4A01.00
Hereditary agammaglobulinaemia with profoundly reduced or absent B cells
Hereditary agammaglobulinaemia with profoundly reduced or absent B cells
Classification
ICD-11
Block
4A00-4A0ZParent Code
4A01.0ICD-10 Mapping
1 equivalentWHO Foundation
View on WHOICD-10 Equivalents(1)
ICD-10 Equivalents
View full mappingCorresponding ICD-10-CM codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(13)
SNOMED CT ↗
- Alveolar proteinosis10501004
- Autosomal agammaglobulinaemia with absent B-cells234534000
- Agammaglobulinaemia, microcephaly, craniosynostosis, severe dermatitis syndrome722281001
- 2'-5'-oligoadenylate synthetase 1-related infantile-onset pulmonary alveolar proteinosis, hypogammaglobulinaemia1197476009
- Agammaglobulinaemia due to TOP2B mutation1230295000
- Autosomal recessive agammaglobulinaemia1297036006
- Agammaglobulinaemia due to SPI1 defect1351647002
- Agammaglobulinaemia due to FNIP1 defect1351648007
- Autosomal dominant agammaglobulinaemia due to E47 transcription factor deficiency1351668001
- Autosomal recessive agammaglobulinaemia due to B cell linker deficiency1351671009
Frequently Asked Questions
What is the ICD-11 code for hereditary agammaglobulinaemia with profoundly reduced or absent b cells?
The ICD-11 code for hereditary agammaglobulinaemia with profoundly reduced or absent b cells is 4A01.00. The full clinical description is "Hereditary agammaglobulinaemia with profoundly reduced or absent B cells".
What does ICD-11 code 4A01.00 mean?
ICD-11 code 4A01.00 represents “Hereditary agammaglobulinaemia with profoundly reduced or absent B cells”. It is classified under Chapter 4: Diseases of the Immune System.
What chapter is 4A01.00 in?
4A01.00 is in Chapter 4: Diseases of the Immune System (codes 4A00-4B4Z).
What is the ICD-10 equivalent of ICD-11 code 4A01.00?
4A01.00 maps to the ICD-10 code: D80.0 (Hereditary hypogammaglobulinemia). This is an equivalent mapping.
What is the difference between ICD-10 and ICD-11?
ICD-11 is the latest revision of the WHO's International Classification of Diseases, succeeding ICD-10. Key differences include: a fully digital-first design, new chapters for sleep-wake disorders, sexual health, and traditional medicine, improved coding for rare diseases, and better integration with electronic health records through extension codes.
What SNOMED CT codes does 4A01.00 map to?
4A01.00 maps to 10 SNOMED CT concepts: 1197476009, 1351648007, 1351647002, 1230295000, 722281001, and 5 more. SNOMED CT is a clinical terminology used in electronic health records.
What UMLS concepts map to ICD-11 code 4A01.00?
4A01.00 is linked to 3 UMLS Concept Unique Identifiers: C2873841, C0494249, C2873842. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.