K00.5
BillableHereditary disturbances in tooth structure, NEC
Hereditary disturbances in tooth structure, not elsewhere classified
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Amelogenesis imperfecta
- Dentinogenesis imperfecta
- Odontogenesis imperfecta
- Dentinal dysplasia
- Shell teeth
Excludes 2
Conditions not included here, but the patient may have both
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- embedded and impacted teeth (K01.-)
Also Known As / Clinical Terms
SNOMED CT
- Hypocalcification of teeth26748006
- Hypomineralisation of teeth26748006
- Hypomineralization of teeth26748006
- Microdontia32337007
- Microdontism32337007
- Congenital abnormality of sclera32809005
- Congenital anomaly of sclera32809005
- Osteosclerosis49347007
- Taurodontism51744007
- Osteogenesis imperfecta type IB63890001
- Osteogenesis imperfecta with blue sclerae AND dentinogenesis imperfecta63890001
- Osteogenesis imperfecta with opalescent teeth63890001
- Shell teeth67504007
- AI - Amelogenesis imperfecta78494001
- Amelogenesis imperfecta78494001
- Congenital enamel hypoplasia78494001
- Amelogenesis imperfecta - hypocalcified109471001
- Amelogenesis imperfecta - hypomineralisation109471001
- Amelogenesis imperfecta - hypomineralization109471001
- Amelogenesis imperfecta, hypocalcification type109471001
- Amelogenesis imperfecta - hypomaturation - autosomal dominant - hypoplastic with taurodontism109472008
- Amelogenesis imperfecta, hypomaturation hypoplasia type with taurodontism109472008
- Amelogenesis imperfecta, hypoplastic type with microdontia109473003
- Amelogenesis imperfecta, pigmented hypomaturation type109474009
- Amelogenesis imperfecta - hypomaturation109475005
- Amelogenesis imperfecta, hypomaturation type109475005
- Amelogenesis imperfecta - hypoplastic109476006
- Amelogenesis imperfecta, hypoplastic type109476006
- Amelogenesis imperfecta and nephrocalcinosis109477002
- Amelogenesis imperfecta, nephrocalcinosis and impaired renal concentration109477002
- Enamel renal syndrome109477002
- Enamel-renal syndrome109477002
- McGibbon Lubinsky syndrome109477002
- Enamel hypomineralisation109487003
- Enamel hypomineralization109487003
- Hypocalcification of enamel109487003
- Hypocalcification of enamel of tooth109487003
- Hypomineralisation of enamel of tooth109487003
- Hypomineralization of enamel of tooth109487003
- Dentin dysplasia109492001
- Dentinal dysplasia109492001
- Dentine dysplasia109492001
- Dentin dysplasia, type I109493006
- Dentine dysplasia - Shield's type I109493006
- Radicular dentine dysplasia109493006
- Rootless teeth109493006
- Anomalous dysplasia of dentine109494000
- Coronal dentine dysplasia109494000
- Dentin dysplasia, type II109494000
- Dentine dysplasia - Shield's type II109494000
- Pulpal dysplasia109494000
- Horner teeth111325003
- Horner's teeth111325003
- Dentinogenesis imperfecta196286005
- Hereditary opalescent dentin196286005
- Odontogenesis imperfecta196287001
- Amelogenesis imperfecta - hypoplastic autosomal dominant - local234961008
- Amelogenesis imperfecta - hypoplastic autosomal dominant - smooth234962001
- Amelogenesis imperfecta - hypoplastic autosomal dominant - rough234963006
- Amelogenesis imperfecta - recessive - rough234964000
- Amelogenesis imperfecta - hypomaturation - recessive pigmented234965004
- Amelogenesis imperfecta - hypomaturation - snow capped teeth234966003
- Dentinogenesis imperfecta - Shield's type I234968002
- Dentinogenesis imperfecta with osteogenesis imperfecta234968002
- Opalescent teeth with osteogenesis imperfecta234968002
- Capdepont teeth234969005
- Dentinogenesis imperfecta - Shield's type II234969005
- Dentinogenesis imperfecta without osteogenesis imperfecta234969005
