I42.0
BillableDilated cardiomyopathy
Dilated cardiomyopathy
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Congestive cardiomyopathy
Includes
Conditions included under this code
- myocardiopathy
Excludes 2
Conditions not included here, but the patient may have both
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- systemic connective tissue disorders (M30-M36)
- transient cerebral ischemic attacks and related syndromes (G45.-)
- ischemic cardiomyopathy (I25.5)
- peripartum cardiomyopathy (O90.3)
- ventricular hypertrophy (I51.7)
Code First
The underlying condition must be sequenced before this code
- pre-existing cardiomyopathy complicating pregnancy and puerperium (O99.4)
Also Known As / Clinical Terms
SNOMED CT
- Dilated cardiomyopathy due to myotonic dystrophy2816000
- Dilated cardiomyopathy secondary to myotonic dystrophy2816000
- Dilated cardiomyopathy due to sarcoidosis6022005
- Dilated cardiomyopathy due to haemochromatosis8209004
- Dilated cardiomyopathy due to hemochromatosis8209004
- Dilated cardiomyopathy secondary to haemochromatosis8209004
- Dilated cardiomyopathy secondary to hemochromatosis8209004
- Dilated cardiomyopathy due to phytanic acid storage disease11104006
- Dilated cardiomyopathy secondary to Refsum disease11104006
- Dilated cardiomyopathy secondary to Refsum's disease11104006
- Dilated cardiomyopathy secondary to phytanic acid storage disease11104006
- Dilated cardiomyopathy caused by radiation12563008
- Secondary dilated cardiomyopathy20529002
- Dilated cardiomyopathy due to rheumatoid arthritis21430002
- Dilated cardiomyopathy due to muscular dystrophy28869005
- Dilated cardiomyopathy secondary to muscular dystrophy28869005
- Dilated cardiomyopathy due to viral myocarditis30496006
- Dilated cardiomyopathy secondary to viral myocarditis30496006
- Dilated cardiomyopathy due to systemic sclerosis35719004
- Familial cardiomyopathy35728003
- Primary familial cardiomyopathy35728003
- Dilated cardiomyopathy due to granuloma39693003
- Dilated cardiomyopathy due to protozoal myocarditis40532006
- Dilated cardiomyopathy due to protozoan myocarditis40532006
- Dilated cardiomyopathy secondary to protozoal myocarditis40532006
- Dilated cardiomyopathy due to fungal myocarditis44630002
- Dilated cardiomyopathy secondary to fungal myocarditis44630002
- Dilated cardiomyopathy due to dermatomyositis46696008
- Dilated cardiomyopathy due to Friedreich ataxia50270004
- Dilated cardiomyopathy due to Friedreich's ataxia50270004
- Familial dilated cardiomyopathy52029003
- Primary familial dilated cardiomyopathy52029003
- Primary idiopathic dilated cardiomyopathy53043001
- Dilated cardiomyopathy due to bacterial myocarditis54830008
- Dilated cardiomyopathy secondary to bacterial myocarditis54830008
- Dilated cardiomyopathy due to amyloidosis58629009
- Dilated cardiomyopathy secondary to amyloidosis58629009
- Dilated cardiomyopathy due to glycogen storage disease58911001
- Dilated cardiomyopathy secondary to glycogen storage disease58911001
- Dilated cardiomyopathy due to familial storage disease60514000
- Dilated cardiomyopathy due to infiltration64749001
- Infiltrative dilated cardiomyopathy64749001
- Dilated cardiomyopathy caused by drug72972005
- Dilated cardiomyopathy secondary to drug72972005
- Drug-induced cardiomyopathy72972005
- Drug-induced specific heart muscle disorder72972005
- Dilated cardiomyopathy due to malignancy74249003
- Dilated cardiomyopathy due to neuromuscular disorder79152002
- Dilated cardiomyopathy due to nutritional deficiency84733009
- Nutritional cardiomyopathy84733009
- Dilated cardiomyopathy due to infection86194008
- Dilated cardiomyopathy due to infectious disease86194008
- Dilated cardiomyopathy due to mucopolysaccharidosis86995005
- Dilated cardiomyopathy due to polyarteritis nodosa91604001
- Dilated cardiomyopathy due to metabolic disorder111285003
- Dilated cardiomyopathy secondary to metabolic disorder111285003
- Metabolic cardiomyopathy111285003
- Primary dilated cardiomyopathy195021004
- Cardiomyopathy due to mucopolysaccharidosis195027000
- Mucopolysaccharidosis cardiomyopathy195027000
- Cardiomyopathy in Friedreich ataxia195030007
- Cardiomyopathy in Friedreich's ataxia195030007
- Cardiomyopathy in myotonic dystrophy195031006
- Congestive obstructive cardiomyopathy233871002
- Congenital woolly hair254231002
- Congenital wooly hair254231002
- Autosomal dominant epidermolysis bullosa simplex398170002
- EBS 1398170002
- CCM - Congestive cardiomyopathy399020009
- COCM - Congestive cardiomyopathy399020009
- Congestive cardiomyopathy399020009
- Congestive dilated cardiomyopathy399020009
- DCM - Dilated cardiomyopathy399020009
- Dilated cardiomyopathy399020009
- Non age related cataract399305009
- Non age-related cataract399305009
- Nonsenile cataract399305009
