N04.9
BillableNephrotic syndrome with unspecified morphologic changes
Nephrotic syndrome with unspecified morphologic changes
Coding Notes
Includes
Conditions included under this code
- congenital nephrotic syndrome
- lipoid nephrosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- hypertensive chronic kidney disease (I12.-)
Excludes 2
Conditions not included here, but the patient may have both
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Code Also
A second code may be required; sequencing depends on circumstances
- any associated kidney failure (N17-N19).
Also Known As / Clinical Terms
SNOMED CT
- Nephritic syndrome7724006
- Nephrotic-nephritic syndrome40233000
- Amyloid nephropathy48713002
- Lardaceous kidney48713002
- Nephropathic amyloidosis48713002
- Renal amyloidosis48713002
- Soapy kidney48713002
- Waxy kidney48713002
- Congenital nephrotic syndrome48796009
- Familial nephrotic syndrome48796009
- NS - Nephrotic syndrome52254009
- Nephrosis52254009
- Nephrotic syndrome52254009
- CAH - Congenital adrenal hypoplasia93235007
- Congenital adrenal hypoplasia93235007
- Congenital hypoplasia of adrenal gland93235007
- Congenital small adrenal gland93235007
- Nephrotic syndrome in amyloidosis197604006
- Malarial nephrosis197606008
- Nephrotic syndrome in malaria197606008
- Nephrotic syndrome in polyarteritis nodosa197607004
- SSNS - Steroid-sensitive nephrotic syndrome236380004
- Steroid-responsive nephrotic syndrome236380004
- Steroid-sensitive nephrotic syndrome236380004
- SRNS - Steroid-resistant nephrotic syndrome236381000
- Steroid-resistant nephrotic syndrome236381000
- Steroid-unresponsive nephrotic syndrome236381000
- SDNS - Steroid-dependent nephrotic syndrome236382007
- Steroid-dependent nephrotic syndrome236382007
- Pulmonic stenosis and congenital nephrosis236530006
- Nephrotic syndrome secondary to glomerulonephritis363233007
- Nephrotic syndrome secondary to systemic disease363234001
- Anasarca442433009
- Steroid sensitive nephrotic syndrome of childhood445119005
- Steroid resistant nephrotic syndrome of childhood449820008
- Childhood nephrotic syndrome705065000
- Disorder of kidney co-occurrent with human immunodeficiency virus infection713504001
- Nephropathy co-occurrent with human immunodeficiency virus infection713504001
- Nephrotic syndrome co-occurrent with human immunodeficiency virus infection713695001
- Sporadic idiopathic nephrosis717191005
- Sporadic idiopathic steroid-resistant nephrotic syndrome717191005
- Multi-drug resistant nephrotic syndrome717760006
- Familial idiopathic steroid-resistant nephrotic syndrome718141008
- Genetic steroid-resistant nephrotic syndrome718141008
- Hereditary steroid-resistant nephrotic syndrome718141008
- Galloway Mowat syndrome721297008
- Galloway syndrome721297008
- Microcephaly, hiatus hernia, nephrotic syndrome721297008
- Nephrosis, neuronal dysmigration syndrome721297008
- Congenital nephrotic syndrome (CNS) due to congenital infection722118005
- Congenital nephrotic syndrome due to congenital infection722118005
- Microcoria and congenital nephrosis syndrome723449004
- Pierson syndrome723449004
- Braun Bayer syndrome724092009
- Nephrosis, deafness, urinary tract, digital malformation syndrome724092009
- Congenital ILNEB (interstitial lung disease, nephrotic syndrome, epidermolysis bullosa) syndrome733453005
- Congenital nephrotic syndrome, epidermolysis bullosa, pulmonary disease syndrome733453005
- Congenital nephrotic syndrome, interstitial lung disease, epidermolysis bullosa syndrome733453005
- LAMB2 (laminin subunit beta 2) related infantile-onset nephrotic syndrome771447009
- LAMB2-related infantile-onset nephrotic syndrome771447009
- Laminin subunit beta 2 related infantile-onset nephrotic syndrome771447009
- Nephrotic syndrome, deafness, pretibial epidermolysis bullosa syndrome773647007
- Nephrotic syndrome, hearing loss, pretibial epidermolysis bullosa syndrome773647007
- Familial steroid-resistant nephrotic syndrome with sensorineural deafness783614008
- Glomerular disease due to infectious disease860892003
- Infective glomerular disease860892003
- Familial steroid-resistant nephrotic syndrome with adrenal insufficiency1187040004
- Primary adrenal insufficiency, steroid-resistant nephrotic syndrome due to SGPL1 (sphingosine-1-phosphate lyase 1) deficiency1187040004
- Primary adrenal insufficiency, steroid-resistant nephrotic syndrome due to SGPL1 deficiency1187040004
- Disorder of glomerulus due to amyloidosis1187557007
- Glomerular disorder due to amyloidosis1187557007
- Idiopathic SRNS (steroid-resistant nephrotic syndrome)1260194003
- Idiopathic steroid-resistant nephrotic syndrome1260194003
- Idiopathic SSNS (steroid-sensitive nephrotic syndrome) with secondary steroid resistance1260198000
- Idiopathic steroid-sensitive nephrotic syndrome with secondary steroid resistance1260198000
- Secondary steroid-resistant nephrotic syndrome1260198000
- Acute nephrotic syndrome1081801000112104
- Edema of kidney74011000119107
- Renal anasarca74011000119107
Frequently Asked Questions
What is ICD-10 code N04.9?
ICD-10-CM code N04.9 represents "Nephrotic syndrome with unspecified morphologic changes". It is a billable/specific code that can be used on a claim.
Is N04.9 a billable code?
Yes, N04.9 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is N04.9 in?
N04.9 is in Chapter 14: Diseases of the Genitourinary System (codes N00-N99).
What codes cannot be used with N04.9?
N04.9 has Excludes1 notes indicating codes that cannot be used together with it, including: hypertensive chronic kidney disease (I12.-).
What SNOMED CT codes does N04.9 map to?
N04.9 maps to 39 SNOMED CT concepts: 1081801000112104, 48713002, 442433009, 724092009, 93235007, and 34 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for N04.9?
N04.9 is linked to 1 UMLS Concept Unique Identifier: C2902894. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.