M04.2
BillableCryopyrin-associated periodic syndromes
Cryopyrin-associated periodic syndromes
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Chronic infantile neurological, cutaneous and articular syndrome [CINCA]
- Familial cold autoinflammatory syndrome
- Familial cold urticaria
- Muckle-Wells syndrome
- Neonatal onset multisystemic inflammatory disorder [NOMID]
Excludes 2
Conditions not included here, but the patient may have both
- arthropathic psoriasis (L40.5-)
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- compartment syndrome (traumatic) (T79.A-)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- Crohn's disease (K50.-)
Also Known As / Clinical Terms
SNOMED CT
- Cold urticaria74774004
- Cold-induced angio-oedema-urticaria74774004
- Cold-induced angioedema-urticaria74774004
- Urticaria caused by cold74774004
- FCAS - familial cold autoinflammatory syndrome238687000
- FCU - familial cold urticaria238687000
- Familial cold autoinflammatory syndrome238687000
- Familial cold urticaria238687000
- CINCA - Chronic infantile neurological, cutaneous and articular syndrome239826001
- Chronic infantile neurological, cutaneous and articular syndrome239826001
- NOMID - Neonatal onset multisystem inflammatory disease239826001
- Neonatal onset multisystem inflammatory disease239826001
- Cryopyrin associated periodic syndrome430079001
- Coagulation factor XII-associated cold autoinflammatory syndrome1348303000
- F12-associated cold autoinflammatory syndrome1348303000
- FACAS - F12-associated cold autoinflammatory syndrome1348303000
UMLS
- Amyloid nephropathy with deafness and urticariaC0268390
- CAPS2C0268390
- CRYOPYRIN-ASSOCIATED PERIODIC SYNDROME 2C0268390
- Familial amyloid nephropathy with urticaria AND deafnessC0268390
- Familial amyloid nephropathy with urticaria AND deafness (disorder)C0268390
- MUCKLE-WELLS SYNDROMEC0268390
- MWSC0268390
- Muckle Wells SyndromeC0268390
- Muckle-Wells SyndromeC0268390
- Muckle-Wells syndromeC0268390
- Muckle-Wells type amyloidosisC0268390
- Syndrome, Muckle-WellsC0268390
- Syndrome, UDAC0268390
- Syndrome, Urticaria-Deafness-AmyloidosisC0268390
- UDA SYNDROMEC0268390
- UDA SyndromeC0268390
- UDA SyndromesC0268390
- URTICARIA-DEAFNESS-AMYLOIDOSIS SYNDROMEC0268390
- Urticaria Deafness Amyloidosis SyndromeC0268390
- Urticaria, Deafness and AmyloidosisC0268390
- Urticaria-Deafness-Amyloidosis SyndromeC0268390
- Urticaria-Deafness-Amyloidosis SyndromesC0268390
- muckle well syndromeC0268390
- muckle-wells syndromeC0268390
- CAPS3C0409818
- CHRONIC NEUROLOGIC CUTANEOUS AND ARTICULAR SYNDROMEC0409818
- CINCAC0409818
- CINCA - Chronic infantile neurological, cutaneous and articular syndromeC0409818
- CINCA SYNDROMEC0409818
- CINCA SyndromeC0409818
- CINCA syndromeC0409818
- CINCA/NOMIDC0409818
- CRYOPYRIN-ASSOCIATED PERIODIC SYNDROME 3C0409818
- Chronic Infantile Neurologic, Cutaneous, and Articular SyndromeC0409818
- Chronic Infantile Neurological Cutaneous and Articular SyndromeC0409818
- Chronic Infantile Neurological, Cutaneous, and Articular SyndromeC0409818
- Chronic Neurologic Cutaneous and Articular SyndromeC0409818
- Chronic Neurologic, Cutaneous, and Articular SyndromeC0409818
- Chronic infantile neurological cutaneous and articular syndromeC0409818
- Chronic infantile neurological, cutaneous and articular syndromeC0409818
- Chronic infantile neurological, cutaneous and articular syndrome (disorder)C0409818
