G11.11
BillableFriedreich ataxia
Friedreich ataxia
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Autosomal recessive Friedreich ataxia
- Friedreich ataxia with retained reflexes
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •cerebral palsyG80
- •hereditary and idiopathic neuropathyG60
- •metabolic disordersE70-E88
Related Codes(2)
Also Known As / Clinical Terms(149)
SNOMED CT
- FA - Friedreich ataxia10394003
- FRDA - Friedreich ataxia10394003
- Familial ataxia10394003
- Friedreich ataxia10394003
- Friedreich's ataxia10394003
- Friedreich's disease10394003
- Dilated cardiomyopathy due to Friedreich ataxia50270004
- Dilated cardiomyopathy due to Friedreich's ataxia50270004
- Cerebellar ataxia associated with another disorder192874000
- Cardiomyopathy in Friedreich ataxia195030007
- Cardiomyopathy in Friedreich's ataxia195030007
- Hypertrophic cardiomyopathy due to Friedreich ataxia890119003
- Posterior cord syndrome due to Friedreich ataxia1343511009
UMLS
- Ataxia, FriedreichC0016719
- Ataxia, Friedreich FamilialC0016719
- Ataxia, Friedreich HereditaryC0016719
- Ataxia, Friedreich SpinocerebellarC0016719
- Ataxia, Friedreich'sC0016719
- Ataxia, Friedreich's FamilialC0016719
- Ataxia, Friedreich's HereditaryC0016719
- Ataxias, FriedreichC0016719
- Ataxias, Friedreich's HereditaryC0016719
- Disease, FriedreichC0016719
- Disease, Friedreich'sC0016719
- FA - Friedreich ataxiaC0016719
- FRDAC0016719
- FRDA - Friedreich ataxiaC0016719
- FRIEDREICH ATAXIAC0016719
- FRIEDREICH DISC0016719
- FRIEDREICHS DISC0016719
- Familial Ataxia, FriedreichC0016719
- Familial Ataxia, Friedreich'sC0016719
- Familial ataxiaC0016719
- Friedreich AtaxiaC0016719
- Friedreich AtaxiasC0016719
- Friedreich DiseaseC0016719
- Friedreich Familial AtaxiaC0016719
- Friedreich Hereditary AtaxiaC0016719
- Friedreich Hereditary Spinal AtaxiaC0016719
- Friedreich Spinocerebellar AtaxiaC0016719
- Friedreich ataxiaC0016719
- Friedreich ataxia (disorder)C0016719
- Friedreich spinocerebellar ataxiaC0016719
- Friedreich's AtaxiaC0016719
- Friedreich's DiseaseC0016719
- Friedreich's Familial AtaxiaC0016719
- Friedreich's Hereditary AtaxiaC0016719
- Friedreich's Hereditary AtaxiasC0016719
- Friedreich's Hereditary Spinal AtaxiaC0016719
- Friedreich's ataxiaC0016719
- Friedreich's diseaseC0016719
- Friedreich's tabesC0016719
- Friedreichs Familial AtaxiaC0016719
- Friedreichs Hereditary AtaxiaC0016719
- Friedrich's ataxiaC0016719
- Hereditary Ataxia, FriedreichC0016719
- Hereditary Ataxia, Friedreich'sC0016719
- Hereditary Ataxias, Friedreich'sC0016719
- Hereditary Spinal Ataxia, FriedreichC0016719
- Hereditary Spinal Ataxia, Friedreich'sC0016719
- Hereditary Spinal SclerosesC0016719
- Hereditary Spinal SclerosisC0016719
- Scleroses, Hereditary SpinalC0016719
- Sclerosis, Hereditary SpinalC0016719
- Spinal Scleroses, HereditaryC0016719
- Spinal Sclerosis, HereditaryC0016719
- Spinocerebellar Ataxia, FriedreichC0016719
- ataxia friedreichC0016719
- ataxia friedrich'sC0016719
- familial ataxiaC0016719
- family ataxiaC0016719
- friedreich ataxiaC0016719
- friedreich diseaseC0016719
- friedreich's ataxiaC0016719
- friedreich's diseaseC0016719
- friedreich's hereditary ataxiaC0016719
- friedreichs ataxiaC0016719
- friedrich's ataxiaC0016719
- friedrick's ataxiaC0016719
- spinal sclerosis hereditaryC0016719
- Autosomal recessive Friedreich ataxiaC2875045
