G31.89
BillableOther specified degenerative diseases of nervous system
Other specified degenerative diseases of nervous system
Coding Notes
Excludes 2
Conditions not included here, but the patient may have both
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- Reye's syndrome (G93.7)
Use Additional Code
Additional codes that should follow this code
- code, if applicable, for codes G31.0-G31.83, G31.85-G31.9, to identify:
- dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)
- dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)
- dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)
- dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)
- dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)
- mild neurocognitive disorder due to known physiological condition (F06.7-)
Also Known As / Clinical Terms
SNOMED CT
- Cerebral degeneration in childhood2584003
- Sporadic cerebellar degeneration21201006
- Hyperaminoaciduria42930003
- Inborn error of amino acid metabolism42930003
- Late cortical cerebellar atrophy43100002
- Marie-Foix-Alajouanine syndrome43100002
- Choreoathetosis43105007
- Corticostriatal spinal degeneration43977004
- Corticostriatal-spinal degeneration43977004
- INAD - Infantile neuroaxonal dystrophy52713000
- Infantile neuroaxonal dystrophy52713000
- Seitelberger disease52713000
- Seitelberger's disease52713000
- Spastic amaurotic axonal idiocy52713000
- Axonal neuropathy60703000
- Dejerine-Thomas syndrome67761004
- Déjérine-Thomas syndrome67761004
- OPCA - Olivopontocerebellar atrophy67761004
- Olivocerebellar atrophy67761004
- Olivopontocerebellar atrophy67761004
- Olivopontocerebellar degeneration67761004
- Thomas' syndrome67761004
- DRPLA - Dentatorubropallidoluysian atrophy68116008
- Dentatorubral-pallidoluysian atrophy68116008
- Dentatorubral-pallidoluysian atrophy (DRPLA)68116008
- Dentatorubropallidoluysian atrophy68116008
- Dentatorubropallidoluysian degeneration68116008
- Haw river syndrome68116008
- Myoclonic epilepsy with choreoathetosis68116008
- Naito-Oyanagi disease68116008
- Juvenile cerebellar degeneration AND myoclonus76156000
- Hereditary degenerative disease of central nervous system106018006
- Optic nerve finding106152006
- Second cranial nerve finding106152006
- Arteriopathic granular atrophy of cerebral cortex111028009
- Cerebellar ataxia associated with another disorder192874000
- Cerebellar deficiency syndrome224186005
- Cerebellar syndrome224186005
- Argyrophilic grain disease230281007
- Chronic hepatocerebral degeneration230305002
- Progressive neuronal degeneration of childhood230363006
- Lawrence-Cavanagh type230364000
- Progressive neuronal degeneration without liver cirrhosis230364000
- Neuroaxonal dystrophy230365004
- Late infantile and juvenile neuroaxonal dystrophy230366003
- Hereditary acantholytic dermatosis254217002
- 3-Methylglutaconic aciduria type 4297233004
- Congenital cerebellar cortical atrophy371313002
- Acute cerebellar syndrome417017003
- Generalised dystonia425492002
- Generalized dystonia425492002
- Disorder of valine metabolism444756000
- Cystic degeneration of brain445166009
- Huntington disease phenocopy syndrome702376003
- Huntington disease-like syndrome702376003
- Huntington disease-like syndrome disorder702376003
- Dysmyelinating leukodystrophy and spastic paraparesis702419001
- Fatty acid hydroxylase associated neurodegeneration702419001
- Spastic paraplegia 35702419001
- Mitochondrial membrane protein associated neurodegeneration709415008
- Mitochondrial protein associated neurodegeneration709415008
- Neurodegeneration with brain iron accumulation 4709415008
- 3-methylglutaconic aciduria type IV with sensorineural deafness, encephalopathy and Leigh-like syndrome711409002
- 3-methylglutaconic aciduria with deafness, encephalopathy, Leigh-like syndrome711409002
- 3-methylglutaconic aciduria with hearing loss, encephalopathy, Leigh-like syndrome711409002
- MEGDEL syndrome711409002
- Olivopontocerebellar atrophy and deafness715483009
- Olivopontocerebellar atrophy co-occurrent with sensorineural hearing loss715483009
- X-linked neurodegenerative syndrome Hamel type718847005
- X-linked neurodegenerative syndrome Bertini type718849008
- Corneal cerebellar syndrome720750004
- Der Kaloustian Jarudi Khoury syndrome720750004
- Spinocerebellar degeneration and corneal dystrophy syndrome720750004
- HIBCH-gene related deficiency of 3-hydroxyisobutyryl coenzyme A hydrolase722488009
- Methacrylic aciduria722488009
- Neurodegeneration due to 3-hydroxyisobutyryl coenzyme A hydrolase deficiency722488009
- Neurodegeneration due to 3-hydroxyisobutyryl-CoA hydrolase deficiency722488009
- Valine metabolic defect722488009
- Chorea due to heredodegenerative disorder722966004
- Keratosis follicularis, dwarfism, cerebral atrophy syndrome723830005
- Kufor Rakeb syndrome723992000
- PARK9 - Parkinson disease 9723992000
- Parkinson disease 9723992000
