E27.1
BillablePrimary adrenocortical insufficiency
Primary adrenocortical insufficiency
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Addison's disease
- Autoimmune adrenalitis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Related Codes(7)
E27.0Other adrenocortical overactivity
E27.2Addisonian crisis
E27.3Drug-induced adrenocortical insufficiency
E27.4Other and unspecified adrenocortical insufficiency
E27.5Adrenomedullary hyperfunction
E27.8Other specified disorders of adrenal gland
E27.9Disorder of adrenal gland, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(173)
SNOMED CT
- Congenital Addison disease12427005
- Congenital primary adrenocortical hypofunction12427005
- Myopathy in Addison disease34253008
- Myopathy in Addison's disease34253008
- Endocrine myopathy57958006
- Muscle disease related to endocrine disease57958006
- Muscle disorders associated with endocrine disease57958006
- Hereditary adrenal unresponsiveness to corticotropin71974009
- Addison disease due to autoimmunity76715008
- Addison's disease due to autoimmunity76715008
- Autoimmune Addison's disease76715008
- Autoimmune adrenal atrophy76715008
- Autoimmune adrenalitis76715008
- CAH - Congenital adrenal hypoplasia93235007
- Congenital adrenal hypoplasia93235007
- Congenital hypoplasia of adrenal gland93235007
- Congenital small adrenal gland93235007
- Hyperpigmentation of oral mucosa235038002
- Melanin pigmentation of oral mucosa235038002
- SRNS - Steroid-resistant nephrotic syndrome236381000
- Steroid-resistant nephrotic syndrome236381000
- Steroid-unresponsive nephrotic syndrome236381000
- RTH (resistance to thyroid hormone) syndrome237559000
- Resistance to TH (thyroid hormone) syndrome237559000
- Resistance to thyroid hormone syndrome237559000
- Thyroid hormone resistance237559000
- Thyroid hormone resistance syndrome237559000
- Pituitary thyroid hormone resistance360348000
- Addison disease363732003
- Addison's disease363732003
- Primary adrenocortical insufficiency373662000
- Primary hypoadrenalism373662000
- Buccal pigmentation due to Addison disease403252006
- Buccal pigmentation due to Addison's disease403252006
- Primary immunodeficiency due to MCM4 (mini-chromosome maintenance complex component 4) deficiency724275005
- Primary immunodeficiency due to MCM4 deficiency724275005
- Primary immunodeficiency with natural killer cell deficiency and adrenal insufficiency724275005
- Melanosis of mucosa of body orifice724847001
- Mucosal melanosis724847001
- Adrenomyodystrophy763311001
- Inherited isolated adrenal insufficiency due to partial CYP11A1 deficiency764960005
- Inherited isolated adrenal insufficiency due to partial cytochrome P450 family 11 subfamily A member 1 deficiency764960005
- Familial glucocorticoid deficiency765326001
- ACTH (adrenocorticotropic hormone) resistance syndrome1156181008
- Adrenocorticotropic hormone insensitivity1156181008
- Adrenocorticotropic hormone resistance syndrome1156181008
- Adrenocorticotropin resistance syndrome1156181008
- Familial steroid-resistant nephrotic syndrome with adrenal insufficiency1187040004
- Primary adrenal insufficiency, steroid-resistant nephrotic syndrome due to SGPL1 (sphingosine-1-phosphate lyase 1) deficiency1187040004
- Primary adrenal insufficiency, steroid-resistant nephrotic syndrome due to SGPL1 deficiency1187040004
UMLS
- ADDISON DISC0001403
- ADDISON DISEASEC0001403
- ADDISONS DISC0001403
- Addison DiseaseC0001403
- Addison diseaseC0001403
- Addison's DiseaseC0001403
- Addison's diseaseC0001403
- Addison's disease (disorder)C0001403
- Addisons DiseaseC0001403
- Adrenal Insufficiency, PrimaryC0001403
- Adrenal insufficiency (Addison disease)C0001403
- Adrenocortical Insufficiencies, PrimaryC0001403
- Adrenocortical Insufficiency, PrimaryC0001403
- Chronic Primary Adrenal InsufficiencyC0001403
- Classic Addison diseaseC0001403
- Disease Addison'sC0001403
- Disease, AddisonC0001403
- Hypoadrenalism, PrimaryC0001403
- Hypoadrenalisms, PrimaryC0001403
- HypocortisolismC0001403
- Insufficiencies, Primary AdrenocorticalC0001403
- Insufficiency, Primary AdrenocorticalC0001403
- Primary Addison diseaseC0001403
- Primary Adrenal InsufficiencyC0001403
- Primary Adrenocortical InsufficienciesC0001403
- Primary Adrenocortical InsufficiencyC0001403
- Primary HypoadrenalismC0001403
- Primary adrenocortical insufficiencyC0001403
- addison diseaseC0001403
- addison's diseaseC0001403
- primary adrenal insufficiencyC0001403
- Addison disease due to autoimmunityC0271737
- Addison's disease due to autoimmunityC0271737
- Addison's disease due to autoimmunity (disorder)C0271737
- Autoimmune Addison diseaseC0271737
- Autoimmune Addison's DiseaseC0271737
- Autoimmune Addison's diseaseC0271737
- Autoimmune AdrenalitisC0271737
- Autoimmune Primary Adrenal InsufficiencyC0271737
