8A03.1

The ICD-11 code for hereditary ataxia is 8A03.1. The full clinical description is "Hereditary ataxia".

ICD-11 code 8A03.1 represents “Hereditary ataxia”. It is classified under Chapter 8: Diseases of the Nervous System.

8A03.1 is in Chapter 8: Diseases of the Nervous System (codes 8A00-8E7Z).

There is no direct ICD-10 mapping available for 8A03.1 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-10. Use the ICD-11 to ICD-10 converter to search for related codes.

ICD-11 is the latest revision of the WHO's International Classification of Diseases, succeeding ICD-10. Key differences include: a fully digital-first design, new chapters for sleep-wake disorders, sexual health, and traditional medicine, improved coding for rare diseases, and better integration with electronic health records through extension codes.

8A03.1 has 9 child codes, including: 8A03.10 (Friedreich ataxia), 8A03.11 (Ataxia due to Cerebrotendinous xanthomatosis), 8A03.12 (Ataxia due to Refsum disease), 8A03.13 (Ataxia due to abetalipoproteinemia), and 5 more.