E76.29
BillableOther mucopolysaccharidoses
Other mucopolysaccharidoses
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- beta-Glucuronidase deficiency
- Maroteaux-Lamy (mild) (severe) syndrome
- Mucopolysaccharidosis, types VI, VII
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- Ehlers-Danlos syndromes (Q79.6-)
Also Known As / Clinical Terms
SNOMED CT
- Maroteaux-Lamy syndrome, intermediate form26015003
- Beta-glucuronidase deficiency43916004
- GUSB deficiency43916004
- MPS VII - Mucopolysaccharidosis VII43916004
- Mucopolysaccharidosis type VII43916004
- Mucopolysaccharidosis, MPS-VII43916004
- Sly disease43916004
- Sly syndrome43916004
- Deficiency of N-acetylgalactosamine-4-sulfatase52677002
- Deficiency of N-acetylgalactosamine-4-sulphatase52677002
- Maroteaux-Lamy syndrome, severe form58263000
- Deficiency of cerebroside-sulfatase66521008
- Deficiency of cerebroside-sulphatase66521008
- Maroteaux-Lamy syndrome, mild form67854007
- ARSB - Arylsulfatase B deficiency69463008
- ARSB - Arylsulphatase B deficiency69463008
- ARSB deficiency69463008
- Arylsulfatase B deficiency69463008
- Arylsulphatase B deficiency69463008
- MPS VI - Mucopolysaccharidosis VI69463008
- Maroteaux-Lamy disease69463008
- Maroteaux-Lamy syndrome69463008
- Mucopolysaccharidosis chondroitin sulfate B69463008
- Mucopolysaccharidosis chondroitin sulphate B69463008
- Mucopolysaccharidosis type VI69463008
- Mucopolysaccharidosis, MPS-VI69463008
- N-acetylgalactosamine-4-sulfatase deficiency69463008
- N-acetylgalactosamine-4-sulphatase deficiency69463008
- Polydystrophic dwarfism69463008
UMLS
- BETA-GLUCURONIDASE DEFICIENCYC0085132
- Beta-Glucuronidase DeficiencyC0085132
- Beta-glucuronidase deficiencyC0085132
- Deficiencies, GUSBC0085132
- Deficiencies, beta-GlucuronidaseC0085132
- Deficiency of beta-glucuronidaseC0085132
- Deficiency of beta-glucuronidase (disorder)C0085132
- Deficiency, GUSBC0085132
- Deficiency, beta-GlucuronidaseC0085132
- Disease, SlyC0085132
- GUSB DEFICIENCYC0085132
- GUSB DeficienciesC0085132
- GUSB DeficiencyC0085132
- GUSB deficiencyC0085132
- MPS 7C0085132
- MPS VIIC0085132
- MPS VII - Mucopolysaccharidosis VIIC0085132
- MPS7C0085132
- MUCOPOLYSACCHARIDOSIS, TYPE VIIC0085132
- Mucopolysaccharidosis 7C0085132
- Mucopolysaccharidosis Type VIIC0085132
- Mucopolysaccharidosis Type VIIsC0085132
- Mucopolysaccharidosis VIIC0085132
- Mucopolysaccharidosis VIIsC0085132
- Mucopolysaccharidosis type VIIC0085132
- Mucopolysaccharidosis type VII (disorder)C0085132
- Mucopolysaccharidosis, MPS-VIIC0085132
- SLY DISC0085132
- SLY SYNDROMEC0085132
- Sly DiseaseC0085132
- Sly SyndromeC0085132
- Sly diseaseC0085132
- Sly syndromeC0085132
- Sly's syndromeC0085132
- Syndrome, SlyC0085132
- Type VII, MucopolysaccharidosisC0085132
- Type VIIs, MucopolysaccharidosisC0085132
- VIIs, MucopolysaccharidosisC0085132
- beta Glucuronidase DeficiencyC0085132
- beta-Glucuronidase DeficienciesC0085132
- beta-Glucuronidase DeficiencyC0085132
- beta-Glucuronidase deficiencyC0085132
- mucopolysaccharidosis type VIIC0085132
- sly diseaseC0085132
- sly syndromeC0085132
- Maroteaux-Lamy (mild) (severe) syndromeC2874283
- Mucopolysaccharidosis, types VI, VIIC2874284
- Other mucopolysaccharidosesC0348491
Frequently Asked Questions
What is the ICD-10 code for other mucopolysaccharidoses?
The ICD-10-CM code for other mucopolysaccharidoses is E76.29. The full clinical description is "Other mucopolysaccharidoses". E76.29 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E76.29 mean?
ICD-10-CM code E76.29 represents "Other mucopolysaccharidoses". It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E76.29 a billable code?
Yes, E76.29 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E76.29 in?
E76.29 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E76.29?
E76.29 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What SNOMED CT codes does E76.29 map to?
E76.29 maps to 7 SNOMED CT concepts: 69463008, 43916004, 52677002, 66521008, 26015003, and 2 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E76.29?
E76.29 is linked to 4 UMLS Concept Unique Identifiers: C0085132, C2874283, C2874284, C0348491. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.