G23.0
BillableHallervorden-Spatz disease
Hallervorden-Spatz disease
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Pigmentary pallidal degeneration
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •multi-system degeneration of the autonomic nervous systemG90.3
Related Codes(5)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(107)
SNOMED CT
- Hallervorden-Spatz disease2992000
- Pigmentary pallidal atrophy2992000
- Pigmentary pallidal degeneration2992000
- Pallidal degeneration230302004
- Chorea due to heredodegenerative disorder722966004
- Dementia due to genetic disease1259476008
- Chorea due to classical neurodegeneration with brain iron accumulation type 11259611004
- Chorea due to classical pantothenate kinase associated neurodegeneration1259611004
- Chorea due to classical pigmentary pallidal degeneration1259611004
- Dementia due to atypical pantothenate kinase associated neurodegeneration1259679007
- Dementia due to atypical pigmentary pallidal degeneration1259679007
- Dementia due to neurodegeneration with brain iron accumulation type 11259679007
- Dementia due to classical neurodegeneration with brain iron accumulation type 11259990004
- Dementia due to classical pantothenate kinase associated neurodegeneration1259990004
- Dementia due to classical pigmentary pallidal degeneration1259990004
- Dystonia due to atypical pantothenate kinase associated neurodegeneration1260360005
- Dystonia due to atypical pigmentary pallidal degeneration1260360005
- Dystonia in neurodegeneration with brain iron accumulation type 11260360005
UMLS
- Brain Iron Accumulation Type I SyndromeC0018523
- Degeneration, Pigmentary PallidalC0018523
- Dystrophies, Juvenile-Onset NeuroaxonalC0018523
- Dystrophy, Juvenile-Onset NeuroaxonalC0018523
- HALLERVORDEN SPATZ DISC0018523
- HALLERVORDEN-SPATZ DISEASEC0018523
- HARP SYNDROME, FORMERLYC0018523
- HARP, FORMERLYC0018523
- HYPOPREBETALIPOPROTEINEMIA, ACANTHOCYTOSIS, RETINITIS PIGMENTOSA, AND PALLIDAL DEGENERATION, FORMERLYC0018523
- Hallervorden Spatz DiseaseC0018523
- Hallervorden Spatz SyndromeC0018523
- Hallervorden-Spatz DiseaseC0018523
- Hallervorden-Spatz SyndromeC0018523
- Hallervorden-Spatz diseaseC0018523
- Juvenile-Onset Neuroaxonal DystrophiesC0018523
- Juvenile-Onset Neuroaxonal DystrophyC0018523
- NBIA 1C0018523
- NBIA1C0018523
- NEURODEGENERATION WITH BRAIN IRON ACCUMULATION 1C0018523
- Neuroaxonal Dystrophies, Juvenile-OnsetC0018523
- Neuroaxonal Dystrophy, Juvenile OnsetC0018523
- Neuroaxonal Dystrophy, Juvenile-OnsetC0018523
- Neurodegeneration With Brain Iron Accumulation 1C0018523
- Neurodegeneration with Brain Iron Accumulation Type 1C0018523
- Neurodegeneration with brain iron accumulation type 1C0018523
- Neurodegeneration, Pantothenate Kinase-AssociatedC0018523
- PANTOTHENATE KINASE-ASSOCIATED NEURODEGENERATIONC0018523
- PKANC0018523
- PKAN NEUROAXONAL DYSTROPHY, JUVENILE-ONSETC0018523
- PKAN Neuroaxonal Dystrophy, Juvenile OnsetC0018523
- PKAN Neuroaxonal Dystrophy, Juvenile-OnsetC0018523
- Pallidal Atrophy, PigmentaryC0018523
- Pantothenate Kinase Associated NeurodegenerationC0018523
- Pantothenate Kinase-Associated NeurodegenerationC0018523
- Pantothenate kinase-associated neurodegenerationC0018523
- Pigmentary Pallidal AtrophyC0018523
- Pigmentary Pallidal DegenerationC0018523
- Pigmentary pallidal atrophyC0018523
- Pigmentary pallidal degenerationC0018523
- Pigmentary pallidal degeneration (disorder)C0018523
- hallervorden spatz diseaseC0018523