- FARRC1847416
- FRIEDREICH ATAXIA WITH RETAINED REFLEXESC1847416
- Friedreich Ataxia with Retained ReflexesC1847416
- Friedreich ataxia with retained reflexesC1847416
Clinical Terms
- Friedreich's ataxia
- Friedreich's Disease
- Ataxia, Friedreich's
- Friedreich's Familial Ataxia
- Friedreich's Hereditary Ataxias
- Friedrich's ataxia
- FRIEDREICH ATAXIA WITH RETAINED REFLEXES
- Friedreich's Hereditary Ataxia
- spinal sclerosis hereditary
- Friedreich Familial Ataxia
- Scleroses, Hereditary Spinal
- friedrick's ataxia
- Cerebellar ataxia associated with another disorder
- Friedreich spinocerebellar ataxia
- Friedreich Disease
- Friedreich ataxia (disorder)
- ataxia friedrich's
- Hereditary Spinal Ataxia, Friedreich
- FRIEDREICH DIS
- FRDA - Friedreich ataxia
- Ataxia, Friedreich's Hereditary
- Friedreich's tabes
- Friedreich Hereditary Ataxia
- Disease, Friedreich's
- friedreichs ataxia
- Cardiomyopathy in Friedreich ataxia
- Familial Ataxia, Friedreich
- Sclerosis, Hereditary Spinal
- Hereditary Ataxia, Friedreich's
- Spinal Scleroses, Hereditary
- Spinocerebellar Ataxia, Friedreich
- Hereditary Spinal Ataxia, Friedreich's
- Spinal Sclerosis, Hereditary
- Friedreichs Hereditary Ataxia
- Dilated cardiomyopathy due to Friedreich's ataxia
- FA - Friedreich ataxia
- Ataxias, Friedreich's Hereditary
- family ataxia
- FARR
- Ataxia, Friedreich Familial
- Familial ataxia
- Hereditary Ataxias, Friedreich's
- Friedreich Hereditary Spinal Ataxia
- Ataxia, Friedreich's Familial
- Ataxia, Friedreich
- Ataxia, Friedreich Hereditary
- FRIEDREICHS DIS
- Dilated cardiomyopathy due to Friedreich ataxia
- Ataxia, Friedreich Spinocerebellar
- Friedreich's Hereditary Spinal Ataxia
- Posterior cord syndrome due to Friedreich ataxia
- FRDA
- Ataxias, Friedreich
- Disease, Friedreich
- Hereditary Spinal Scleroses
- Hypertrophic cardiomyopathy due to Friedreich ataxia
- Autosomal recessive Friedreich ataxia
- Familial Ataxia, Friedreich's
- ataxia friedreich
- Hereditary Ataxia, Friedreich
- Friedreich Ataxias
- Friedreichs Familial Ataxia
- Cardiomyopathy in Friedreich's ataxia
- Hereditary Spinal Sclerosis
Frequently Asked Questions
What is the ICD-10 code for friedreich ataxia?
The ICD-10-CM code for friedreich ataxia is G11.11. The full clinical description is "Friedreich ataxia". G11.11 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code G11.11 mean?
ICD-10-CM code G11.11 represents “Friedreich ataxia”. It is classified under Chapter 6: Diseases of the Nervous System and is a billable/specific code that can be used on a claim.
Is G11.11 a billable code?
Yes, G11.11 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is G11.11 in?
G11.11 is in Chapter 6: Diseases of the Nervous System (codes G00-G99).
What SNOMED CT codes does G11.11 map to?
G11.11 maps to 6 SNOMED CT concepts: 195030007, 192874000, 50270004, 10394003, 890119003, and 1 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for G11.11?
G11.11 is linked to 3 UMLS Concept Unique Identifiers: C0016719, C2875045, C1847416. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does G11.11 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like friedreich ataxia affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of G11.11?
There is no direct ICD-11 mapping available for G11.11 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.