E71.110
BillableIsovaleric acidemia
Isovaleric acidemia
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Related Codes(2)
Also Known As / Clinical Terms(41)
SNOMED CT
- IVD-gene related isovaleryl-coenzyme A dehydrogenase deficiency87827003
- Isovaleric acid CoA dehydrogenase deficiency87827003
- Isovaleric acid-CoA dehydrogenase deficiency87827003
- Isovaleric acidaemia87827003
- Isovaleric acidemia87827003
- Isovaleryl-CoA dehydrogenase deficiency87827003
- Isovaleryl-coenzyme A dehydrogenase deficiency87827003
UMLS
- Acidemia, isovalericC0268575
- ISOVALERIC ACID CoA DEHYDROGENASE DEFICIENCYC0268575
- ISOVALERIC ACIDEMIAC0268575
- IVAC0268575
- IVD DEFICIENCYC0268575
- IVD deficiencyC0268575
- IVD-gene related isovaleryl-coenzyme A dehydrogenase deficiencyC0268575
- Isovaleric Acid-CoA Dehydrogenase DeficiencyC0268575
- Isovaleric AcidemiaC0268575
- Isovaleric acid CoA dehydrogenase deficiencyC0268575
- Isovaleric acid-CoA dehydrogenase deficiencyC0268575
- Isovaleric acidaemiaC0268575
- Isovaleric acidemiaC0268575
- IsovalericacidemiaC0268575
- Isovaleryl CoA carboxylase deficiencyC0268575
- Isovaleryl-CoA Dehydrogenase DeficiencyC0268575
- Isovaleryl-CoA dehydrogenase deficiencyC0268575
- Isovaleryl-coenzyme A dehydrogenase deficiencyC0268575
- Isovaleryl-coenzyme A dehydrogenase deficiency (disorder)C0268575
- isovaleric acidemiaC0268575
- isovaleryl coA dehydrogenase deficiencyC0268575
Clinical Terms
- Isovaleric acid CoA dehydrogenase deficiency
- IVD DEFICIENCY
- Isovaleryl CoA carboxylase deficiency
- IVA
- Isovaleryl-CoA dehydrogenase deficiency
- Isovaleric acid-CoA dehydrogenase deficiency
- Acidemia, isovaleric
- Isovalericacidemia
- Isovaleryl-coenzyme A dehydrogenase deficiency
- isovaleryl coA dehydrogenase deficiency
- Isovaleric acidaemia
- IVD-gene related isovaleryl-coenzyme A dehydrogenase deficiency
- Isovaleryl-coenzyme A dehydrogenase deficiency (disorder)
Frequently Asked Questions
What is the ICD-10 code for isovaleric acidemia?
The ICD-10-CM code for isovaleric acidemia is E71.110. The full clinical description is "Isovaleric acidemia". E71.110 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E71.110 mean?
ICD-10-CM code E71.110 represents “Isovaleric acidemia”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E71.110 a billable code?
Yes, E71.110 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E71.110 in?
E71.110 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E71.110?
E71.110 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What SNOMED CT codes does E71.110 map to?
E71.110 maps to 1 SNOMED CT concept: 87827003. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E71.110?
E71.110 is linked to 1 UMLS Concept Unique Identifier: C0268575. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E71.110 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like isovaleric acidemia affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E71.110?
There is no direct ICD-11 mapping available for E71.110 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.