E74.89
BillableOther specified disorders of carbohydrate metabolism
Other specified disorders of carbohydrate metabolism
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Essential pentosuria
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
- diabetes mellitus (E08-E13)
- hypoglycemia NOS (E16.2)
- increased secretion of glucagon (E16.3)
- mucopolysaccharidosis (E76.0-E76.3)
Excludes 2
Conditions not included here, but the patient may have both
- Ehlers-Danlos syndromes (Q79.6-)
Also Known As / Clinical Terms
SNOMED CT
- Disacchariduria1038000
- Non glucose melituria3427001
- Nonglucosuric melituria3427001
- Xylosuria23860007
- Syndrome of carbohydrate intolerance29736007
- Pentose disorder57507002
- GSD X - glycogen storage disease type X61772003
- Glycogen storage disease type X61772003
- Muscle phosphoglycerate mutase deficiency61772003
- Phosphoglucomutase deficiency61772003
- Alpha, alpha-trehalase deficiency84193000
- Trehalase deficiency84193000
- Trehalose intolerance84193000
- Deficiency of ALR2124109002
- Deficiency of aldehyde reductase124109002
- Deficiency of polyol dehydrogenase (NADP^+^)124109002
- Deficiency of glucose dehydrogenase124132003
- Deficiency of glucose oxidase124143006
- Deficiency of glucose oxyhydrase124143006
- Deficiency of gluconate 2-dehydrogenase124150005
- Deficiency of benzaldehyde dehydrogenase (NADP^+^)124156004
- Deficiency of benzaldehyde dehydrogenase (nicotinamide adenine dinucleotide phosphate ^+^)124156004
- Deficiency of glyceraldehyde-3-phosphate dehydrogenase124158003
- Deficiency of triosephosphate dehydrogenase124158003
- Deficiency of maltose phosphorylase124266003
- Deficiency of glucokinase124298009
- Deficiency of rhamnulokinase124301008
- Deficiency of mannokinase124303006
- Deficiency of glucose-phosphate kinase124305004
- Deficiency of phosphoglucokinase124305004
- Deficiency of gluconokinase124307007
- Deficiency of xylulokinase124312008
- Deficiency of glycerol kinase124322002
- Familial hyperglycerolaemia124322002
- Familial hyperglycerolemia124322002
- GK1 deficiency124322002
- GKD - Glycerol kinase deficiency124322002
- Glycerol kinase deficiency124322002
- Hyperglycerolaemia124322002
- Hyperglycerolemia124322002
- Deficiency of phosphoglycerate kinase124335006
- Deficiency of glycosyltransferase124386001
- Deficiency of transglycosylase124386001
- Deficiency of glucose-1-phosphatase124438009
- Deficiency of bisphosphoglycerate phosphatase124440004
- Deficiency of glucosulfatase124448006
- Deficiency of glucosulphatase124448006
- Deficiency of glycosulfatase124448006
- Deficiency of glycosulphatase124448006
- Deficiency of alpha-amylase124452006
- Deficiency of glycogenase124452006
- Deficiency of beta-amylase124453001
- Deficiency of saccharogen amylase124453001
- Deficiency of endo-1,3(4)-beta-glucanase124456009
- Deficiency of endo-1,3-beta-glucanase124456009
- Deficiency of laminarinase124456009
- Deficiency of amygdalase124463009
- Deficiency of beta-glucosidase124463009
- Deficiency of cellobiase124463009
- Deficiency of gentiobiase124463009
- Deficiency of alpha-mannosidase124466001
- Deficiency of beta-fructofuranosidase124467005
- Deficiency of invertase124467005
- Deficiency of saccharase124467005
- Deficiency of beta-glucuronidase124470009
- Deficiency of 6-alpha-D-glucosidase124472001
- Deficiency of amylo-1,6-glucosidase124472001
- Deficiency of dextrin124472001
- Deficiency of exo-1,3-alpha-glucanase124476003
- Deficiency of glucan 1,3-alpha-glucosidase124476003
- Deficiency of aldose 1-epimerase124663000
- Deficiency of aldose mutarotase124663000
- Deficiency of mutarotase124663000
- Deficiency of glucose-6-phosphate isomerase124669001
