D81.31

Billable

Severe combined immunodef due to adenosine deaminase defic

Severe combined immunodeficiency due to adenosine deaminase deficiency

Status

Billable / Specific

Block

D80-D89

Parent Code

D81.3

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • ADA deficiency with SCID
  • Adenosine deaminase [ADA] deficiency with severe combined immunodeficiency

Includes

Conditions included under this code

  • defects in the complement system
  • immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
  • sarcoidosis

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(3)
D81.30

Adenosine deaminase deficiency, unspecified

BillableD81.32

Adenosine deaminase 2 deficiency

BillableD81.39

Other adenosine deaminase deficiency

Billable
Also Known As / Clinical Terms(60)

SNOMED CT

UMLS

Clinical Terms

  • SCID DUE TO ADA DEFICIENCY, EARLY-ONSET
  • Swiss type agammaglobulinemia
  • Adenosine deaminase-deficient severe combined immunodeficiency disease
  • SCID (severe combined immunodeficiency) due to absent ADA (adenosine deaminase)
  • Adenosine Deaminase Deficient Severe Combined Immunodeficiency
  • Severe combined immunodeficiency due to absent adenosine deaminase
  • Severe Combined Immunodeficiency, Autosomal Recessive, T Cell-Negative, B Cell-Negative, Nk Cell-Negative, Due To Adenosine Deaminase Deficiency
  • Severe combined immunodeficiency due to absent lymphoid stem cells (disorder)
  • Adenosine Deaminase Deficiency
  • Adenosine Deaminase Severe Combined Immunodeficiency
  • Bubble boy disease
  • Agammaglobulinemia, Swiss type
  • SCID DUE TO ADA DEFICIENCY
  • ADA-SCID
  • SCID (severe combined immunodeficiency) due to absent lymphoid stem cells
  • ADA deficiency with SCID
  • SCID (severe combined immunodeficiency) due to absent adenosine deaminase
  • Adenosine Deaminase Severe Combined Immune Deficiency
  • Severe combined immunodeficiency due to ADA deficiency
  • Severe combined immunodeficiency, alymphocytotic type
  • Severe combined immunodeficiency due to absent lymphoid stem cells
  • SCID1
  • Adenosine deaminase [ADA] deficiency with severe combined immunodeficiency
  • Agammaglobulinaemia - Swiss type
Frequently Asked Questions
What is the ICD-10 code for severe combined immunodef due to adenosine deaminase defic?

The ICD-10-CM code for severe combined immunodef due to adenosine deaminase defic is D81.31. The full clinical description is "Severe combined immunodeficiency due to adenosine deaminase deficiency". D81.31 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code D81.31 mean?

ICD-10-CM code D81.31 represents “Severe combined immunodeficiency due to adenosine deaminase deficiency”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.

Is D81.31 a billable code?

Yes, D81.31 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is D81.31 in?

D81.31 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).

What codes cannot be used with D81.31?

D81.31 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20); and 1 more.

What SNOMED CT codes does D81.31 map to?

D81.31 maps to 2 SNOMED CT concepts: 22406001, 36980009. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for D81.31?

D81.31 is linked to 1 UMLS Concept Unique Identifier: C0392607. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does D81.31 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like severe combined immunodef due to adenosine deaminase defic affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of D81.31?

There is no direct ICD-11 mapping available for D81.31 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.