C49.9
BillableMalignant neoplasm of connective and soft tissue, unsp
Malignant neoplasm of connective and soft tissue, unspecified
Coding Notes
Includes
Conditions included under this code
- malignant neoplasm of blood vessel
- malignant neoplasm of bursa
- malignant neoplasm of cartilage
- malignant neoplasm of fascia
- malignant neoplasm of fat
- malignant neoplasm of ligament, except uterine
- malignant neoplasm of lymphatic vessel
- malignant neoplasm of muscle
- malignant neoplasm of synovia
- malignant neoplasm of tendon (sheath)
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- malignant neoplasm of cartilage (of):
- •articularC40-C41
- •larynxC32.3
- •noseC30.0
- •malignant neoplasm of connective tissue of breastC50
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(9)
C49.0Malig neoplm of conn and soft tissue of head, face and neck
C49.1Malig neoplm of conn and soft tiss of upper limb, inc shldr
C49.2Malig neoplm of conn and soft tissue of lower limb, inc hip
C49.3Malignant neoplasm of connective and soft tissue of thorax
C49.4Malignant neoplasm of connective and soft tissue of abdomen
C49.5Malignant neoplasm of connective and soft tissue of pelvis
C49.6Malignant neoplasm of conn and soft tissue of trunk, unsp
C49.8Malignant neoplasm of ovrlp sites of conn and soft tissue
C49.AGastrointestinal stromal tumor
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(349)
SNOMED CT
- Primary malignant neoplasm of blood vessel93714009
- Primary malignant neoplasm of muscle93913006
- Skin tumor of smooth muscle origin254765000
- Skin tumour of smooth muscle origin254765000
- Cutaneous leiomyosarcoma254771006
- Liposarcoma254829001
- Malignant lipomatous tumor254829001
- Malignant lipomatous tumour254829001
- Sarcoma of bone and connective tissue255067005
- Malignant neoplasm of dermis255096006
- Malignant tumor of dermis255096006
- Malignant tumour of dermis255096006
- Malignant neoplasm of soft tissue269469005
- Malignant tumor of soft tissue269469005
- Malignant tumour of soft tissue269469005
- Malignant neoplasm of bone, connective tissue, skin and breast271467005
- Malignant neoplasm of fibrous tissue276797002
- Malignant tumor of fibrous tissue276797002
- Malignant tumour of fibrous tissue276797002
- Rhabdomyosarcoma302847003
- Rhabdosarcoma302847003
- Malignant synovioma302851001
- Synovial sarcoma302851001
- Local recurrence of malignant neoplasm of soft tissue314974009
- Local recurrence of malignant tumor of soft tissue314974009
- Local recurrence of malignant tumour of soft tissue314974009
- Cancer of muscle363495004
- Malignant neoplasm of muscle363495004
- Malignant tumor of muscle363495004
- Malignant tumour of muscle363495004
- Vaccine-induced fibrosarcoma370511006
- Primary malignant neoplasm of soft tissues372010005
- Pleomorphic malignant fibrous histiocytoma of skin398903003
- Myxofibrosarcoma of skin400175006
- Myxoid malignant fibrous histiocytoma of skin400175006
- Clear cell sarcoma402561003
- Malignant melanoma of soft tissues402561003
- Malignant neoplasm of subcutaneous fibrous tissue402871009
- Angiosarcoma403977003
- Haemangioendothelioma403980002
- Hemangioendothelioma403980002
- Epithelioid haemangioendothelioma403981003
- Epithelioid hemangioendothelioma403981003
- Intravascular angiosarcoma403985007
- Lymphangiosarcoma403986008
- Infantile fibrosarcoma403996004
- Malignant infantile fibrosarcoma403996004
- Malignant fibrous histiocytoma of skin404014008
- Superficial malignant fibrous histiocytoma of skin404015009
- Giant cell malignant fibrous histiocytoma of skin404016005
- Inflammatory malignant fibrous histiocytoma of skin404017001
- Malignant granular cell tumor404041003
- Malignant granular cell tumour404041003
- Epithelioid leiomyosarcoma of skin404045007
- Myxoid leiomyosarcoma of skin404046008
- Cutaneous leiomyosarcoma with granular cell change404047004