- Deficiency of hexosephosphate isomerase124669001
- Deficiency of oxoisomerase124669001
- Deficiency of phosphoglucoisomerase124669001
- Deficiency of phosphohexose isomerase124669001
- Deficiency of glucosamine-6-phosphate isomerase124670000
- Deficiency of bisphosphoglycerate mutase124678007
- Deficiency of bisphosphoglycerate synthase124678007
- Deficiency of diphosphoglycerate mutase124678007
- Deficiency of glycerate phosphomutase124678007
- Disorder of glucose metabolism126877002
- Essential benign pentosuria190764000
- Essential pentosuria190764000
- L-xylulose reductase deficiency190764000
- L-xylulosuria190764000
- Xylitol dehydrogenase deficiency190764000
- HIES - hyperimmunoglobulin E syndrome191009009
- Hyper-IgE syndrome191009009
- Hyperimmunoglobulin E syndrome191009009
- Genetically determined myasthenia230669004
- Congenital myasthenia230672006
- Congenital myasthenia syndrome230672006
- Congenital myasthenic syndrome230672006
- Disorder of glucose regulation237597000
- Disorder of glycerol metabolism237977000
- Glycerol intolerance syndrome237978005
- Disorder of glycerate metabolism237979002
- D-Glyceric aciduria237980004
- Deficiency of amylopectin 6-glucanohydrolase272064009
- Glycerol kinase deficiency - isolated297256008
- Deficiency of amylase302250008
- Deficiency of glycosidase302661005
- Deficiency of aldonolactonase360686003
- Deficiency of gluconolactonase360697003
- Deficiency of protein kinase387814004
- Deficiency of phosphorylase b kinase387817006
- Carbohydrate deficient glycoprotein syndrome type 1c709412006
- Carbohydrate deficient glycoprotein syndrome type V709412006
- Congenital disorder of glycosylation type 1c709412006
- ALG12-congenital disorder of glycosylation711155008
- Congenital disorder of glycosylation type 1G711155008
- Congenital disorder of glycosylation type Ig711155008
- Deficiency of phosphomannomutase 2712640001
- Deficiency of glucosyltransferase 1712641002
- COG7 (component of oligomeric golgi complex 7) congenital disorder of glycosylation717773005
- COG7 congenital disorder of glycosylation717773005
- Carbohydrate deficient glycoprotein syndrome type IIe717773005
- Component of oligomeric golgi complex 7 congenital disorder of glycosylation717773005
- Congenital disorder of glycosylation type 2e717773005
- Congenital disorder of glycosylation type IIe717773005
- COG8 (component of oligomeric golgi complex 8) congenital disorder of glycosylation717774004
- COG8 congenital disorder of glycosylation717774004
- Carbohydrate deficient glycoprotein syndrome type IIh717774004
- Component of oligomeric golgi complex 8 congenital disorder of glycosylation717774004
- Congenital disorder of glycosylation type 2h717774004
- Congenital disorder of glycosylation type IIh717774004
- CDG2G - carbohydrate deficient glycoprotein syndrome type 2G718750004
- COG1 (component of oligomeric golgi complex 1) congenital disorder of glycosylation718750004
- COG1 congenital disorder of glycosylation718750004
- Carbohydrate deficient glycoprotein syndrome type 2g718750004
- Carbohydrate deficient glycoprotein syndrome type IIg718750004
- Component of oligomeric golgi complex 1 congenital disorder of glycosylation718750004
- Congenital disorder of glycosylation type IIg718750004
- CDG2J - carbohydrate deficient glycoprotein syndrome type 2J718751000
- COG4 (component of oligomeric golgi complex 4) congenital disorder of glycosylation718751000
- COG4 congenital disorder of glycosylation718751000
- Carbohydrate deficient glycoprotein syndrome type 2j718751000
- Carbohydrate deficient glycoprotein syndrome type IIj718751000
- Component of oligomeric golgi complex 4 congenital disorder of glycosylation718751000
