E76.29

Billable

Other mucopolysaccharidoses

Other mucopolysaccharidoses

Status

Billable / Specific

Block

E70-E88

Parent Code

E76.2

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • beta-Glucuronidase deficiency
  • Maroteaux-Lamy (mild) (severe) syndrome
  • Mucopolysaccharidosis, types VI, VII

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(2)
E76.21

Morquio mucopolysaccharidoses

E76.22

Sanfilippo mucopolysaccharidoses

Billable
Also Known As / Clinical Terms(133)

SNOMED CT

UMLS

Clinical Terms

  • Sly Syndrome
  • Polydystrophic dwarfism
  • beta-Glucuronidase deficiency
  • Mucopolysaccharidosis type VI
  • Deficiency of beta-glucuronidase
  • Arylsulfatase B deficiency
  • Mucopolysaccharidosis VIIs
  • Type VII, Mucopolysaccharidosis
  • Maroteaux-Lamy syndrome, intermediate form
  • MPS VII
  • Deficiency of N-acetylgalactosamine-4-sulfatase
  • Mucopolysaccharidosis chondroitin sulphate B
  • Deficiency, GUSB
  • Mucopolysaccharidosis, MPS-VII
  • Mucopolysaccharidosis type VII (disorder)
  • Mucopolysaccharidosis, types VI, VII
  • ARSB - Arylsulphatase B deficiency
  • Mucopolysaccharidosis, MPS-VI
  • Mucopolysaccharidosis Type VIIs
  • Sly Disease
  • Deficiency of N-acetylgalactosamine-4-sulphatase
  • Mucopolysaccharidosis chondroitin sulfate B
  • MPS7
  • Maroteaux-Lamy syndrome
  • Syndrome, Sly
  • Maroteaux-Lamy syndrome, severe form
  • ARSB - Arylsulfatase B deficiency
  • GUSB Deficiencies
  • Deficiencies, GUSB
  • Mucopolysaccharidosis VII
  • beta-Glucuronidase Deficiencies
  • N-acetylgalactosamine-4-sulphatase deficiency
  • Deficiency of cerebroside-sulfatase
  • Mucopolysaccharidosis type VII
  • Deficiencies, beta-Glucuronidase
  • Type VIIs, Mucopolysaccharidosis
  • Deficiency of cerebroside-sulphatase
  • GUSB deficiency
  • N-acetylgalactosamine-4-sulfatase deficiency
  • VIIs, Mucopolysaccharidosis
  • beta Glucuronidase Deficiency
  • Arylsulphatase B deficiency
  • Sly's syndrome
  • Maroteaux-Lamy (mild) (severe) syndrome
  • MUCOPOLYSACCHARIDOSIS, TYPE VII
  • Maroteaux-Lamy disease
  • MPS VI - Mucopolysaccharidosis VI
  • MPS 7
  • MPS VII - Mucopolysaccharidosis VII
  • Disease, Sly
  • ARSB deficiency
  • Deficiency, beta-Glucuronidase
  • Mucopolysaccharidosis 7
  • SLY DIS
  • Maroteaux-Lamy syndrome, mild form
  • Deficiency of beta-glucuronidase (disorder)
Frequently Asked Questions
What is the ICD-10 code for other mucopolysaccharidoses?

The ICD-10-CM code for other mucopolysaccharidoses is E76.29. The full clinical description is "Other mucopolysaccharidoses". E76.29 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code E76.29 mean?

ICD-10-CM code E76.29 represents “Other mucopolysaccharidoses”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.

Is E76.29 a billable code?

Yes, E76.29 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is E76.29 in?

E76.29 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).

What codes cannot be used with E76.29?

E76.29 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.

What SNOMED CT codes does E76.29 map to?

E76.29 maps to 7 SNOMED CT concepts: 69463008, 43916004, 52677002, 66521008, 26015003, and 2 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for E76.29?

E76.29 is linked to 4 UMLS Concept Unique Identifiers: C0085132, C2874283, C2874284, C0348491. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does E76.29 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other mucopolysaccharidoses affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of E76.29?

There is no direct ICD-11 mapping available for E76.29 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.