E76.22

Billable

Sanfilippo mucopolysaccharidoses

Sanfilippo mucopolysaccharidoses

Status

Billable / Specific

Block

E70-E88

Parent Code

E76.2

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Mucopolysaccharidosis, type III (A) (B) (C) (D)
  • Sanfilippo A syndrome
  • Sanfilippo B syndrome
  • Sanfilippo C syndrome
  • Sanfilippo D syndrome

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Excludes 2

Conditions not included here, but the patient may have both

  • Ehlers-Danlos syndromes (Q79.6-)

Also Known As / Clinical Terms

SNOMED CT

UMLS

Frequently Asked Questions

What is the ICD-10 code for sanfilippo mucopolysaccharidoses?

The ICD-10-CM code for sanfilippo mucopolysaccharidoses is E76.22. The full clinical description is "Sanfilippo mucopolysaccharidoses". E76.22 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code E76.22 mean?

ICD-10-CM code E76.22 represents "Sanfilippo mucopolysaccharidoses". It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.

Is E76.22 a billable code?

Yes, E76.22 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is E76.22 in?

E76.22 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).

What codes cannot be used with E76.22?

E76.22 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.

What SNOMED CT codes does E76.22 map to?

E76.22 maps to 5 SNOMED CT concepts: 75238000, 59990008, 15892005, 41572006, 88393000. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for E76.22?

E76.22 is linked to 6 UMLS Concept Unique Identifiers: C0086649, C0086648, C0086650, C0086647, C2874281, and 1 more. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.