E71.121
BillablePropionic acidemia
Propionic acidemia
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- Ehlers-Danlos syndromes (Q79.6-)
Also Known As / Clinical Terms
SNOMED CT
- Hyperglycinaemia with ketosis and leucopenia69080001
- Hyperglycinemia with ketosis and leukopenia69080001
- Ketotic glycinaemia69080001
- Ketotic glycinemia69080001
- Ketotic hyperglycinaemia69080001
- Ketotic hyperglycinemia69080001
- PCC - Propionyl-CoA carboxylase deficiency69080001
- Propionic acidaemia69080001
- Propionic acidemia69080001
- Propionic aciduria69080001
- Propionyl-CoA carboxylase deficiency69080001
- Deficiency of propionyl-CoA carboxylase124718009
- Deficiency of propionyl-coenzyme A carboxylase124718009
- PCCA-gene related propionyl-coenzyme A carboxylase deficiency pccA complementation group303094000
- Propionyl-CoA carboxylase deficiency pccA complementation group303094000
- Propionyl-coenzyme A carboxylase deficiency pccA complementation group303094000
- PCCB-gene related propionyl-coenzyme A carboxylase deficiency pccBC complementation group303095004
- Propionyl-CoA carboxylase deficiency pccBC complementation group303095004
- Propionyl-coenzyme A carboxylase deficiency pccBC complementation group303095004
- Propionic acidaemia, type I399087009
- Propionic acidemia, type I399087009
- Propionic acidaemia, type II399149003
- Propionic acidemia, type II399149003
UMLS
- Acidemia PropionicC0268579
- Acidemia PropionicsC0268579
- Acidemia, PropionicC0268579
- Carboxylase Deficiencies, Propionyl-CoAC0268579
- Carboxylase Deficiency, Propionyl-CoAC0268579
- Deficiencies, Propionyl-CoA CarboxylaseC0268579
- Deficiency, PCCC0268579
- Deficiency, Propionyl-CoA CarboxylaseC0268579
- GLYCINEMIA, KETOTICC0268579
- Glycinemia, KetoticC0268579
- Glycinemias, KetoticC0268579
- HYPERGLYCINEMIA WITH KETOACIDOSIS AND LEUKOPENIAC0268579
- Hyperglycinaemia with ketosis and leucopeniaC0268579
- Hyperglycinemia With Ketoacidosis And LeukopeniaC0268579
- Hyperglycinemia with ketoacidosis and leukopeniaC0268579
- Hyperglycinemia with ketosis and leukopeniaC0268579
- Hyperglycinemia, KetoticC0268579
- Hyperglycinemias, KetoticC0268579
- KETOTIC HYPERGLYCINEMIAC0268579
- Ketotic GlycinemiaC0268579
- Ketotic GlycinemiasC0268579
- Ketotic HyperglycinemiaC0268579
- Ketotic HyperglycinemiasC0268579
- Ketotic glycinaemiaC0268579
- Ketotic glycinemiaC0268579
- Ketotic hyperglycinaemiaC0268579
- Ketotic hyperglycinemiaC0268579
- PCC - Propionyl-CoA carboxylase deficiencyC0268579
- PCC DeficienciesC0268579
- PCC DeficiencyC0268579
- PCC deficiencyC0268579
- PROPC0268579
- PROPIONIC ACIDEMIAC0268579
- Propionic AcidemiaC0268579
- Propionic AcidemiasC0268579
- Propionic acidaemiaC0268579
- Propionic acidemiaC0268579
- Propionic acidemia (disorder)C0268579
- Propionic aciduriaC0268579
- Propionic, AcidemiaC0268579
- PropionicacidemiaC0268579
- PropionicacidemiasC0268579
- Propionyl CoA Carboxylase DeficiencyC0268579
- Propionyl-CoA Carboxylase DeficienciesC0268579
- Propionyl-CoA Carboxylase DeficiencyC0268579
- Propionyl-CoA carboxylase deficiencyC0268579
- ketotic glycinemiaC0268579
- ketotic hyperglycinaemiaC0268579
- ketotic hyperglycinemiaC0268579
- propionic acidaemiaC0268579
- propionic acidemiaC0268579
- propionyl coA carboxylase deficiencyC0268579
Frequently Asked Questions
What is the ICD-10 code for propionic acidemia?
The ICD-10-CM code for propionic acidemia is E71.121. The full clinical description is "Propionic acidemia". E71.121 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E71.121 mean?
ICD-10-CM code E71.121 represents "Propionic acidemia". It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E71.121 a billable code?
Yes, E71.121 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E71.121 in?
E71.121 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E71.121?
E71.121 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What SNOMED CT codes does E71.121 map to?
E71.121 maps to 6 SNOMED CT concepts: 124718009, 69080001, 303094000, 303095004, 399087009, and 1 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E71.121?
E71.121 is linked to 1 UMLS Concept Unique Identifier: C0268579. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.