AutoICD API

E88.01

Billable

Alpha-1-antitrypsin deficiency

Alpha-1-antitrypsin deficiency

Status

Billable / Specific

Block

E70-E88

Parent Code

E88.0

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • AAT deficiency

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
  • histiocytosis X (chronic) (C96.6)
  • monoclonal gammopathy (of undetermined significance) (D47.2)
  • polyclonal hypergammaglobulinemia (D89.0)
  • Waldenström macroglobulinemia (C88.00)

Excludes 2

Conditions not included here, but the patient may have both

  • Ehlers-Danlos syndromes (Q79.6-)
  • disorder of lipoprotein metabolism (E78.-)

Use Additional Code

Additional codes that should follow this code

  • codes for associated conditions

Also Known As / Clinical Terms

SNOMED CT

UMLS

Frequently Asked Questions

What is the ICD-10 code for alpha-1-antitrypsin deficiency?

The ICD-10-CM code for alpha-1-antitrypsin deficiency is E88.01. The full clinical description is "Alpha-1-antitrypsin deficiency". E88.01 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code E88.01 mean?

ICD-10-CM code E88.01 represents "Alpha-1-antitrypsin deficiency". It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.

Is E88.01 a billable code?

Yes, E88.01 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is E88.01 in?

E88.01 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).

What codes cannot be used with E88.01?

E88.01 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 7 more.

Are additional codes required with E88.01?

Yes, when using E88.01 you should also code: codes for associated conditions.

What SNOMED CT codes does E88.01 map to?

E88.01 maps to 5 SNOMED CT concepts: 403415009, 30188007, 190944000, 402687009, 233674008. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for E88.01?

E88.01 is linked to 1 UMLS Concept Unique Identifier: C0221757. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.