- H-ABC - hypomyelination, atrophy of basal ganglia and cerebellum724283004
- Hypomyelinating leucodystrophy with atrophy of basal ganglia and cerebellum724283004
- Hypomyelinating leukodystrophy with atrophy of basal ganglia and cerebellum724283004
- Hypomyelination with atrophy of basal ganglia and cerebellum syndrome724283004
- Chorea co-occurrent and due to Huntington disease-like condition724764007
- Chorea with Huntington disease-like condition724764007
- Chorea co-occurrent and due to dentatorubropallidoluysian degeneration724765008
- Chorea with dentatorubropallidoluysian degeneration724765008
- ADSD - autosomal dominant striatal neurodegeneration725392005
- Autosomal dominant striatal neurodegeneration725392005
- COASY protein-associated neurodegeneration732264002
- CoPAN - coenzyme A synthase protein associated neurodegeneration732264002
- Coenzyme A synthase protein associated neurodegeneration732264002
- Neurodegeneration with brain iron accumulation due to COASY mutation732264002
- BPAN - beta-propeller protein-associated neurodegeneration732959007
- Beta-propeller protein-associated neurodegeneration732959007
- Neurodegeneration with brain iron accumulation type 5732959007
- Static encephalopathy of childhood with neurodegeneration in adulthood732959007
- TUBB4A (tubulin beta 4A class IVa) related leukodystrophy769065000
- TUBB4A-related hypomyelinating leukodystrophy769065000
- TUBB4A-related leukodystrophy769065000
- Tubulin beta 4A class IVa related leukodystrophy769065000
- PEHO-like syndrome770678005
- PEHOL (progressive encephalopathy with edema, hypsarrhythmia, and optic atrophy-like) syndrome770678005
- PEHOL (progressive encephalopathy with oedema, hypsarrhythmia, and optic atrophy-like) syndrome770678005
- Progressive encephalopathy with edema, hypsarrhythmia, and optic atrophy-like syndrome770678005
- Progressive encephalopathy with oedema, hypsarrhythmia, and optic atrophy-like syndrome770678005
- Infantile cerebral and cerebellar atrophy with postnatal progressive microcephaly770725000
- Huntington disease-like 3770939009
- Early-onset progressive neurodegeneration, blindness, ataxia, spasticity syndrome771514002
- Severe neurodegenerative syndrome due to BSCL2 deficiency773555005
- Severe neurodegenerative syndrome due to BSCL2, seipin lipid droplet biogenesis associated deficiency773555005
- Severe neurodegenerative syndrome with lipodystrophy773555005
- PRKAR1B-related neurodegenerative dementia with intermediate filaments774069007
- Protein kinase cAMP-dependent type I regulatory subunit beta-related neurodegenerative dementia with intermediate filaments774069007
- Fatal post-viral neurodegenerative disorder774206008
- Autosomal recessive cerebral atrophy776087007
- Diffuse cerebral and cerebellar atrophy, intractable seizures, progressive microcephaly syndrome782737003
- C9ORF72-related Huntington disease phenocopy782743001
- Huntington disease-like syndrome due to C9ORF72 expansions782743001
- Huntington disease-like syndrome due to chromosome 9 open reading frame 72 expansions782743001
- Asparagine synthetase deficiency782757004
- Congenital microcephaly, severe encephalopathy, progressive cerebral atrophy syndrome782757004
- Infantile spasms, psychomotor retardation, progressive brain atrophy, basal ganglia disease syndrome782886007
- Early-onset prion disease with prominent psychiatric features784371009
- HDL1 - Huntington disease-like 1784371009
- Huntington disease-like 1784371009
- Alpha synuclein pathology785810000
- Alpha synucleinopathy785810000
- Synucleinopathy785810000
- Atrophy of pyramidal tract1144384000
- Atrophy of cerebellar vermis1144387007
- Diffuse atrophy of cerebellar structure1144426002
- Diffuse atrophy of cerebellum1144426002
- Diffuse atrophy of cerebral structure1144427006
- Diffuse atrophy of cerebrum1144427006
- Global brain atrophy1144430004
- Childhood-onset motor and cognitive regression syndrome with extrapyramidal movement disorder1167373005
- Early-onset progressive encephalopathy, hearing loss, pons hypoplasia, brain atrophy syndrome1169356004
- Early-onset progressive diffuse brain atrophy, microcephaly, muscle weakness, optic atrophy syndrome1172593006
- Global developmental delay, visual anomalies, progressive cerebellar atrophy, truncal hypotonia syndrome1172696009
- PCCA - progressive cerebello-cerebral atrophy1208481000
- Progressive cerebello-cerebral atrophy1208481000
- Degeneration of pineal gland1217040009
- Pineal degeneration1217040009
- Pineal gland degeneration1217040009
- GPAA1-related biosynthesis defect1217381009
- Glycosylphosphatidylinositol anchor attachment 1-related biosynthesis defect1217381009
- Neurodevelopmental delay, seizures, ophthalmic anomalies, osteopenia, cerebellar atrophy syndrome1217381009
- PCNA-related progressive neurodegenerative photosensitivity syndrome1228871002
- Proliferating cell nuclear antigen-related progressive neurodegenerative photosensitivity syndrome1228871002