- Hereditary opalescent dentine234969005
- Brandywine type of dentinogenesis imperfecta234970006
- Dentinogenesis imperfecta - Shield's type III234970006
- Brachyolmia254088006
- Osteogenesis imperfecta type I385482004
- van de Hoeve syndrome385482004
- Hyperplasia of gingiva441798003
- Hyperplastic gingiva441798003
- Deep occlusal groove699685006
- Pronounced occlusal groove699685006
- Amelogenesis imperfecta and gingival hyperplasia syndrome707607008
- Amelogenesis imperfecta co-occurrent with cone rod dystrophy707608003
- Jalili syndrome707608003
- Autosomal recessive brachyolmia and amelogenesis imperfecta syndrome716195006
- Brachyolmia and amelogenesis imperfecta syndrome716195006
- Platyspondyly amelogenesis imperfecta716195006
- Verloes Bourguignon syndrome716195006
- Chondrodysplasia, dentinogenesis imperfecta, joint laxity syndrome717823001
- Goldblatt chondrodysplasia717823001
- Goldblatt syndrome717823001
- Odontochondrodysplasia717823001
- Trichodysplasia with amelogenesis imperfecta syndrome719911000
- Dentinogenesis imperfecta, short stature, hearing loss, intellectual disability syndrome721089006
- Dermo odontodysplasia721091003
- Dermo-odonto dysplasia721091003
- Dermoodonto dysplasia721091003
- Skeletal dysplasia with wormian bone, multiple fractures, dentinogenesis imperfecta syndrome733468006
- Suarez Stickler syndrome733468006
- Dentin dysplasia with sclerotic bone syndrome770943008
- Dentin dysplasia, sclerotic bones syndrome770943008
- Atypical dentin dysplasia due to SMOC2 deficiency783059004
- Atypical dentin dysplasia due to SPARC related modular calcium binding 2 deficiency783059004
- Dentin dysplasia type 1 with microdontia and shape anomalies783059004
- Hypocalcification of enamel of teeth1258915002
- Hypomineralisation of enamel of teeth1258915002
- Hypomineralization of enamel of teeth1258915002
UMLS
- AI - Amelogenesis imperfectaC0002452
- Amelogenesis ImperfectaC0002452
- Amelogenesis imperfectaC0002452
- Amelogenesis imperfecta (disorder)C0002452
- Congenital Enamel HypoplasiaC0002452
- Congenital enamel hypoplasiaC0002452
- amelogenesis imperfectaC0002452
- DGIC0011436
- Dentinogenesis ImperfectaC0011436
- Dentinogenesis imperfectaC0011436
- Dentinogenesis imperfecta (disorder)C0011436
- Hereditary opalescent dentinC0011436
- dentinogenesis imperfectaC0011436
- Dentin DysplasiaC0011430
- Dentin DysplasiasC0011430
- Dentin dysplasiaC0011430
- Dentin dysplasia (disorder)C0011430
- Dentinal dysplasiaC0011430
- Dentine dysplasiaC0011430
- Dysplasia, DentinC0011430
- Dysplasias, DentinC0011430
- dentin dysplasiaC0011430
- dentinal dysplasiaC0011430
- Hereditary disturbances in tooth structure, NECC0868847
- Hereditary disturbances in tooth structure, not elsewhere classifiedC0868847
- Odontogenesis ImperfectaC0028878
- Odontogenesis imperfectaC0028878
- Odontogenesis imperfecta (disorder)C0028878
- Shell teethC2981132
- Shell teeth (disorder)C2981132
Frequently Asked Questions
What is ICD-10 code K00.5?
ICD-10-CM code K00.5 represents "Hereditary disturbances in tooth structure, not elsewhere classified". It is a billable/specific code that can be used on a claim.
Is K00.5 a billable code?
Yes, K00.5 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is K00.5 in?
K00.5 is in Chapter 11: Diseases of the Digestive System (codes K00-K95).
What SNOMED CT codes does K00.5 map to?
K00.5 maps to 46 SNOMED CT concepts: 78494001, 109471001, 109475005, 109472008, 234965004, and 41 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for K00.5?
K00.5 is linked to 6 UMLS Concept Unique Identifiers: C0002452, C0011436, C0011430, C0868847, C0028878, and 1 more. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.