4A01.01

The ICD-11 code for immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of b cells is 4A01.01. The full clinical description is "Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells".

ICD-11 code 4A01.01 represents “Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells”. It is classified under Chapter 4: Diseases of the Immune System.

4A01.01 is in Chapter 4: Diseases of the Immune System (codes 4A00-4B4Z).

4A01.01 maps to the ICD-10 code: D80.1 (Nonfamilial hypogammaglobulinemia). This is an equivalent mapping.

ICD-11 is the latest revision of the WHO's International Classification of Diseases, succeeding ICD-10. Key differences include: a fully digital-first design, new chapters for sleep-wake disorders, sexual health, and traditional medicine, improved coding for rare diseases, and better integration with electronic health records through extension codes.

4A01.01 maps to 8 SNOMED CT concepts: 119249001, 402791005, 234635007, 234637004, 119250001, and 3 more. SNOMED CT is a clinical terminology used in electronic health records.

4A01.01 is linked to 4 UMLS Concept Unique Identifiers: C0086438, C1386923, C2873843, C0494250. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.