- ALG1 congenital disorder of glycosylation720941007
- ALG1-CDG - asparagine-linked glycosylation 1 congenital disorder of glycosylation720941007
- Asparagine-linked glycosylation 1 congenital disorder of glycosylation720941007
- Carbohydrate deficient glycoprotein syndrome type Ik720941007
- Congenital disorder of glycosylation type 1K720941007
- Mannosyltransferase 1 deficiency720941007
- ALG3 congenital disorder of glycosylation720976009
- ALG3-CDG - asparagine-linked glycosylation 3 congenital disorder of glycosylation720976009
- Asparagine-linked glycosylation 3 congenital disorder of glycosylation720976009
- Carbohydrate deficient glycoprotein syndrome type Id720976009
- Congenital disorder of glycosylation type 1d720976009
- Congenital disorder of glycosylation type Id720976009
- Mannosyltransferase 6 deficiency720976009
- ALG8 congenital disorder of glycosylation720977000
- ALG8-CDG - asparagine-linked glycosylation 8 congenital disorder of glycosylation720977000
- Asparagine-linked glycosylation 8 congenital disorder of glycosylation720977000
- Carbohydrate deficient glycoprotein syndrome type Ih720977000
- Congenital disorder of glycosylation type 1h720977000
- Congenital disorder of glycosylation type Ih720977000
- Glucosyltransferase 2 deficiency720977000
- ALG9 congenital disorder of glycosylation720978005
- ALG9-CDG - asparagine-linked glycosylation 9 congenital disorder of glycosylation720978005
- Asparagine-linked glycosylation 9 congenital disorder of glycosylation720978005
- Carbohydrate deficient glycoprotein syndrome type IL720978005
- Congenital disorder of glycosylation type 1L720978005
- Congenital disorder of glycosylation type IL720978005
- Mannosyltransferase 7-9 deficiency720978005
- CDG2I - carbohydrate deficient glycoprotein syndrome type IIi721100009
- COG5 (component of oligomeric golgi complex 5) congenital disorder of glycosylation721100009
- COG5 congenital disorder of glycosylation721100009
- Carbohydrate deficient glycoprotein syndrome type IIi721100009
- Component of oligomeric golgi complex 5 congenital disorder of glycosylation721100009
- Congenital disorder of glycosylation type IIi721100009
- CMP-sialic acid transporter deficiency723624008
- Carbohydrate deficient glycoprotein syndrome type IIf723624008
- Congenital disorder of glycosylation type 2f723624008
- Congenital disorder of glycosylation type IIf723624008
- SLC35A1 (solute carrier family 35 member A1) congenital disorder of glycosylation723624008
- SLC35A1 congenital disorder of glycosylation723624008
- Solute carrier family 35 member A1 congenital disorder of glycosylation723624008
- Carbohydrate deficient glycoprotein syndrome type If724096007
- Congenital disorder of glycosylation type 1f724096007
- MPDU1-CDG - mannose-P-dolichol utilisation defect 1 - congenital disorder of glycosylation724096007
- MPDU1-CDG - mannose-P-dolichol utilization defect 1 - congenital disorder of glycosylation724096007
- Mannose-P-dolichol utilisation defect 1724096007
- Mannose-P-dolichol utilization defect 1724096007
- Carbohydrate deficient glycoprotein syndrome type IIb725028009
- Congenital disorder of glycosylation type 2b725028009
- Congenital disorder of glycosylation type IIb725028009
- Glucosidase 1 deficiency725028009
- MOGS CDG - mannosyl-oligosaccharide glycosidase congenital disorder of glycosylation725028009
- Mannosyl-oligosaccharide glycosidase congenital disorder of glycosylation725028009
- Carbohydrate deficient glycoprotein syndrome type Ie725078006
- Congenital disorder of glycosylation type 1e725078006
- DPM1-CDG - dolichyl-phosphate mannosyltransferase 1 catalytic subunit congenital disorder of glycosylation725078006