- hallervorden spatz syndromeC0018523
- hallervorden-spatz diseaseC0018523
- hallervorden-spatz syndromeC0018523
Clinical Terms
- HARP, FORMERLY
- Neurodegeneration with brain iron accumulation type 1
- Brain Iron Accumulation Type I Syndrome
- PKAN NEUROAXONAL DYSTROPHY, JUVENILE-ONSET
- Chorea due to classical pantothenate kinase associated neurodegeneration
- Dementia due to genetic disease
- NBIA 1
- Dystrophies, Juvenile-Onset Neuroaxonal
- Hallervorden Spatz Syndrome
- Neuroaxonal Dystrophy, Juvenile Onset
- Juvenile-Onset Neuroaxonal Dystrophies
- PKAN
- PKAN Neuroaxonal Dystrophy, Juvenile Onset
- Dementia due to classical neurodegeneration with brain iron accumulation type 1
- Dementia due to classical pigmentary pallidal degeneration
- Hallervorden-Spatz Syndrome
- Dementia due to classical pantothenate kinase associated neurodegeneration
- Dementia due to neurodegeneration with brain iron accumulation type 1
- Dementia due to atypical pigmentary pallidal degeneration
- Dystonia in neurodegeneration with brain iron accumulation type 1
- Pigmentary pallidal degeneration (disorder)
- HYPOPREBETALIPOPROTEINEMIA, ACANTHOCYTOSIS, RETINITIS PIGMENTOSA, AND PALLIDAL DEGENERATION, FORMERLY
- HALLERVORDEN SPATZ DIS
- Neurodegeneration With Brain Iron Accumulation 1
- Pantothenate kinase-associated neurodegeneration
- Pigmentary Pallidal Atrophy
- hallervorden spatz disease
- Pigmentary pallidal degeneration
- Dementia due to atypical pantothenate kinase associated neurodegeneration
- HARP SYNDROME, FORMERLY
- Dystonia due to atypical pigmentary pallidal degeneration
- Pallidal Atrophy, Pigmentary
- NBIA1
- Neurodegeneration, Pantothenate Kinase-Associated
- Degeneration, Pigmentary Pallidal
- Neuroaxonal Dystrophy, Juvenile-Onset
- Juvenile-Onset Neuroaxonal Dystrophy
- Pantothenate Kinase Associated Neurodegeneration
- Chorea due to classical neurodegeneration with brain iron accumulation type 1
- Chorea due to heredodegenerative disorder
- Chorea due to classical pigmentary pallidal degeneration
- Pallidal degeneration
- Dystonia due to atypical pantothenate kinase associated neurodegeneration
- Dystrophy, Juvenile-Onset Neuroaxonal
- Neuroaxonal Dystrophies, Juvenile-Onset
Frequently Asked Questions
What is the ICD-10 code for hallervorden-spatz disease?
The ICD-10-CM code for hallervorden-spatz disease is G23.0. The full clinical description is "Hallervorden-Spatz disease". G23.0 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code G23.0 mean?
ICD-10-CM code G23.0 represents “Hallervorden-Spatz disease”. It is classified under Chapter 6: Diseases of the Nervous System and is a billable/specific code that can be used on a claim.
Is G23.0 a billable code?
Yes, G23.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is G23.0 in?
G23.0 is in Chapter 6: Diseases of the Nervous System (codes G00-G99).
What SNOMED CT codes does G23.0 map to?
G23.0 maps to 8 SNOMED CT concepts: 1259611004, 722966004, 1259679007, 1259990004, 1259476008, and 3 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for G23.0?
G23.0 is linked to 1 UMLS Concept Unique Identifier: C0018523. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does G23.0 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like hallervorden-spatz disease affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of G23.0?
G23.0 maps to the ICD-11 code: 5C64.10 (Iron overload diseases).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.