- Autosomal recessive childhood-onset dystonia DYT29 type1236805005
- Childhood-onset generalised dystonia, optic atrophy syndrome1236805005
- Childhood-onset generalized dystonia, optic atrophy syndrome1236805005
- DYT29 - dystonia 291236805005
- MEPAN syndrome1236805005
- Mitochondrial enoyl coenzyme A reductase protein-associated neurodegeneration syndrome1236805005
- CARKD deficiency1251446004
- NAD(P)HX dehydratase deficiency1251446004
- Apolipoprotein A-I binding protein deficiency1251447008
- NAD(P)HX epimerase deficiency1251447008
- USP18 deficiency1251449006
- Ubiquitin specific peptidase 18 deficiency1251449006
- Combined cerebellar and peripheral ataxia, deafness, diabetes mellitus syndrome1255271005
- Combined cerebellar and peripheral ataxia, hearing loss, diabetes mellitus syndrome1255271005
- Juvenile-onset diabetes mellitus, central and peripheral neurodegeneration syndrome1255271005
- Type 1 diabetes mellitus, central and peripheral neurodegeneration syndrome1255271005
- Autoimmune cerebellar degeneration1259088002
- Autoimmune degeneration of cerebellum1259088002
- Chorea due to Huntington disease-like 31259685000
- Chorea due to Huntington disease-like 21259689006
- Chorea due to hereditary ataxia1259691003
- Chorea due to Huntington disease-like 11259694006
- Chorea due to chronic hepatocerebral degeneration1259703003
- ANOAC (axonal neuropathy, optic atrophy, cognitive deficit) syndrome1260129000
- Axonal neuropathy, optic atrophy, cognitive deficit syndrome1260129000
- Infantile-onset axonal motor and sensory neuropathy, optic atrophy, neurodegenerative syndrome1260129000
- HPDL (4-hydroxyphenylpyruvate dioxygenase like) related infantile neurodegeneration, progressive spasticity, intellectual disability, white matter lesions syndrome1303585005
- HPDL-related Leigh-like encephalopathy1303585005
- HPDL-related infantile neurodegeneration, progressive spasticity, intellectual disability, white matter lesions syndrome1303585005
- Infantile neurodegeneration, progressive spasticity, intellectual disability, white matter lesions syndrome1303585005
- CLCN6-related childhood-onset progressive neurodegeneration, peripheral neuropathy syndrome1340172003
- Chloride voltage-gated channel 6-related childhood-onset progressive neurodegeneration, peripheral neuropathy syndrome1340172003
- Atrophy of corticospinal tract1363021001
- Early-onset neurodegeneration, choreoathetoid movement, microcytic anaemia due to IREB2 mutation1366590005
- Early-onset neurodegeneration, choreoathetoid movement, microcytic anaemia due to iron responsive element binding protein 2 gene mutation1366590005
- Early-onset neurodegeneration, choreoathetoid movement, microcytic anemia due to IREB2 mutation1366590005
- Early-onset neurodegeneration, choreoathetoid movement, microcytic anemia due to iron responsive element binding protein 2 gene mutation1366590005
- NDCAMA - neurodegeneration, choreoathetoid movement, microcytic anaemia1366590005
- NDCAMA - neurodegeneration, choreoathetoid movement, microcytic anemia1366590005
- Acquired atrophy of cerebellum800703961000119100
- Acquired cerebellar atrophy800703961000119100
- Hereditary cerebellar atrophy431641000124107
- Progressive chorea27751000119104
Frequently Asked Questions
What is the ICD-10 code for other specified degenerative diseases of nervous system?
The ICD-10-CM code for other specified degenerative diseases of nervous system is G31.89. The full clinical description is "Other specified degenerative diseases of nervous system". G31.89 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code G31.89 mean?
ICD-10-CM code G31.89 represents "Other specified degenerative diseases of nervous system". It is classified under Chapter 6: Diseases of the Nervous System and is a billable/specific code that can be used on a claim.
Is G31.89 a billable code?
Yes, G31.89 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is G31.89 in?
G31.89 is in Chapter 6: Diseases of the Nervous System (codes G00-G99).
Are additional codes required with G31.89?
Yes, when using G31.89 you should also code: code, if applicable, for codes G31.0-G31.83, G31.85-G31.9, to identify:; dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4); dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-); dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3); dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2); dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0); mild neurocognitive disorder due to known physiological condition (F06.7-).
What SNOMED CT codes does G31.89 map to?
G31.89 maps to 94 SNOMED CT concepts: 297233004, 711409002, 725392005, 1260129000, 800703961000119100, and 89 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for G31.89?
G31.89 is linked to 1 UMLS Concept Unique Identifier: C0477365. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.