E71.111
Billable3-methylglutaconic aciduria
3-methylglutaconic aciduria
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- Ehlers-Danlos syndromes (Q79.6-)
Also Known As / Clinical Terms
SNOMED CT
- 3-Methylglutaconic aciduria237950009
- 3-Methylglutaconic aciduria type 1237951008
- 3-Methylglutaconyl-CoA hydratase deficiency with 3-methylglutaconic acid237951008
- AUH-gene related 3-methylglutaconic aciduria type 1237951008
- 3-Methylglutaconic aciduria with normal 3-methylglutaconyl-CoA hydratase activity237952001
- 3-Methylglutaconic aciduria with normal 3-methylglutaconyl-coenzyme A hydratase activity237952001
- 3-Methylglutaconic aciduria type 3297232009
- Costeff syndrome297232009
- 3-Methylglutaconic aciduria type 4297233004
- Unclassified 3-methylglutaconic aciduria297235006
- 3-methylglutaconic aciduria type IV with sensorineural deafness, encephalopathy and Leigh-like syndrome711409002
- 3-methylglutaconic aciduria with deafness, encephalopathy, Leigh-like syndrome711409002
- 3-methylglutaconic aciduria with hearing loss, encephalopathy, Leigh-like syndrome711409002
- MEGDEL syndrome711409002
- 3-methylglutaconic aciduria type 5711412004
- Dilated cardiomyopathy with ataxia syndrome711412004
- 3-methylglutaconic aciduria type 7764860006
- 3-methylglutaconic aciduria type VII764860006
- 3-methylglutaconic aciduria, cataract, neurologic involvement, neutropenia syndrome764860006
- CLBP (ClpB homolog, mitochondrial AAA ATPase chaperonin) deficiency764860006
- MGA7 - 3-methylglutaconic aciduria type 7764860006
- 3-methylglutaconic aciduria type 81222671009
- 3-methylglutaconic aciduria type 91222672002
- 3-methylglutaconic aciduria, epilepsy, spasticity, severe intellectual disability syndrome1222672002
Frequently Asked Questions
What is the ICD-10 code for 3-methylglutaconic aciduria?
The ICD-10-CM code for 3-methylglutaconic aciduria is E71.111. The full clinical description is "3-methylglutaconic aciduria". E71.111 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E71.111 mean?
ICD-10-CM code E71.111 represents "3-methylglutaconic aciduria". It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E71.111 a billable code?
Yes, E71.111 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E71.111 in?
E71.111 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E71.111?
E71.111 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What SNOMED CT codes does E71.111 map to?
E71.111 maps to 11 SNOMED CT concepts: 237950009, 237951008, 297232009, 297233004, 237952001, and 6 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E71.111?
E71.111 is linked to 1 UMLS Concept Unique Identifier: C3696376. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.