G04.81
BillableOther encephalitis and encephalomyelitis
Other encephalitis and encephalomyelitis
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Noninfectious acute disseminated encephalomyelitis (noninfectious ADEM)
Includes
Conditions included under this code
- acute ascending myelitis
- meningoencephalitis
- meningomyelitis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •acute transverse myelitisG37.3
- •alcoholic encephalopathyG31.2
- •multiple sclerosisG35
- •myalgic encephalomyelitisG93.32
- •subacute necrotizing myelitisG37.4
- •toxic encephalitisG92.8
- •toxic encephalopathyG92.8
Code Also
A second code may be required; sequencing depends on circumstances
Related Codes(2)
Also Known As / Clinical Terms(137)
SNOMED CT
- Experimental allergic encephalomyelitis27040004
- Meningoencephalomyelitis29197009
- Allergic encephalomyelitis50776006
- Pyogranulomatous meningoencephalomyelitis55234004
- Granulomatous meningoencephalomyelitis58766009
- Inflammatory reticulosis58766009
- Allergic encephalitis70884002
- Allergic encephalopathy70884002
- Meningomyelitis74772000
- HIV 2 infection79019005
- Human immunodeficiency virus II infection79019005
- Autoimmune encephalitis95643007
- Autoimmune encephalopathy95643007
- Infectious mononucleosis encephalitis230175007
- Focal encephalitis230189002
- Brainstem encephalitis230190006
- Rasmussen encephalitis230191005
- Rasmussen syndrome230191005
- Limbic encephalitis230192003
- Limbic encephalopathy230192003
- HIV - Human immunodeficiency virus encephalitis398329009
- Human immunodeficiency virus encephalitis398329009
- Bickerstaff brainstem encephalitis427086003
- Bickerstaff encephalitis427086003
- Bickerstaff's brainstem encephalitis427086003
- Limbic encephalitis with N-methyl-D-aspartate receptor antibodies716684004
- Limbic encephalitis with caspr2 antibodies763793004
- Limbic encephalitis with contactin-associated protein-like 2 antibodies763793004
- Limbic encephalitis with LGI1 antibodies763794005
- Limbic encephalitis with leucine-rich glioma-inactivated 1 antibodies763794005
- Non-herpetic acute limbic encephalitis764998005
- Acute limbic encephalitis following transplant773275000
- PALE - post-transplant acute limbic encephalitis773275000
- Post-transplant acute limbic encephalitis773275000
- Limbic encephalitis with DPP6 (dipeptidyl-peptidase 6) antibodies773395008
- Limbic encephalitis with DPP6 antibodies773395008
- Limbic encephalitis with DPPX antibodies773395008
- Limbic encephalitis with dipeptidyl-peptidase 6 antibodies773395008
- CLIPPERS - chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids773688007
- Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids773688007
- Encephalitis caused by human immunodeficiency virus type 2840442003
- Human immunodeficiency virus type 2 encephalitis840442003
- Encephalitis caused by Retroviridae1163070000
- Retroviridae encephalitis1163070000
- Limbic encephalitis with neurexin-3 antibodies1169361002
- Autonomic disorder due to encephalitis1259060008
- Disorder of autonomic nervous system due to encephalitis1259060008
- Autonomic disorder due to autoimmune encephalitis1259067006
- Disorder of autonomic nervous system due to autoimmune encephalitis1259067006
- Autoimmune disorder of spinal cord1259085004
- Autoimmune myelopathy1259085004
- Autoimmune spinal cord disorder1259085004
- Autoimmune cerebellar inflammation1259086003
- Autoimmune cerebellitis1259086003
- Autoimmune inflammation of cerebellum1259086003
- Anti-NMDA receptor encephalitis1259087007
- Autoimmune encephalitis caused by N-methyl-D-aspartate receptor antibody1259087007
- Autoimmune acquired autonomic encephalomyelitis1259089005
- Dementia due to Hashimoto encephalopathy1259471003
- Dementia due to steroid-responsive encephalopathy associated with autoimmune thyroiditis1259471003
- Dementia due to autoimmune encephalitis1259586006
- ALE - autoimmune limbic encephalitis1300193002
- Autoimmune limbic encephalitis1300193002
- Anti-NMDA (N-methyl D-Aspartate) receptor encephalitis452281000124106
- Autoimmune encephalitis caused by N-methyl D-aspartate receptor antibody452281000124106
- Rasmussen syndrome, intractable435341000124104
- Rasmussen syndrome, refractory435341000124104
UMLS
Clinical Terms
- Limbic encephalitis with caspr2 antibodies
- Limbic encephalitis with N-methyl-D-aspartate receptor antibodies
