G11.9
BillableHereditary ataxia, unspecified
Hereditary ataxia, unspecified
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Hereditary cerebellar ataxia NOS
- Hereditary cerebellar degeneration
- Hereditary cerebellar disease
- Hereditary cerebellar syndrome
Excludes 2
Conditions not included here, but the patient may have both
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- cerebral palsy (G80.-)
- hereditary and idiopathic neuropathy (G60.-)
- metabolic disorders (E70-E88)
Also Known As / Clinical Terms
SNOMED CT
- Primary cerebellar degeneration23732000
- Cerebral ataxia28634005
- Primary hypersomnia36124002
- Hereditary cerebellar degeneration37650008
- Choreoathetosis43105007
- Paroxysmal choreoathetosis49949003
- Paroxysmal dyskinesia49949003
- Retinitis pigmentosa-deafness syndrome57838006
- Usher syndrome57838006
- Usher's syndrome57838006
- Gelineau's syndrome60380001
- Narcolepsy60380001
- Narcoleptic syndrome60380001
- Paroxysmal sleep60380001
- Hallgren's syndrome73119000
- Retinitis pigmentosa-deafness-ataxia syndrome73119000
- Hereditary choroidal atrophy74469006
- Hereditary choroidal dystrophy74469006
- Cerebellar ataxia85102008
- Holmes' disease85592008
- Primary progressive cerebellar degeneration85592008
- Posthemiplegic ataxia90791004
- Spinocerebellar disease91502009
- Cerebellar ataxia associated with another disorder192874000
- Progressive cerebellar ataxia230233000
- Paroxysmal dystonia230310003
- Chronic deafness232325008
- Cutaneous syndrome with ichthyosis239057002
- Conorenal syndrome254092004
- Renal dysplasia, retinal pigmentary dystrophy, cerebellar ataxia, skeletal dysplasia syndrome254092004
- Saldino-Mainzer dysplasia254092004
- Ichthyosis, cerebellar degeneration and hepatosplenomegaly403779009
- Episodic ataxia421455009
- Fragile X associated tremor ataxia syndrome448045004
- AOA1 (ataxia oculomotor apraxia type 1)715366004
- Ataxia oculomotor apraxia type 1715366004
- Autosomal recessive ataxia with oculomotor apraxia type 1715366004
- Autosomal recessive cerebellar ataxia with oculomotor apraxia type 1715366004
- Cerebellar ataxia and ectodermal dysplasia715371006
- Cerebellar ataxia co-occurrent with ectodermal dysplasia715371006
- Dystonia 9715564000
- Paroxysmal dystonic choreoathetosis with episodic ataxia and spasticity715564000
- Boucher Neuhäuser syndrome715984007
- Cerebellar ataxia with hypogonadism and choroidal dystrophy syndrome715984007
- Episodic ataxia type 7718752007
- Congenital cataract with ataxia and deafness syndrome719102004
- Ataxia with deafness and intellectual disability syndrome720517001
- Reardon Baraitser syndrome720517001
- CAPOS (cerebellar ataxia, areflexia, pes cavus, optic atrophy, sensorineural hearing loss) syndrome720634003
- Cerebellar ataxia, areflexia, pes cavus, optic atrophy, sensorineural hearing loss syndrome720634003
- EAST (epilepsy, ataxia, sensorineural deafness, and tubulopathy) syndrome721207002
- SESAME (seizures, sensorineural deafness, ataxia, mental retardation, electrolyte imbalance) syndrome721207002
- SESAME syndrome721207002
- Seizure, sensorineural deafness, ataxia, intellectual disability, electrolyte imbalance syndrome721207002
- Autosomal dominant cerebellar ataxia, deafness and narcolepsy syndrome722293005
- Ataxia due to mitochondrial mutations722967008
- ARCA2 - autosomal recessive cerebellar ataxia type 2725394006
- Autosomal recessive ataxia due to coenzyme Q10 deficiency725394006
- Autosomal recessive ataxia due to ubiquinone deficiency725394006
- Autosomal recessive spinocerebellar ataxia type 9725394006
- AOA2 - ataxia oculomotor apraxia type 2725408001
- Autosomal recessive cerebellar ataxia with oculomotor apraxia type 2725408001
- SCAR1 - spinocerebellar ataxia autosomal recessive 1725408001
- Spinocerebellar ataxia with axonal neuropathy type 2725408001
- Myoclonus, cerebellar ataxia, deafness syndrome733065003
- Hereditary ataxia763597000
- Early-onset progressive neurodegeneration, blindness, ataxia, spasticity syndrome771514002