- Embryonal rhabdomyosarcoma404051002
- Botryoid rhabdomyosarcoma404052009
- Sarcoma botryoides404052009
- Alveolar rhabdomyosarcoma404053004
- Pleomorphic rhabdomyosarcoma404054005
- Spindle cell rhabdomyosarcoma404055006
- Alveolar soft part sarcoma404056007
- Adipocytic liposarcoma404067008
- Sclerosing liposarcoma404068003
- Myxoid liposarcoma404069006
- Pleomorphic liposarcoma404071006
- Dedifferentiated liposarcoma404072004
- Spindle cell liposarcoma404073009
- Extraskeletal osteosarcoma404077005
- Chondroid sarcoma404079008
- Extraskeletal myxoid chondrosarcoma404079008
- Low-grade fibromyxoid sarcoma404088004
- Surgical margin uninvolved by sarcoma405911005
- Surgical margin involved by sarcoma405912003
- Surgical margin involvement by sarcoma cannot be assessed405914002
- Intergroup rhabdomyosarcoma study post-surgical clinical group finding405917009
- Intergroup rhabdomyosarcoma study post-surgical clinical group IIIA: Localised or locally extensive tumour, gross residual disease after biopsy only405962008
- Intergroup rhabdomyosarcoma study post-surgical clinical group IIIA: Localized or locally extensive tumor, gross residual disease after biopsy only405962008
- Intergroup rhabdomyosarcoma study post-surgical clinical group IIIB: Localised or locally extensive tumour, gross residual disease after major resection (greater than 50 percent debulking)405963003
- Intergroup rhabdomyosarcoma study post-surgical clinical group IIIB: Localised or locally extensive tumour, gross residual disease after major resection (greater than 50% debulking)405963003
- Intergroup rhabdomyosarcoma study post-surgical clinical group IIIB: Localized or locally extensive tumor, gross residual disease after major resection (greater than 50 percent debulking)405963003
- Intergroup rhabdomyosarcoma study post-surgical clinical group IIIB: Localized or locally extensive tumor, gross residual disease after major resection (greater than 50% debulking)405963003
- Intergroup rhabdomyosarcoma study post-surgical clinical group IV: Any size primary tumor, with or without regional lymph node involvement, with distant metastases, without respect to surgical approach to primary tumor405964009
- Intergroup rhabdomyosarcoma study post-surgical clinical group IV: Any size primary tumour, with or without regional lymph node involvement, with distant metastases, without respect to surgical approach to primary tumour405964009
- Primary leiomyosarcoma423807009
- Sarcoma424413001
- Sarcoma of soft tissue424952003
- Malignant fibromatous neoplasm443250000
- Malignant fibrous histiocytoma443439001
- Leiomyosarcoma443719001
- Leiomyosarcoma of connective tissue447804006
- Ewing sarcoma of soft tissue447951009
- Ewing's sarcoma of soft tissue447951009
- Fibrosarcoma of connective tissue448139005
- Malignant neoplasm of connective tissue448274000
- Liposarcoma of connective tissue448554008
- Sarcoma of connective tissue449293008
- Primary liposarcoma of soft tissue of limb721577002
- Primary synovial sarcoma of soft tissue of limb721579004
- Primary myxofibrosarcoma723076008
- Epithelioid sarcoma782827000
- Extraskeletal myxoid chondrosarcoma of soft tissue of limb860832001
- DSRCT - desmoplastic small round cell tumor1156420003
- DSRCT - desmoplastic small round cell tumour1156420003
- Desmoplastic small round cell tumor1156420003
- Desmoplastic small round cell tumour1156420003
- Metastatic sarcoma of retroperitoneum1251498002
- Metastatic sarcoma to retroperitoneum1251498002
- Secondary sarcoma of retroperitoneum1251498002
- Malignant neoplasm of blood vessel1254957001
- Primary fibrosarcoma of connective tissue1259453005
- Primary botryoid rhabdomyosarcoma1259582008
- Primary sarcoma botryoides1259582008
- Primary spindle cell rhabdomyosarcoma1259583003
- Primary extraskeletal osteosarcoma1259585005