- Autosomal recessive familial woolly hair403795009
- Autosomal recessive familial wooly hair403795009
- Dilated cardiomyopathy with connective tissue disorder413994008
- Dilated cardiomyopathy due to taurine deficiency413995009
- Dilated cardiomyopathy of ischaemic origin426856002
- Dilated cardiomyopathy of ischemic origin426856002
- Ischaemic congestive cardiomyopathy426856002
- Ischemic congestive cardiomyopathy426856002
- Heart disease caused by ionising radiation430401005
- Heart disease caused by ionizing radiation430401005
- Dilated cardiomyopathy with genetic marker471890009
- Ischaemic congestive cardiomyopathy due to coronary artery disease472100003
- Ischaemic dilated cardiomyopathy due to coronary artery disease472100003
- Ischemic congestive cardiomyopathy due to coronary artery disease472100003
- Ischemic dilated cardiomyopathy due to coronary artery disease472100003
- Cardiovascular abnormality due to infectious myocarditis472811009
- Cardiovascular abnormality due to infective myocarditis472811009
- Secondary nonischemic congestive cardiomyopathy699668009
- DMD-associated dilated cardiomyopathy702424003
- Dilated cardiomyopathy 3B702424003
- Duchenne muscular dystrophy-associated dilated cardiomyopathy702424003
- X-linked dilated cardiomyopathy702424003
- Microcephalus cardiomyopathy syndrome719380003
- Microcephaly cardiomyopathy syndrome719380003
- Winship Viljoen Leary syndrome719380003
- Cardiogenital syndrome719451006
- Dilated cardiomyopathy with hypergonadotropic hypogonadism syndrome719451006
- Malouf syndrome719451006
- Najjar syndrome719451006
- Carvajal syndrome719835006
- Keratoderma with woolly hair type II719835006
- Keratoderma with wooly hair type II719835006
- Woolly hair and palmoplantar keratoderma with dilated cardiomyopathy syndrome719835006
- Wooly hair and palmoplantar keratoderma with dilated cardiomyopathy syndrome719835006
- Cardiomyopathy with cataract and hip spine disease syndrome720609003
- Krasnow Qazi syndrome720609003
- Sensorineural deafness with dilated cardiomyopathy syndrome723993005
- Familial dilated cardiomyopathy with conduction defect due to LMNA mutation766883006
- Familial dilated cardiomyopathy with conduction defect due to lamin A/C mutation766883006
- Cardiomyopathy due to connective tissue disease860837007
- Cardiomyopathy due to storage disease860839005
- Dilated cardiomyopathy due to mitochondrial disease871639003
- Infiltrative cardiomyopathy871646007
- Dilated cardiomyopathy due to carnitine deficiency880014009
- Dilated cardiomyopathy due to lysosomal storage disease880038008
- Dilated cardiomyopathy caused by anthracycline880042006
- Dilated cardiomyopathy caused by anthracycline toxicity880042006
- Dilated cardiomyopathy due to electrolyte imbalance1149109001
- Dilated cardiomyopathy due to parasitic myocarditis1153452008
- Intermediate epidermolysis bullosa simplex with cardiomyopathy1177176009
- EKC (erythrokeratodermia cardiomyopathy) syndrome1179293006
- Erythrokeratodermia cardiomyopathy syndrome1179293006
- Dilated cardiomyopathy due to scleroderma1264404009
- Cardiomyopathy caused by drug16228931000119102
- Cardiomyopathy due to viral infection204981000119101
- Nonischemic congestive cardiomyopathy111000119104
- Toxic cardiomyopathy103331000119103
- Toxic dilated cardiomyopathy165468981000119105
UMLS
- CCM - Congestive cardiomyopathyC0007193
- COCM - Congestive cardiomyopathyC0007193
- Cardiomyopathies, DilatedC0007193
- Cardiomyopathy, DilatedC0007193
- Cardiomyopathy, dilatedC0007193
- Congestive (dilated) cardiomyopathyC0007193
- Congestive cardiomyopathyC0007193
- Congestive cardiomyopathy (disorder)C0007193
- Congestive dilated cardiomyopathyC0007193
- DCMC0007193
- DCM - Dilated cardiomyopathyC0007193
- Dilated CardiomyopathiesC0007193
- Dilated CardiomyopathyC0007193
- Dilated cardiomyopathyC0007193
- Primary dilated cardiomyopathyC0007193
- Primary dilated cardiomyopathy (disorder)C0007193
- Stretched and thinned heart muscleC0007193
- cardiomyopathy congestiveC0007193
- cardiomyopathy dilatedC0007193
- congestive cardiomyopathyC0007193
- dilated cardiomyopathyC0007193
- primary dilated cardiomyopathyC0007193
Frequently Asked Questions
What is ICD-10 code I42.0?
ICD-10-CM code I42.0 represents "Dilated cardiomyopathy". It is a billable/specific code that can be used on a claim.
Is I42.0 a billable code?
Yes, I42.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is I42.0 in?
I42.0 is in Chapter 9: Diseases of the Circulatory System (codes I00-I99).
What SNOMED CT codes does I42.0 map to?
I42.0 maps to 73 SNOMED CT concepts: 398170002, 403795009, 399020009, 719451006, 16228931000119102, and 68 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for I42.0?
I42.0 is linked to 1 UMLS Concept Unique Identifier: C0007193. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.