- Focal encephalitis
- Retroviridae encephalitis
- Rasmussen syndrome, refractory
- Autonomic disorder due to autoimmune encephalitis
- Bickerstaff's brainstem encephalitis
- Dementia due to autoimmune encephalitis
- Human immunodeficiency virus encephalitis
- Autonomic disorder due to encephalitis
- Autoimmune encephalitis caused by N-methyl-D-aspartate receptor antibody
- Meningoencephalomyelitis
- Dementia due to Hashimoto encephalopathy
- Anti-NMDA (N-methyl D-Aspartate) receptor encephalitis
- HIV 2 infection
- Allergic encephalitis
- Meningomyelitis
- Autoimmune limbic encephalitis
- Rasmussen syndrome
- Rasmussen syndrome, intractable
- Autoimmune spinal cord disorder
- HIV - Human immunodeficiency virus encephalitis
- Autoimmune encephalitis
- Autoimmune acquired autonomic encephalomyelitis
- Bickerstaff brainstem encephalitis
- Experimental allergic encephalomyelitis
- Autoimmune cerebellitis
- Limbic encephalitis
- Allergic encephalomyelitis
- Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids
- Infectious mononucleosis encephalitis
- Dementia due to steroid-responsive encephalopathy associated with autoimmune thyroiditis
- Anti-NMDA receptor encephalitis
- Autoimmune myelopathy
- CLIPPERS - chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids
- Encephalitis caused by human immunodeficiency virus type 2
- Limbic encephalitis with DPP6 antibodies
- Encephalitis caused by Retroviridae
- Limbic encephalitis with DPPX antibodies
- Noninfectious acute disseminated encephalomyelitis (noninfectious ADEM)
- Limbic encephalopathy
- Disorder of autonomic nervous system due to encephalitis
- Bickerstaff encephalitis
- Limbic encephalitis with contactin-associated protein-like 2 antibodies
- Autoimmune cerebellar inflammation
- Granulomatous meningoencephalomyelitis
- Non-herpetic acute limbic encephalitis
- PALE - post-transplant acute limbic encephalitis
- Limbic encephalitis with LGI1 antibodies
- Post-transplant acute limbic encephalitis
- Brainstem encephalitis
- Allergic encephalopathy
- Inflammatory reticulosis
- Rasmussen encephalitis
- Limbic encephalitis with DPP6 (dipeptidyl-peptidase 6) antibodies
- Pyogranulomatous meningoencephalomyelitis
- Disorder of autonomic nervous system due to autoimmune encephalitis
- ALE - autoimmune limbic encephalitis
- Autoimmune disorder of spinal cord
- Autoimmune inflammation of cerebellum
- Human immunodeficiency virus type 2 encephalitis
- Limbic encephalitis with leucine-rich glioma-inactivated 1 antibodies
- Limbic encephalitis with dipeptidyl-peptidase 6 antibodies
- Autoimmune encephalitis caused by N-methyl D-aspartate receptor antibody
- Human immunodeficiency virus II infection
- Limbic encephalitis with neurexin-3 antibodies
- Acute limbic encephalitis following transplant
- Autoimmune encephalopathy
Frequently Asked Questions
What is the ICD-10 code for other encephalitis and encephalomyelitis?
The ICD-10-CM code for other encephalitis and encephalomyelitis is G04.81. The full clinical description is "Other encephalitis and encephalomyelitis". G04.81 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code G04.81 mean?
ICD-10-CM code G04.81 represents “Other encephalitis and encephalomyelitis”. It is classified under Chapter 6: Diseases of the Nervous System and is a billable/specific code that can be used on a claim.
Is G04.81 a billable code?
Yes, G04.81 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is G04.81 in?
G04.81 is in Chapter 6: Diseases of the Nervous System (codes G00-G99).
What codes cannot be used with G04.81?
G04.81 has Excludes1 notes indicating codes that cannot be used together with it, including: encephalopathy NOS (G93.40).
What SNOMED CT codes does G04.81 map to?
G04.81 maps to 37 SNOMED CT concepts: 1300193002, 773275000, 70884002, 50776006, 452281000124106, and 32 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for G04.81?
G04.81 is linked to 2 UMLS Concept Unique Identifiers: C2875021, C2875022. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does G04.81 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other encephalitis and encephalomyelitis affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of G04.81?
There is no direct ICD-11 mapping available for G04.81 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.