- Primary malignant granular cell tumor1259785007
- Primary malignant granular cell tumour1259785007
- Primary malignant synovioma1268484002
- Primary synovial sarcoma1268484002
- Primary alveolar soft part sarcoma1268531004
- Primary Ewing sarcoma of soft tissue1268534007
- Primary Ewing's sarcoma of soft tissue1268534007
- Primary epithelioid sarcoma1268547002
- Primary malignant fibrous histiocytoma1268715005
- Primary epithelioid haemangioendothelioma1268904009
- Primary epithelioid hemangioendothelioma1268904009
- Primary desmoplastic small round cell tumor1269044006
- Primary desmoplastic small round cell tumour1269044006
- Metastatic rhabdomyosarcoma1269121005
- Metastatic rhabdosarcoma1269121005
- Metastatic embryonal rhabdomyosarcoma1279882001
- Undifferentiated pleomorphic sarcoma1290751005
- Undifferentiated round cell sarcoma1290803006
- Undifferentiated spindle cell sarcoma1290807007
- Myxoid pleomorphic liposarcoma1290810000
- Classic epithelioid sarcoma1290825000
- Well differentiated liposarcoma1290827008
- Low grade myofibroblastic sarcoma1290828003
- Sclerosing epithelioid fibrosarcoma1290851003
- Fibrosarcoma1290852005
- Epithelioid myxofibrosarcoma1290855007
- Intimal sarcoma1290865001
- Large cell epithelioid sarcoma1290886001
- Proximal epithelioid sarcoma1290886001
- Anaplastic embryonal rhabdomyosarcoma1290888000
- Spindle cell synovial sarcoma1290889008
- Biphasic synovial sarcoma1290890004
- Poorly differentiated synovial sarcoma1290891000
- Epithelioid liposarcoma1290895009
- Inflammatory liposarcoma1290901007
- Myxoinflammatory fibroblastic sarcoma1290902000
- Undifferentiated sarcoma1290903005
- Malignant ossifying fibromyxoid tumor1292988006
- Malignant ossifying fibromyxoid tumour1292988006
- Malignant solitary fibrous tumor1292990007
- Malignant solitary fibrous tumour1292990007
- Lipoma-like liposarcoma1293066000
- Ectomesenchymoma1295216003
- Rhabdomyosarcoma with ganglionic differentiation1295216003
- Malignant tenosynovial giant cell tumor1295242003
- Malignant tenosynovial giant cell tumour1295242003
- Malignant phosphaturic mesenchymal tumor1295266009
- Malignant phosphaturic mesenchymal tumour1295266009
- Metastatic spindle cell rhabdomyosarcoma1336170004
- Metastatic spindle cell rhabdosarcoma1336170004
- Metastatic malignant synovioma1336171000
- Metastatic synovial sarcoma1336171000
- Metastatic fibrosarcoma1336176005
- Metastatic myxofibrosarcoma1336182008
- Metastatic pleomorphic rhabdomyosarcoma1336185005
- Metastatic infantile fibrosarcoma1339049006
- Metastatic malignant infantile fibrosarcoma1339049006
UMLS
Clinical Terms
- Primary fibrosarcoma of connective tissue
- Malignant tumour of muscle
- Primary alveolar soft part sarcoma
- Malignant melanoma of soft tissues
- Primary malignant synovioma
- Malignant neoplasm of blood vessel
- Malignant infantile fibrosarcoma
- Primary Ewing sarcoma of soft tissue
- Secondary sarcoma of retroperitoneum
- Primary myxofibrosarcoma
- Primary malignant neoplasm of muscle
- Epithelioid myxofibrosarcoma
- Rhabdomyosarcoma
- Metastatic malignant infantile fibrosarcoma
- Metastatic rhabdosarcoma
- Primary malignant neoplasm of blood vessel
- Metastatic malignant synovioma
- Spindle cell synovial sarcoma
- Malignant phosphaturic mesenchymal tumour
- Metastatic spindle cell rhabdomyosarcoma
- Ewing sarcoma of soft tissue
- Botryoid rhabdomyosarcoma
- Ewing's sarcoma of soft tissue
- Haemangioendothelioma
- Infantile fibrosarcoma
- Myxoid liposarcoma
- Anaplastic embryonal rhabdomyosarcoma
- Metastatic rhabdomyosarcoma
- Myxoid pleomorphic liposarcoma
- Metastatic embryonal rhabdomyosarcoma
- Malignant lipomatous tumour
- Malignant fibrous histiocytoma of skin
- Large cell epithelioid sarcoma
- Sarcoma of connective tissue
- Extraskeletal myxoid chondrosarcoma