- Chronic infantile neurological, cutaneous and articular syndrome [CINCA]C0409818
- Chronic, Infantile, Neurological, Cutaneous, Articular SyndromeC0409818
- IOMIDC0409818
- IOMID SyndromeC0409818
- IOMID SyndromesC0409818
- Infantile Onset Multisystem Inflammatory DiseaseC0409818
- MULTISYSTEM INFLAMMATORY DISEASE, NEONATAL-ONSETC0409818
- Multisystem Inflammatory Disease, Neonatal OnsetC0409818
- Multisystem Inflammatory Disease, Neonatal-OnsetC0409818
- NOMIDC0409818
- NOMID - Neonatal onset multisystem inflammatory diseaseC0409818
- Neonatal Onset Multisystem Inflammatory DiseaseC0409818
- Neonatal onset multisystem inflammatory diseaseC0409818
- Neonatal-Onset Multisystem Inflammatory DiseaseC0409818
- Neonatal-onset multisystemic inflammatory diseaseC0409818
- Prieur Griscelli SyndromeC0409818
- Prieur-Griscelli SyndromeC0409818
- Prieur-Griscelli SyndromesC0409818
- Syndrome, IOMIDC0409818
- Syndrome, Prieur-GriscelliC0409818
- COLD HYPERSENSITIVITYC0343068
- COLD URTICARIA, FAMILIALC0343068
- COLD-INDUCED AUTOINFLAMMATORY SYNDROME, FAMILIALC0343068
- Cold Induced Autoinflammatory Syndrome, FamilialC0343068
- Cold Urticaria, FamilialC0343068
- Cold-Induced Autoinflammatory Syndrome, FamilialC0343068
- FCASC0343068
- FCAS - familial cold autoinflammatory syndromeC0343068
- FCUC0343068
- FCU - familial cold urticariaC0343068
- Familial Cold Autoinflammatory SyndromeC0343068
- Familial Cold Induced Autoinflammatory SyndromeC0343068
- Familial Cold UrticariaC0343068
- Familial Cold UrticariasC0343068
- Familial Cold-Induced Autoinflammatory SyndromeC0343068
- Familial cold autoinflammatory syndromeC0343068
- Familial cold urticariaC0343068
- Familial cold urticaria (disorder)C0343068
- Urticaria, Familial ColdC0343068
- Cryopyrin Associated Periodic SyndromeC2316212
- Cryopyrin Associated Periodic SyndromesC2316212
- Cryopyrin associated periodic syndromeC2316212
- Cryopyrin associated periodic syndrome (disorder)C2316212
- Cryopyrin-Associated Periodic SyndromeC2316212
- Cryopyrin-Associated Periodic SyndromesC2316212
- Cryopyrin-associated periodic syndromesC2316212
- CryopyrinopathiesC2316212
- CryopyrinopathyC2316212
- Neonatal onset multisystemic inflammatory disorder [NOMID]C4268692
Frequently Asked Questions
What is the ICD-10 code for cryopyrin-associated periodic syndromes?
The ICD-10-CM code for cryopyrin-associated periodic syndromes is M04.2. The full clinical description is "Cryopyrin-associated periodic syndromes". M04.2 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code M04.2 mean?
ICD-10-CM code M04.2 represents "Cryopyrin-associated periodic syndromes". It is classified under Chapter 13: Diseases of the Musculoskeletal System and Connective Tissue and is a billable/specific code that can be used on a claim.
Is M04.2 a billable code?
Yes, M04.2 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is M04.2 in?
M04.2 is in Chapter 13: Diseases of the Musculoskeletal System and Connective Tissue (codes M00-M99).
What SNOMED CT codes does M04.2 map to?
M04.2 maps to 5 SNOMED CT concepts: 239826001, 1348303000, 74774004, 430079001, 238687000. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for M04.2?
M04.2 is linked to 5 UMLS Concept Unique Identifiers: C0268390, C0409818, C0343068, C2316212, C4268692. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.