4A00.1

The ICD-11 code for defects in the complement system is 4A00.1. The full clinical description is "Defects in the complement system".

ICD-11 code 4A00.1 represents “Defects in the complement system”. It is classified under Chapter 4: Diseases of the Immune System.

4A00.1 is in Chapter 4: Diseases of the Immune System (codes 4A00-4B4Z).

There is no direct ICD-10 mapping available for 4A00.1 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-10. Use the ICD-11 to ICD-10 converter to search for related codes.

ICD-11 is the latest revision of the WHO's International Classification of Diseases, succeeding ICD-10. Key differences include: a fully digital-first design, new chapters for sleep-wake disorders, sexual health, and traditional medicine, improved coding for rare diseases, and better integration with electronic health records through extension codes.

4A00.1 has 8 child codes, including: 4A00.10 (Immunodeficiency with an early component of complement deficiency), 4A00.11 (Immunodeficiency with a late component of complement deficiency), 4A00.12 (Immunodeficiency with factor B deficiency), 4A00.13 (Immunodeficiency with factor D anomaly), and 4 more.