- Intergroup rhabdomyosarcoma study post-surgical clinical group IIIA: Localised or locally extensive tumour, gross residual disease after biopsy only
- Primary Ewing's sarcoma of soft tissue
- Undifferentiated sarcoma
- Primary sarcoma botryoides
- Intergroup rhabdomyosarcoma study post-surgical clinical group IIIB: Localized or locally extensive tumor, gross residual disease after major resection (greater than 50 percent debulking)
- Lipoma-like liposarcoma
- Malignant ossifying fibromyxoid tumor
- Well differentiated liposarcoma
- Malignant granular cell tumor
- Metastatic fibrosarcoma
- Primary epithelioid sarcoma
- Malignant neoplasm of dermis
- Sclerosing epithelioid fibrosarcoma
- Biphasic synovial sarcoma
- Intergroup rhabdomyosarcoma study post-surgical clinical group IV: Any size primary tumor, with or without regional lymph node involvement, with distant metastases, without respect to surgical approach to primary tumor
- Intergroup rhabdomyosarcoma study post-surgical clinical group IV: Any size primary tumour, with or without regional lymph node involvement, with distant metastases, without respect to surgical approach to primary tumour
- Synovial sarcoma
- Alveolar soft part sarcoma
- Inflammatory liposarcoma
- Cancer of muscle
- Dedifferentiated liposarcoma
- Intergroup rhabdomyosarcoma study post-surgical clinical group IIIB: Localized or locally extensive tumor, gross residual disease after major resection (greater than 50% debulking)
- Malignant solitary fibrous tumor
- Metastatic sarcoma to retroperitoneum
- Sarcoma
- Surgical margin involved by sarcoma
- Primary synovial sarcoma
- Malignant tumour of fibrous tissue
- Intergroup rhabdomyosarcoma study post-surgical clinical group IIIB: Localised or locally extensive tumour, gross residual disease after major resection (greater than 50 percent debulking)
- Sarcoma botryoides
- Pleomorphic rhabdomyosarcoma
- Epithelioid hemangioendothelioma
- Undifferentiated spindle cell sarcoma
- Embryonal rhabdomyosarcoma
- Malignant neoplasm of fibrous tissue
- Primary epithelioid hemangioendothelioma
- Metastatic synovial sarcoma
- Malignant tumour of soft tissue
- Surgical margin involvement by sarcoma cannot be assessed
- Myxoid leiomyosarcoma of skin
- Lymphangiosarcoma
- Epithelioid leiomyosarcoma of skin
- Leiomyosarcoma
- Malignant neoplasm of subcutaneous fibrous tissue
- Malignant tumor of dermis
- Myxoinflammatory fibroblastic sarcoma
- Malignant synovioma
- Leiomyosarcoma of connective tissue
- Intravascular angiosarcoma
- Surgical margin uninvolved by sarcoma
- Alveolar rhabdomyosarcoma
- Malignant tumor of muscle
- Giant cell malignant fibrous histiocytoma of skin
- Intimal sarcoma
- Malignant phosphaturic mesenchymal tumor
- Desmoplastic small round cell tumour
- Clear cell sarcoma
- Malignant fibromatous neoplasm
- Myxoid malignant fibrous histiocytoma of skin
- Malignant tenosynovial giant cell tumor
- Low grade myofibroblastic sarcoma
- Skin tumor of smooth muscle origin
- Primary synovial sarcoma of soft tissue of limb
- Sarcoma of bone and connective tissue
- Metastatic spindle cell rhabdosarcoma
- Low-grade fibromyxoid sarcoma
- Malignant neoplasm of connective tissue
- Primary malignant granular cell tumor
- Local recurrence of malignant neoplasm of soft tissue
- Ectomesenchymoma
- DSRCT - desmoplastic small round cell tumor
- Malignant tumor of fibrous tissue
- Liposarcoma of connective tissue
- DSRCT - desmoplastic small round cell tumour
- Local recurrence of malignant tumor of soft tissue
- Liposarcoma
- Local recurrence of malignant tumour of soft tissue
- Malignant tumour of dermis
- Extraskeletal osteosarcoma
- Primary liposarcoma of soft tissue of limb
- Intergroup rhabdomyosarcoma study post-surgical clinical group IIIA: Localized or locally extensive tumor, gross residual disease after biopsy only
- Undifferentiated round cell sarcoma
