E71.310
BillableLong chain/very long chain acyl CoA dehydrogenase deficiency
Long chain/very long chain acyl CoA dehydrogenase deficiency
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- LCAD deficiency
- VLCAD deficiency
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
- peroxisomal disorders (E71.5)
- Refsum's disease (G60.1)
- Schilder's disease (G37.0)
Also Known As / Clinical Terms
SNOMED CT
- Acyl-CoA dehydrogenase deficiency82319005
- Acyl-coenzyme A dehydrogenase deficiency82319005
- Deficiency of acyl-CoA dehydrogenase82319005
- LCAD - Long chain acyl-CoA dehydrogenase deficiency237996001
- Long chain acyl-CoA dehydrogenase deficiency237996001
- Long chain acyl-coenzyme A dehydrogenase deficiency237996001
- VLCAD - Very long chain acyl-CoA dehydrogenase deficiency237997005
- Very long chain acyl-CoA dehydrogenase deficiency237997005
- Very long chain acyl-coenzyme A dehydrogenase deficiency237997005
- Combined deficiency of long chain 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase238000002
- Combined deficiency of long chain 3-hydroxyacyl-coenzyme A dehydrogenase and enoyl-coenzyme A hydratase238000002
UMLS
- ACADVLC3887523
- ACADVLDC3887523
- ACYL-CoA DEHYDROGENASE, VERY LONG-CHAIN, DEFICIENCY OFC3887523
- AcadvlC3887523
- Acyl-CoA Dehydrogenase, Very Long-Chain DeficiencyC3887523
- Acyl-CoA Dehydrogenase, Very Long-Chain, Deficiency ofC3887523
- Acyl-CoA dehydrogenase very long chain deficiencyC3887523
- Acyl-Coa Dehydrogenase Very Long Chain DeficiencyC3887523
- VLCADC3887523
- VLCAD - Very long chain acyl-CoA dehydrogenase deficiencyC3887523
- VLCAD DEFICIENCYC3887523
- VLCAD deficiencyC3887523
- VLCAD-CC3887523
- VLCAD-HC3887523
- Very Long-Chain Acyl Coenzyme A Dehydrogenase DeficiencyC3887523
- Very Long-Chain Acyl-CoA Dehydrogenase DeficiencyC3887523
- Very Long-Chain Acyl-Coenzyme A Dehydrogenase DeficiencyC3887523
- Very long chain acyl-CoA dehydrogenase deficiencyC3887523
- Very long chain acyl-coenzyme A dehydrogenase deficiencyC3887523
- Very long chain acyl-coenzyme A dehydrogenase deficiency (disorder)C3887523
- Very long-chain acyl coenzyme A dehydrogenase deficiencyC3887523
- Very long-chain acyl-CoA dehydrogenase deficiencyC3887523
- Very long-chain acyl-coenzyme A dehydrogenase deficiencyC3887523
- Vlcad-CC3887523
- Vlcad-HC3887523
- Acyl-CoA Dehydrogenase, Long-Chain DeficiencyC0220711
- Acyl-Coa Dehydrogenase, Long-Chain, Deficiency ofC0220711
- LCADC0220711
- LCAD - Long chain acyl-CoA dehydrogenase deficiencyC0220711
- LCAD deficiencyC0220711
- Long chain acyl-CoA dehydrogenase deficiencyC0220711
- Long chain acyl-coenzyme A dehydrogenase deficiencyC0220711
- Long chain acyl-coenzyme A dehydrogenase deficiency (disorder)C0220711
- Long-Chain Acyl-CoA Dehydrogenase DeficiencyC0220711
- Long-Chain Acyl-Coenzyme A Dehydrogenase DeficiencyC0220711
- Long-chain acyl-CoA dehydrogenase deficiencyC0220711
- Long-chain acyl-coenzyme A dehydrogenase deficiencyC0220711
- Long chain/very long chain acyl CoA dehydrogenase deficiencyC2874239
Frequently Asked Questions
What is the ICD-10 code for long chain/very long chain acyl coa dehydrogenase deficiency?
The ICD-10-CM code for long chain/very long chain acyl coa dehydrogenase deficiency is E71.310. The full clinical description is "Long chain/very long chain acyl CoA dehydrogenase deficiency". E71.310 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E71.310 mean?
ICD-10-CM code E71.310 represents "Long chain/very long chain acyl CoA dehydrogenase deficiency". It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E71.310 a billable code?
Yes, E71.310 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E71.310 in?
E71.310 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E71.310?
E71.310 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 6 more.
What SNOMED CT codes does E71.310 map to?
E71.310 maps to 4 SNOMED CT concepts: 82319005, 238000002, 237996001, 237997005. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E71.310?
E71.310 is linked to 3 UMLS Concept Unique Identifiers: C3887523, C0220711, C2874239. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.