E74.01
Billablevon Gierke disease
von Gierke disease
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Type I glycogen storage disease
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
- diabetes mellitus (E08-E13)
- hypoglycemia NOS (E16.2)
- increased secretion of glucagon (E16.3)
- mucopolysaccharidosis (E76.0-E76.3)
Excludes 2
Conditions not included here, but the patient may have both
- Ehlers-Danlos syndromes (Q79.6-)
Also Known As / Clinical Terms
SNOMED CT
- Glycogen storage disease, hepatic form6075009
- GSD I7265005
- Glycogen storage disease, type 17265005
- Glycogen storage disease, type I7265005
- Hepatorenal glycogen storage disease7265005
- Liver glycogen disease7265005
- von Gierke disease7265005
- von Gierke's disease7265005
- Glucose 6-phosphate transport defect30102006
- Glucose-6-phosphate transport defect30102006
- Glycogen storage disease type Ib30102006
- Deficiency of glucose-6-phosphatase124437004
- Glucose transport defect237966006
- Glycogen storage disease type Id237966006
- Glycogen storage disease type Ia444707001
UMLS
- DEFIC GLUCOSEPHOSPHATASEC0017920
- Deficiencies, Glucose-6-PhosphataseC0017920
- Deficiencies, GlucosephosphataseC0017920
- Deficiency of glucose-6-phosphataseC0017920
- Deficiency of glucose-6-phosphatase (disorder)C0017920
- Deficiency, Glucose-6-PhosphataseC0017920
- Deficiency, GlucosephosphataseC0017920
- Disease, GierkeC0017920
- Disease, Gierke'sC0017920
- Disease, von GierkeC0017920
- Disease, von Gierke'sC0017920
- GIERKE DISC0017920
- GIERKES DISC0017920
- GLUCOSE 6 PHOSPHATASE DEFICC0017920
- GLUCOSEPHOSPHATASE DEFICC0017920
- GLYCOGEN STORAGE DIS IC0017920
- GSD IC0017920
- GSD type IC0017920
- Gierke DiseaseC0017920
- Gierke's DiseaseC0017920
- Gierkes DiseaseC0017920
- Glucose 6 Phosphatase DeficiencyC0017920
- Glucose-6-Phosphatase DeficienciesC0017920
- Glucose-6-Phosphatase DeficiencyC0017920
- Glucose-6-phosphatase deficiencyC0017920
- Glucosephosphatase DeficienciesC0017920
- Glucosephosphatase DeficiencyC0017920
- Glycogen Storage Disease 1 (GSD I)C0017920
- Glycogen Storage Disease Type IC0017920
- Glycogen storage disease type IC0017920
- Glycogen storage disease, type 1C0017920
- Glycogen storage disease, type IC0017920
- Glycogen storage disease, type I (disorder)C0017920
- Glycogenosis 1C0017920
- HEPATORENAL GLYCOGEN STORAGE DISC0017920
- Hepatorenal Glycogen Storage DiseaseC0017920
- Hepatorenal form of glycogen storage diseaseC0017920
- Hepatorenal glycogen storage diseaseC0017920
- Hepatorenal glycogenosisC0017920
- Liver glycogen diseaseC0017920
- Type I glycogen storage diseaseC0017920
- Von Gierke diseaseC0017920
- Von Gierke's diseaseC0017920
- disease glycogen i storage typeC0017920
- diseases gierke's vonC0017920
- gierke's diseaseC0017920
- glucose 6 phosphatase deficiencyC0017920
- glucose-6-phosphatase deficiencyC0017920
- glycogen storage disease iC0017920
- glycogen storage disease type IC0017920
- glycogen storage disease type iC0017920
- glycogenosis type IC0017920
- glycogenosis type iC0017920
- hepatorenal glycogen storage diseaseC0017920
- hepatorenal glycogenosisC0017920
- i glycogen storage diseaseC0017920
- type i glycogen storage diseaseC0017920
- von Gierke DiseaseC0017920
- von Gierke diseaseC0017920
- von Gierke's DiseaseC0017920
- von Gierke's diseaseC0017920
- von Gierkes DiseaseC0017920
- von gierke diseaseC0017920
- von gierke's diseaseC0017920
- von gierkes diseaseC0017920
Frequently Asked Questions
What is the ICD-10 code for von gierke disease?
The ICD-10-CM code for von gierke disease is E74.01. The full clinical description is "von Gierke disease". E74.01 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E74.01 mean?
ICD-10-CM code E74.01 represents "von Gierke disease". It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E74.01 a billable code?
Yes, E74.01 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E74.01 in?
E74.01 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E74.01?
E74.01 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 7 more.
What SNOMED CT codes does E74.01 map to?
E74.01 maps to 6 SNOMED CT concepts: 124437004, 7265005, 30102006, 237966006, 444707001, and 1 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E74.01?
E74.01 is linked to 1 UMLS Concept Unique Identifier: C0017920. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.