- Autoimmune adrenal atrophyC0271737
- Autoimmune adrenalitisC0271737
- adrenalitisC0271737
- autoimmune addison's diseaseC0271737
- autoimmune adrenalitisC0271737
- Primary adrenal insufficiencyC5848257
- Primary adrenocortical failureC5848257
- Primary adrenocortical insufficiency (disorder)C5848257
- Primary hypoadrenalismC5848257
Clinical Terms
- Autoimmune Addison disease
- Congenital small adrenal gland
- Steroid-resistant nephrotic syndrome
- Adrenal Insufficiency, Primary
- Muscle disorders associated with endocrine disease
- Primary immunodeficiency with natural killer cell deficiency and adrenal insufficiency
- Hypocortisolism
- Primary hypoadrenalism
- Primary adrenocortical failure
- primary adrenal insufficiency
- Melanosis of mucosa of body orifice
- Addison's disease due to autoimmunity (disorder)
- Disease Addison's
- Autoimmune Addison's disease
- Pituitary thyroid hormone resistance
- CAH - Congenital adrenal hypoplasia
- Addison disease
- Hypoadrenalism, Primary
- Thyroid hormone resistance syndrome
- Adrenocorticotropic hormone insensitivity
- Primary adrenocortical insufficiency (disorder)
- Congenital primary adrenocortical hypofunction
- Addisons Disease
- Familial steroid-resistant nephrotic syndrome with adrenal insufficiency
- Congenital hypoplasia of adrenal gland
- autoimmune adrenalitis
- Hyperpigmentation of oral mucosa
- Classic Addison disease
- Primary immunodeficiency due to MCM4 (mini-chromosome maintenance complex component 4) deficiency
- Congenital adrenal hypoplasia
- Hypoadrenalisms, Primary
- Disease, Addison
- Adrenocorticotropin resistance syndrome
- Steroid-unresponsive nephrotic syndrome
- Chronic Primary Adrenal Insufficiency
- Endocrine myopathy
- Adrenocortical Insufficiencies, Primary
- Congenital Addison disease
- Hereditary adrenal unresponsiveness to corticotropin
- Resistance to TH (thyroid hormone) syndrome
- Buccal pigmentation due to Addison disease
- addison's disease
- Primary adrenal insufficiency, steroid-resistant nephrotic syndrome due to SGPL1 (sphingosine-1-phosphate lyase 1) deficiency
- Buccal pigmentation due to Addison's disease
- ADDISONS DIS
- Familial glucocorticoid deficiency
- Inherited isolated adrenal insufficiency due to partial CYP11A1 deficiency
- Inherited isolated adrenal insufficiency due to partial cytochrome P450 family 11 subfamily A member 1 deficiency
- Insufficiencies, Primary Adrenocortical
- Adrenocorticotropic hormone resistance syndrome
- Addison's disease (disorder)
- Primary immunodeficiency due to MCM4 deficiency
- Addison's disease due to autoimmunity
- Autoimmune Primary Adrenal Insufficiency
- adrenalitis
- Adrenal insufficiency (Addison disease)
- Insufficiency, Primary Adrenocortical
- Addison disease due to autoimmunity
- SRNS - Steroid-resistant nephrotic syndrome
- Adrenocortical Insufficiency, Primary
- ADDISON DIS
- Primary adrenal insufficiency, steroid-resistant nephrotic syndrome due to SGPL1 deficiency
- RTH (resistance to thyroid hormone) syndrome
- Muscle disease related to endocrine disease
- Adrenomyodystrophy
- ACTH (adrenocorticotropic hormone) resistance syndrome
- Mucosal melanosis
- Autoimmune adrenal atrophy
- Thyroid hormone resistance
- Primary Adrenocortical Insufficiencies
- Myopathy in Addison's disease
- Myopathy in Addison disease
- Primary Addison disease
- Melanin pigmentation of oral mucosa
- Resistance to thyroid hormone syndrome
Frequently Asked Questions
What is the ICD-10 code for primary adrenocortical insufficiency?
The ICD-10-CM code for primary adrenocortical insufficiency is E27.1. The full clinical description is "Primary adrenocortical insufficiency". E27.1 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E27.1 mean?
ICD-10-CM code E27.1 represents “Primary adrenocortical insufficiency”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E27.1 a billable code?
Yes, E27.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E27.1 in?
E27.1 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E27.1?
E27.1 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); galactorrhea (N64.3); gynecomastia (N62); and 4 more.
What SNOMED CT codes does E27.1 map to?
E27.1 maps to 20 SNOMED CT concepts: 1156181008, 363732003, 76715008, 763311001, 403252006, and 15 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E27.1?
E27.1 is linked to 3 UMLS Concept Unique Identifiers: C0001403, C0271737, C5848257. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E27.1 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like primary adrenocortical insufficiency affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E27.1?
E27.1 maps to the ICD-11 code: 5A74.0 (Acquired adrenocortical insufficiency).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.