G90.1
BillableFamilial dysautonomia [Riley-Day]
Familial dysautonomia [Riley-Day]
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- dysfunction of the autonomic nervous system due to alcohol (G31.2)
Excludes 2
Conditions not included here, but the patient may have both
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Also Known As / Clinical Terms
UMLS
- HSAN3C0013364
- HSN-IIIC0013364
- DYSC0013364
- DYSAUTONOMIA, FAMILIALC0013364
- Dominant Hereditary Sensory Neuropathy, Type IIIC0013364
- Dominant hereditary sensory neuropathy, type IIIC0013364
- Dysautonomia, FamilialC0013364
- Familial DysautonomiaC0013364
- Familial dysautonomiaC0013364
- Familial dysautonomia (disorder)C0013364
- Familial dysautonomia [Riley-Day]C0013364
- HSAN (Hereditary Sensory and Autonomic Neuropathy) Type IIIC0013364
- HSAN 3C0013364
- HSAN IIIC0013364
- HSAN Type IIIC0013364
- HSAN type IIIC0013364
- Hereditary Sensory Neuropathy Type 3C0013364
- Hereditary Sensory Neuropathy, Dominant, Type 3C0013364
- Hereditary Sensory Neuropathy, Dominant, Type IIIC0013364
- Hereditary Sensory Neuropathy, Type 3, DominantC0013364
- Hereditary Sensory and Autonomic Neuropathy 3C0013364
- Hereditary Sensory and Autonomic Neuropathy Type IIIC0013364
- Hereditary sensory and autonomic neuropathy type IIIC0013364
- Hereditary sensory and autonomic neuropathy, type IIIC0013364
- Hereditary-Sensory and Autonomic Neuropathy Type IIIC0013364
- NEUROPATHY, HEREDITARY SENSORY AND AUTONOMIC, TYPE IIIC0013364
- Neuropathy, Hereditary Sensory And Autonomic, Type IIIC0013364
- Neuropathy, Hereditary Sensory and Autonomic, Type IIIC0013364
- Neuropathy, Hereditary and Autonomic, Type IIIC0013364
- RILEY-DAY SYNDROMEC0013364
- Riley Day SyndromeC0013364
- Riley Day syndromeC0013364
- Riley-Day SyndromeC0013364
- Riley-Day syndromeC0013364
- Type 3 Hereditary Sensory Neuropathy, DominantC0013364
- Type III Hereditary Sensory Neuropathy, DominantC0013364
- dysautonomia familialC0013364
- familial autonomic nervous dysfunctionC0013364
- familial dysautonomiaC0013364
- riley day syndromeC0013364
- riley days syndromeC0013364
- riley-day syndromeC0013364
SNOMED CT
- Dominant hereditary sensory neuropathy, type III29159009
- Familial dysautonomia29159009
- HSAN III29159009
- Hereditary sensory and autonomic neuropathy type III29159009
- Hereditary sensory and autonomic neuropathy, type III29159009
- Riley-Day syndrome29159009
- Hereditary dysautonomia with motor neuropathy230557001
- Lisker Garcia Ramos syndrome230557001
- Peripheral motor neuropathy dysautonomia syndrome230557001
Frequently Asked Questions
What is ICD-10 code G90.1?
ICD-10-CM code G90.1 represents "Familial dysautonomia [Riley-Day]". It is a billable/specific code that can be used on a claim.
Is G90.1 a billable code?
Yes, G90.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is G90.1 in?
G90.1 is in Chapter 6: Diseases of the Nervous System (codes G00-G99).
What codes cannot be used with G90.1?
G90.1 has Excludes1 notes indicating codes that cannot be used together with it, including: dysfunction of the autonomic nervous system due to alcohol (G31.2).
What SNOMED CT codes does G90.1 map to?
G90.1 maps to 2 SNOMED CT concepts: 29159009, 230557001. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for G90.1?
G90.1 is linked to 1 UMLS Concept Unique Identifier: C0013364. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.