- Dolichol-phosphate-mannose synthase 1 deficiency725078006
- Carbohydrate deficient glycoprotein syndrome type Ij725079003
- Congenital disorder of glycosylation type 1j725079003
- Congenital disorder of glycosylation type Ij725079003
- DPAGT1-CDG - dolichyl-phosphate n-acetylglucosamine phosphotransferase congenital disorder of glycosylation725079003
- Dolichyl-phosphate N-acetylgalactosamine phosphotransferase deficiency725079003
- Carbohydrate deficient glycoprotein syndrome type Ir733083006
- Congenital disorder of glycosylation type 1r733083006
- Congenital disorder of glycosylation type Ir733083006
- DDOST-CDG - dolichyl-diphosphooligosaccharide-protein glycosyltransferase congenital disorder of glycosylation733083006
- Dolichyl-diphosphooligosaccharide-protein glycosyltransferase congenital disorder of glycosylation733083006
- Carbohydrate deficient glycoprotein syndrome type In733084000
- Congenital disorder of glycosylation type 1n733084000
- Congenital disorder of glycosylation type In733084000
- Man5GlcNAc2-dolichylpyrophosphate flippase deficiency733084000
- RFT1-CDG (congenital disorder of glycosylation)733084000
- RFT1-congenital disorder of glycosylation733084000
- ALG11-CDG - asparagine-linked glycosylation 11 congenital disorder of glycosylation733085004
- Asparagine-linked glycosylation 11 congenital disorder of glycosylation733085004
- Carbohydrate deficient glycoprotein syndrome type Ip733085004
- Congenital disorder of glycosylation type 1p733085004
- Congenital disorder of glycosylation type Ip733085004
- Congenital disorder of glycosylation type 1w733111000
- Congenital disorder of glycosylation type Iw733111000
- STT3A-CDG (congenital disorder of glycosylation)733111000
- Carbohydrate deficient glycoprotein syndrome type Ix733112007
- Congenital disorder of glycosylation type 1x733112007
- Congenital disorder of glycosylation type Ix733112007
- STT3B-CDG (congenital disorder of glycosylation)733112007
- Carbohydrate deficient glycoprotein syndrome type Iy733115009
- Congenital disorder of glycosylation type 1y733115009
- Congenital disorder of glycosylation type Iy733115009
- SSR4-CDG - signal sequence receptor subunit 4 congenital disorder of glycosylation733115009
- Signal sequence receptor subunit 4 congenital disorder of glycosylation733115009
- ALG13-CDG (congenital disorder of glycosylation)733451007
- Congenital disorder of glycosylation type 1s733451007
- Congenital disorder of glycosylation type Is733451007
- Congenital disorder of glycosylation type 1q733601006
- Congenital disorder of glycosylation type Iq733601006
- SRD5A3-CDG - steroid 5 alpha-reductase 3 congenital disorder of glycosylation733601006
- CDG2M - congenital disorder of glycosylation type 2m771516000
- Congenital disorder of glycosylation type 2m771516000
- Congenital disorder of glycosylation type IIm771516000
- SLC35A2-CDG - solute carrier family 35 member A2 congenital disorder of glycosylation771516000
- Solute carrier family 35 member A2 congenital disorder of glycosylation771516000
- XYLT1-CDG773418007
- XYLT1-CDG - xylosyltransferase 1 congenital disorder of glycosylation773418007
- Xylosyltransferase 1 congenital disorder of glycosylation773418007
- Congenital disorder of glycosylation type 1t783717008
- Congenital disorder of glycosylation type It783717008
- PGM1-CDG - Phosphoglucomutase 1-related congenital disorder of glycosylation783717008
- PGM1-related congenital disorder of glycosylation783717008
- Phosphoglucomutase 1-related congenital disorder of glycosylation783717008
- Phosphoglucomutase-1 deficiency783717008
- Congenital disorder of glycosylation type 1i897592003
