F84.2
BillableRett's syndrome
Rett's syndrome
Coding Notes
Includes
Conditions included under this code
- disorders of psychological development
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Code Also
A second code may be required; sequencing depends on circumstances
- any associated medical condition and intellectual disabilities
Related Codes(5)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(85)
SNOMED CT
- Cerebroatrophic hyperammonaemia68618008
- Cerebroatrophic hyperammonemia68618008
- RTS - Rett syndrome68618008
- Rett disorder68618008
- Rett syndrome68618008
- Rett's disorder68618008
- Atypical Rett syndrome718393002
- Dementia due to genetic disease1259476008
- Dystonia due to Rett syndrome1260362002
- MECP2 (methyl-cytosine phosphate guanine binding protein-2) disorder1296869000
- MECP2 related disorder1296869000
- Methyl-CpG (cytosine phosphate guanine) binding protein-2 disorder1296869000
- Methyl-CpG binding protein 2 related disorder1296869000
- Methyl-cytosine phosphate guanine binding protein-2 related disorder1296869000
- Dementia due to Rett syndrome130121000119104
- Dementia due to Rett's syndrome130121000119104
UMLS
- AUTISM, DEMENTIA, ATAXIA, AND LOSS OF PURPOSEFUL HAND USEC0035372
- Autism Dementia Ataxia Loss of Purposeful Hand Use SyndromeC0035372
- Autism, Dementia, Ataxia, and Loss of Purposeful Hand UseC0035372
- Autism-Dementia-Ataxia-Loss of Purposeful Hand Use SyndromeC0035372
- Autism-dementia-ataxia-loss of purposeful hand use syndromeC0035372
- Cerebroatrophic HyperammonemiaC0035372
- Cerebroatrophic HyperammonemiasC0035372
- Cerebroatrophic hyperammonaemiaC0035372
- Cerebroatrophic hyperammonemiaC0035372
- Hyperammonemia, CerebroatrophicC0035372
- Hyperammonemias, CerebroatrophicC0035372
- RETT DISC0035372
- RETT SYNDROMEC0035372
- RETTS DISC0035372
- RTSC0035372
- RTS - Rett syndromeC0035372
- RTTC0035372
- Rett DisorderC0035372
- Rett SyndromeC0035372
- Rett disorderC0035372
- Rett syndromeC0035372
- Rett syndrome (disorder)C0035372
- Rett's DisorderC0035372
- Rett's SyndromeC0035372
- Rett's disorderC0035372
- Rett's syndromeC0035372
- Retts SyndromeC0035372
- Syndrome, RettC0035372
- Syndrome, Rett'sC0035372
- cerebroatrophic hyperammonemiaC0035372
- disorder rettsC0035372
- rett disorderC0035372
- rett syndromeC0035372
- rett's disorderC0035372
- rett's syndromeC0035372
- retts syndromeC0035372
- syndrome rettC0035372
Clinical Terms
- RTT
- MECP2 related disorder
- Rett syndrome
- Rett's Disorder
- Cerebroatrophic hyperammonemia
- Autism-Dementia-Ataxia-Loss of Purposeful Hand Use Syndrome
- Dementia due to genetic disease
- RETT DIS
- Methyl-CpG (cytosine phosphate guanine) binding protein-2 disorder
- RTS
- Dementia due to Rett syndrome
- MECP2 (methyl-cytosine phosphate guanine binding protein-2) disorder
- rett disorder
- Retts Syndrome
- Autism, Dementia, Ataxia, and Loss of Purposeful Hand Use
- Hyperammonemias, Cerebroatrophic
- Methyl-cytosine phosphate guanine binding protein-2 related disorder
- Syndrome, Rett
- RTS - Rett syndrome
- Dementia due to Rett's syndrome
- RETTS DIS
- Cerebroatrophic Hyperammonemias
- Cerebroatrophic hyperammonaemia
- Syndrome, Rett's
- Rett syndrome (disorder)
- Methyl-CpG binding protein 2 related disorder
- Hyperammonemia, Cerebroatrophic
- disorder retts
- Autism Dementia Ataxia Loss of Purposeful Hand Use Syndrome
- syndrome rett
- Atypical Rett syndrome
- Dystonia due to Rett syndrome
Frequently Asked Questions
What is the ICD-10 code for rett's syndrome?
The ICD-10-CM code for rett's syndrome is F84.2. The full clinical description is "Rett's syndrome". F84.2 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code F84.2 mean?
ICD-10-CM code F84.2 represents “Rett's syndrome”. It is classified under Chapter 5: Mental, Behavioral and Neurodevelopmental Disorders and is a billable/specific code that can be used on a claim.
Is F84.2 a billable code?
Yes, F84.2 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is F84.2 in?
F84.2 is in Chapter 5: Mental, Behavioral and Neurodevelopmental Disorders (codes F01-F99).
What codes cannot be used with F84.2?
F84.2 has Excludes1 notes indicating codes that cannot be used together with it, including: Asperger's syndrome (F84.5); Autistic disorder (F84.0); Other childhood disintegrative disorder (F84.3).
What SNOMED CT codes does F84.2 map to?
F84.2 maps to 6 SNOMED CT concepts: 718393002, 68618008, 130121000119104, 1259476008, 1260362002, and 1 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for F84.2?
F84.2 is linked to 1 UMLS Concept Unique Identifier: C0035372. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does F84.2 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like rett's syndrome affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of F84.2?
F84.2 maps to the ICD-11 code: LD90.4 (Rett syndrome).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.