- Fibrosarcoma
- Poorly differentiated synovial sarcoma
- Desmoplastic small round cell tumor
- Skin tumour of smooth muscle origin
- Primary malignant fibrous histiocytoma
- Pleomorphic liposarcoma
- Adipocytic liposarcoma
- Malignant fibrous histiocytoma
- Fibrosarcoma of connective tissue
- Malignant tumor of soft tissue
- Primary botryoid rhabdomyosarcoma
- Metastatic pleomorphic rhabdomyosarcoma
- Malignant solitary fibrous tumour
- Pleomorphic malignant fibrous histiocytoma of skin
- Primary malignant granular cell tumour
- Spindle cell liposarcoma
- Intergroup rhabdomyosarcoma study post-surgical clinical group finding
- Rhabdosarcoma
- Vaccine-induced fibrosarcoma
- Epithelioid liposarcoma
- Cutaneous leiomyosarcoma with granular cell change
- Primary malignant neoplasm of soft tissues
- Spindle cell rhabdomyosarcoma
- Malignant ossifying fibromyxoid tumour
- Classic epithelioid sarcoma
- Undifferentiated pleomorphic sarcoma
- Extraskeletal myxoid chondrosarcoma of soft tissue of limb
- Malignant neoplasm of soft tissue
- Inflammatory malignant fibrous histiocytoma of skin
- Sclerosing liposarcoma
- Epithelioid sarcoma
- Intergroup rhabdomyosarcoma study post-surgical clinical group IIIB: Localised or locally extensive tumour, gross residual disease after major resection (greater than 50% debulking)
- Epithelioid haemangioendothelioma
- Chondroid sarcoma
- Metastatic myxofibrosarcoma
- Malignant neoplasm of bone, connective tissue, skin and breast
- Hemangioendothelioma
- Malignant neoplasm of muscle
- Myxofibrosarcoma of skin
- Primary spindle cell rhabdomyosarcoma
- Malignant granular cell tumour
- Cutaneous leiomyosarcoma
- Angiosarcoma
- Primary epithelioid haemangioendothelioma
- Superficial malignant fibrous histiocytoma of skin
- Primary leiomyosarcoma
- Sarcoma of soft tissue
- Metastatic infantile fibrosarcoma
- Malignant lipomatous tumor
- Primary extraskeletal osteosarcoma
- Rhabdomyosarcoma with ganglionic differentiation
- Primary desmoplastic small round cell tumor
- Proximal epithelioid sarcoma
- Primary desmoplastic small round cell tumour
- Metastatic sarcoma of retroperitoneum
- Malignant tenosynovial giant cell tumour
Frequently Asked Questions
What is the ICD-10 code for malignant neoplasm of connective and soft tissue, unsp?
The ICD-10-CM code for malignant neoplasm of connective and soft tissue, unsp is C49.9. The full clinical description is "Malignant neoplasm of connective and soft tissue, unspecified". C49.9 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code C49.9 mean?
ICD-10-CM code C49.9 represents “Malignant neoplasm of connective and soft tissue, unspecified”. It is classified under Chapter 2: Neoplasms and is a billable/specific code that can be used on a claim.
Is C49.9 a billable code?
Yes, C49.9 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is C49.9 in?
C49.9 is in Chapter 2: Neoplasms (codes C00-D49).
What codes cannot be used with C49.9?
C49.9 has Excludes1 notes indicating codes that cannot be used together with it, including: malignant neoplasm of cartilage (of):; articular (C40-C41); larynx (C32.3); and 2 more.
What SNOMED CT codes does C49.9 map to?
C49.9 maps to 122 SNOMED CT concepts: 404067008, 404053004, 404056007, 1290888000, 403977003, and 117 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for C49.9?
C49.9 is linked to 1 UMLS Concept Unique Identifier: C0348362. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does C49.9 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like malignant neoplasm of connective and soft tissue, unsp affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of C49.9?
C49.9 maps to the ICD-11 code: 2B5K (Unspecified malignant soft tissue tumours or sarcomas of bone or articular cartilage of other or unspecified sites).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.