- Mannosyltransferase 2 deficiency897592003
- Carbohydrate deficient glycoprotein syndrome type IIn1187171005
- Congenital disorder of glycosylation type 2n1187171005
- Congenital disorder of glycosylation type IIn1187171005
- SLC39A8 congenital disorder of glycosylation1187171005
- SLC39A8-CDG - solute carrier family 39 member 8 congenital disorder of glycosylation1187171005
- Solute carrier family 39 member 8 congenital disorder of glycosylation1187171005
- CCDC115 congenital disorder of glycosylation1187174002
- CCDC115-CDG - coiled-coil domain containing 115 congenital disorder of glycosylation1187174002
- Carbohydrate deficient glycoprotein syndrome type IIo1187174002
- Coiled-coil domain containing 115 congenital disorder of glycosylation1187174002
- Congenital disorder of glycosylation type 2o1187174002
- Congenital disorder of glycosylation type IIo1187174002
- Glycogen storage disease due to phosphoglycerate kinase 1 deficiency1187462006
- Glycogenosis due to phosphoglycerate kinase 1 deficiency1187462006
- Combined immunodeficiency due to PGM3 (phosphoglucomutase 3) deficiency1187623009
- PGM3-CDG - phosphoglucomutase 3-related congenital disorder of glycosylation1187623009
- PGM3-related congenital disorder of glycosylation1187623009
- Phosphoglucomutase 3-related congenital disorder of glycosylation1187623009
- CDG1CC - congenital disorder of glycosylation type 1cc1365658002
- Congenital disorder of glycosylation type 1cc1365658002
- Congenital disorder of glycosylation type Icc1365658002
- MAGT1-CDG (congenital disorder of glycosylation)1365658002
- MAGT1-congenital disorder of glycosylation1365658002
- Magnesium transporter 1-congenital disorder of glycosylation1365658002
- Congenital myasthenic syndrome with ALG14-CDG (congenital disorder of glycosylation)1366554003
- Congenital myasthenic syndrome with glycosylation defect due to ALG14 UDP-N-acetylglucosaminyltransferase subunit gene mutation1366554003
- Congenital myasthenic syndrome with glycosylation defect due to ALG14 gene mutation1366554003
UMLS
- Essential benign pentosuriaC0268162
- Essential pentosuriaC0268162
- Essential pentosuria (disorder)C0268162
- L-XYLULOSE REDUCTASE DEFICIENCYC0268162
- L-XYLULOSURIAC0268162
- L-Xylulose reductase deficiencyC0268162
- L-XylulosuriaC0268162
- L-xylulose reductase deficiencyC0268162
- L-xylulosuriaC0268162
- PENTOSURIAC0268162
- PNTSUC0268162
- PentosuriaC0268162
- XYLITOL DEHYDROGENASE DEFICIENCYC0268162
- Xylitol dehydrogenase deficiencyC0268162
- deficiency dehydrogenase xylitolC0268162
- pentosuriaC0268162
- Other specified disorders of carbohydrate metabolismC0348487
Frequently Asked Questions
What is the ICD-10 code for other specified disorders of carbohydrate metabolism?
The ICD-10-CM code for other specified disorders of carbohydrate metabolism is E74.89. The full clinical description is "Other specified disorders of carbohydrate metabolism". E74.89 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E74.89 mean?
ICD-10-CM code E74.89 represents "Other specified disorders of carbohydrate metabolism". It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E74.89 a billable code?
Yes, E74.89 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E74.89 in?
E74.89 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E74.89?
E74.89 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 7 more.
What SNOMED CT codes does E74.89 map to?
E74.89 maps to 93 SNOMED CT concepts: 720941007, 733085004, 711155008, 733451007, 720976009, and 88 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E74.89?
E74.89 is linked to 2 UMLS Concept Unique Identifiers: C0268162, C0348487. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.