystrophy
- BVMD - Best vitelliform macular dystrophy
- Juvenile-onset vitelliform macular dystrophy
- Retinal vitelliform deposits
- Early-onset vitelliform macular dystrophy
- Inherited retinal dystrophy primarily involving retinal pigment epithelium
- Adult vitelliform macular dystrophy
- Adult-onset vitelliform macular dystrophy
- Pattern dystrophy of macula
- AOFMD - adult-onset foveomacular dystrophy
- Pseudo-Best disease
- Best vitelliform macular dystrophy
- Fundus pulverulentus
- MCRPE - Martinique crinkled retinal pigment epitheliopathy
- Vitelliform macular dystrophy type 2
- AVMD - adult vitelliform macular dystrophy
- Cone-rod retinal dystrophy
- Hereditary retinal dystrophy primarily involving retinal pigment epithelium
- Patterned macular dystrophy 3
- Multifocal pattern dystrophy simulating Stargardt disease
- Gass disease
- Multifocal pattern dystrophy of retinal pigment epithelium simulating fundus flavimaculatus
- Multifocal pattern dystrophy simulating fundus flavimaculatus
- Spondylometaphyseal dysplasia with cone-rod dystrophy syndrome
- Martinique crinkled retinal pigment epitheliopathy
- BMD - Best macular dystrophy
- Jalili syndrome
- Retinal pigment epithelial dystrophy
- Adult-onset foveomacular dystrophy
- Biallelic RPE65 mutation associated retinal dystrophy
Frequently Asked Questions
What is the ICD-10 code for dystrophies primarily w the retinal pigment epithelium?
The ICD-10-CM code for dystrophies primarily w the retinal pigment epithelium is H35.54. The full clinical description is "Dystrophies primarily involving the retinal pigment epithelium". H35.54 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code H35.54 mean?
ICD-10-CM code H35.54 represents “Dystrophies primarily involving the retinal pigment epithelium”. It is classified under Chapter 7: Diseases of the Eye and Adnexa and is a billable/specific code that can be used on a claim.
Is H35.54 a billable code?
Yes, H35.54 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is H35.54 in?
H35.54 is in Chapter 7: Diseases of the Eye and Adnexa (codes H00-H59).
What codes cannot be used with H35.54?
H35.54 has Excludes1 notes indicating codes that cannot be used together with it, including: dystrophies primarily involving Bruch's membrane (H31.1-).
What SNOMED CT codes does H35.54 map to?
H35.54 maps to 15 SNOMED CT concepts: 232049001, 707608003, 763387005, 764969006, 80328002, and 10 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for H35.54?
H35.54 is linked to 2 UMLS Concept Unique Identifiers: C0154865, C2880985. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does H35.54 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like dystrophies primarily w the retinal pigment epithelium affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of H35.54?
There is no direct ICD-11 mapping available for H35.54 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.