E71.311
BillableMedium chain acyl CoA dehydrogenase deficiency
Medium chain acyl CoA dehydrogenase deficiency
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- MCAD deficiency
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
- peroxisomal disorders (E71.5)
- Refsum's disease (G60.1)
- Schilder's disease (G37.0)
Also Known As / Clinical Terms
SNOMED CT
- Acyl-CoA dehydrogenase deficiency82319005
- Acyl-coenzyme A dehydrogenase deficiency82319005
- Deficiency of acyl-CoA dehydrogenase82319005
- ACADM (acyl-CoA dehydrogenase medium chain) deficiency128596003
- ACADM-gene related medium-chain acyl-coenzyme A dehydrogenase deficiency128596003
- MCAD - Medium chain acyl-CoA dehydrogenase deficiency128596003
- MCAD deficiency128596003
- Medium chain acyl-CoA dehydrogenase deficiency128596003
- Medium chain acyl-coenzyme A dehydrogenase deficiency128596003
- Medium-chain acyl-coenzyme A dehydrogenase deficiency128596003
UMLS
- ACADM (acyl-CoA dehydrogenase medium chain) deficiencyC0220710
- ACADM DEFICIENCYC0220710
- ACADM DeficiencyC0220710
- ACADM deficiencyC0220710
- ACADM-gene related medium-chain acyl-coenzyme A dehydrogenase deficiencyC0220710
- ACADMDC0220710
- ACYL-CoA DEHYDROGENASE, MEDIUM-CHAIN, DEFICIENCY OFC0220710
- Acyl-CoA Dehydrogenase, Medium-Chain DeficiencyC0220710
- Acyl-CoA dehydrogenase, medium chain, deficiency ofC0220710
- Acyl-Coa Dehydrogenase, Medium-Chain, Deficiency ofC0220710
- CARNITINE DEFICIENCY SECONDARY TO MEDIUM-CHAIN ACYL-CoA DEHYDROGENASE DEFICIENCYC0220710
- Carnitine Deficiency Secondary To Medium-Chain Acyl-Coa Dehydrogenase DeficiencyC0220710
- Deficiency of medium-chain acyl-CoA dehydrogenaseC0220710
- MCADC0220710
- MCAD - Medium chain acyl-CoA dehydrogenase deficiencyC0220710
- MCAD DEFICIENCYC0220710
- MCAD DeficiencyC0220710
- MCAD deficiencyC0220710
- MCADDC0220710
- MCADH DEFICIENCYC0220710
- MCADH DeficiencyC0220710
- MCADH deficiencyC0220710
- Medium Chain Acyl-Coa Dehydrogenase DeficiencyC0220710
- Medium chain acyl CoA dehydrogenase deficiencyC0220710
- Medium chain acyl-CoA dehydrogenase deficiencyC0220710
- Medium chain acyl-coenzyme A dehydrogenase deficiencyC0220710
- Medium-Chain Acyl-CoA Dehydrogenase DeficiencyC0220710
- Medium-Chain Acyl-Coenzyme A Dehydrogenase DeficiencyC0220710
- Medium-chain Acyl-CoA dehydrogenase deficiencyC0220710
- Medium-chain acyl-CoA dehydrogenase deficiencyC0220710
- Medium-chain acyl-coenzyme A dehydrogenase deficiencyC0220710
- Medium-chain acyl-coenzyme A dehydrogenase deficiency (disorder)C0220710
- mcad deficiencyC0220710
Frequently Asked Questions
What is the ICD-10 code for medium chain acyl coa dehydrogenase deficiency?
The ICD-10-CM code for medium chain acyl coa dehydrogenase deficiency is E71.311. The full clinical description is "Medium chain acyl CoA dehydrogenase deficiency". E71.311 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E71.311 mean?
ICD-10-CM code E71.311 represents "Medium chain acyl CoA dehydrogenase deficiency". It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E71.311 a billable code?
Yes, E71.311 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E71.311 in?
E71.311 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E71.311?
E71.311 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 6 more.
What SNOMED CT codes does E71.311 map to?
E71.311 maps to 2 SNOMED CT concepts: 128596003, 82319005. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E71.311?
E71.311 is linked to 1 UMLS Concept Unique Identifier: C0220710. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.