- Autosomal recessive cerebellar ataxia, epilepsy, intellectual disability syndrome due to TUD deficiency773498006
- SCAR23 - spinocerebellar ataxia autosomal recessive type 23773498006
- Spinocerebellar ataxia autosomal recessive type 23773498006
- Gemignani syndrome782690007
- Spinocerebellar ataxia, amyotrophy, deafness syndrome782690007
- Autosomal recessive cerebellar ataxia due to STIP1 homology and U-box containing protein 1 deficiency782719004
- Autosomal recessive cerebellar ataxia due to STUB1 (STIP1 homology and U-box containing protein 1) deficiency782719004
- Autosomal recessive cerebellar ataxia due to STUB1 deficiency782719004
- SCAR16 - spinocerebellar ataxia autosomal recessive type 16782719004
- Spinocerebellar ataxia autosomal recessive type 16782719004
- Autosomal recessive cerebellar ataxia, epilepsy, intellectual disability syndrome due to RUBCN deficiency782721009
- Autosomal recessive cerebellar ataxia, epilepsy, intellectual disability syndrome due to RUN and cysteine rich domain containing beclin 1 interacting protein deficiency782721009
- Autosomal recessive cerebellar ataxia-epilepsy-intellectual disability syndrome due to RUBCN (RUN and cysteine rich domain containing beclin 1 interacting protein) deficiency782721009
- Autosomal recessive spinocerebellar ataxia type 15782721009
- SCAR15 - autosomal recessive spinocerebellar ataxia type 15782721009
- Salih ataxia782721009
- Infantile cerebellar and retinal degeneration782822006
- Ataxia with tapetoretinal degeneration syndrome783203003
- X-linked progressive cerebellar ataxia827172005
- Non-progressive cerebellar ataxia1119354003
- AOA4 - ataxia, oculomotor apraxia type 41217230002
- Cerebellar ataxia with oculomotor apraxia type 41217230002
- Optic atrophy, ataxia, peripheral neuropathy, global developmental delay syndrome1222655009
- Chorea due to hereditary ataxia1259691003
- PADDAS syndrome1260097007
- PUM1-associated developmental disability, ataxia, seizure syndrome1260097007
- Pumilio RNA binding family member 1-associated developmental disability, ataxia, seizure syndrome1260097007
- SCA47 - spinocerebellar ataxia type 471260097007
- Cerebellar ataxia, brain abnormalities, cardiac conduction defects syndrome1303586006
- Neurodevelopmental delay, hypotonia, cerebellar ataxia, cardiac conduction defects syndrome1303586006
- Neurodevelopmental delay, hypotonia, cerebellar atrophy, cardiac conduction defects syndrome1303586006
- Hereditary cerebellar atrophy431641000124107
- Retinal pigment epithelial dystrophy342581000119102
UMLS
- Cerebellar Ataxia, MarieC0270749
- Cerebellar Ataxia, Marie'sC0270749
- Hereditary Cerebellar AtaxiaC0270749
- Hereditary cerebellar ataxiaC0270749
- Hereditary cerebellar ataxia NOSC0270749
- Marie Cerebellar AtaxiaC0270749
- Marie cerebellar ataxiaC0270749
- Marie's Cerebellar AtaxiaC0270749
- Marie's cerebellar ataxiaC0270749
- Marie's cerebellar ataxia (disorder)C0270749
- familial cerebellar ataxiaC0270749
- hereditary cerebellar ataxiaC0270749
- marie's ataxiaC0270749
- Hereditary ataxia NOSC5779602
- Hereditary ataxia, unspecifiedC5779602
- Hereditary cerebellar degenerationC0270752
- Hereditary cerebellar degeneration (disorder)C0270752
- hereditary cerebellar degenerationC0270752
- Hereditary cerebellar diseaseC2875048
- Hereditary cerebellar syndromeC2875049
Frequently Asked Questions
What is ICD-10 code G11.9?
ICD-10-CM code G11.9 represents "Hereditary ataxia, unspecified". It is a billable/specific code that can be used on a claim.
Is G11.9 a billable code?
Yes, G11.9 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is G11.9 in?
G11.9 is in Chapter 6: Diseases of the Nervous System (codes G00-G99).
What SNOMED CT codes does G11.9 map to?
G11.9 maps to 54 SNOMED CT concepts: 715366004, 725408001, 1217230002, 725394006, 722967008, and 49 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for G11.9?
G11.9 is linked to 5 UMLS Concept Unique Identifiers: C0270749, C5779602, C0270752, C2875048, C2875049. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.