I27.0
BillablePrimary pulmonary hypertension
Primary pulmonary hypertension
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Heritable pulmonary arterial hypertension
- Idiopathic pulmonary arterial hypertension
- Primary group 1 pulmonary hypertension
- Primary pulmonary arterial hypertension
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- systemic connective tissue disorders (M30-M36)
- transient cerebral ischemic attacks and related syndromes (G45.-)
Also Known As / Clinical Terms
SNOMED CT
- Idiopathic pulmonary arteriosclerosis49778009
- Ayerza syndrome78862003
- Ayerza's syndrome78862003
- Cardiopathia nigra78862003
- Cor pulmonale83291003
- Pulmonary heart disease83291003
- Right heart failure due to pulmonary hypertension83291003
- Sporadic primary pulmonary hypertension233943009
- Familial primary pulmonary hypertension233944003
- Finding of pulmonary arterial pressure301141002
- Observation of pulmonary arterial pressure301141002
- Heritable pulmonary arterial hypertension697897003
- Idiopathic pulmonary arterial hypertension697898008
- Heritable pulmonary arterial hypertension due to BMPR2 mutation697899000
- Heritable pulmonary arterial hypertension due to bone morphogenetic protein receptor type II mutation697899000
- Heritable pulmonary arterial hypertension due to ACVRL1 or endoglin mutation697900005
- Heritable pulmonary arterial hypertension due to ALK1 or endoglin mutation697900005
- Heritable pulmonary arterial hypertension due to activin A receptor type II-like kinase 1 or endoglin mutation697900005
- Pulmonary arterial pressure above reference range863928009
- Pulmonary arterial pressure increased863928009
- Right ventricular failure due to disorder of pulmonary circulation1208848007
- Right ventricular failure due to pulmonary vascular disease1208848007
UMLS
- FPPHC0340543
- Familial Primary Pulmonary HypertensionC0340543
- Familial primary pulmonary hypertensionC0340543
- Familial primary pulmonary hypertension (disorder)C0340543
- Familial pulmonary arterial hypertensionC0340543
- HPAHC0340543
- Heritable Pulmonary Arterial HypertensionC0340543
- Heritable pulmonary arterial hypertensionC0340543
- Heritable pulmonary arterial hypertension (disorder)C0340543
- Hypertension, Idiopathic PulmonaryC3203102
- Hypertension, Primary PulmonaryC3203102
- IPAHC3203102
- Idiopathic Pulmonary Arterial HypertensionC3203102
- Idiopathic Pulmonary HypertensionC3203102
- Idiopathic pulmonary arterial hypertensionC3203102
- Idiopathic pulmonary arterial hypertension (disorder)C3203102
- PAHC3203102
- PHTC3203102
- PULMONARY ARTERIAL HYPERTENSIONC3203102
- Primary pulmonary arterial hypertensionC3203102
- Pulmonary Hypertension, IdiopathicC3203102
- Pulmonary Hypertension, PrimaryC3203102
- Idiopathic pulmonary hypertensionC0152171
- PPHC0152171
- PPHTC0152171
- Primary Pulmonary HypertensionC0152171
- Primary pulmonary hypertensionC0152171
- Pulmonary hypertension primaryC0152171
- hypertension primary pulmonaryC0152171
- primary pulmonary hypertensionC0152171
- pulmonary primary hypertensionC0152171
- Primary group 1 pulmonary hypertensionC4509206
Frequently Asked Questions
What is ICD-10 code I27.0?
ICD-10-CM code I27.0 represents "Primary pulmonary hypertension". It is a billable/specific code that can be used on a claim.
Is I27.0 a billable code?
Yes, I27.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is I27.0 in?
I27.0 is in Chapter 9: Diseases of the Circulatory System (codes I00-I99).
What codes cannot be used with I27.0?
I27.0 has Excludes1 notes indicating codes that cannot be used together with it, including: persistent pulmonary hypertension of newborn (P29.30); pulmonary hypertension NOS (I27.20); secondary pulmonary arterial hypertension (I27.21); and 1 more.
What SNOMED CT codes does I27.0 map to?
I27.0 maps to 12 SNOMED CT concepts: 78862003, 83291003, 233944003, 301141002, 697897003, and 7 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for I27.0?
I27.0 is linked to 4 UMLS Concept Unique Identifiers: C0340543, C3203102, C0152171, C4509206. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.