D84.89
BillableOther immunodeficiencies
Other immunodeficiencies
Coding Notes
Includes
Conditions included under this code
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Also Known As / Clinical Terms
SNOMED CT
- Chediak-Higashi-like syndrome37548006
- Griscelli syndrome37548006
- Griscelli syndrome with immunodeficiency37548006
- Hypopigmentation-immunodeficiency disease37548006
- Partial albinism with immunodeficiency37548006
- T lymphocyte disorder44306006
- Alymphocytosis48813009
- Lymphocytopenia48813009
- Lymphopenia48813009
- Immune defect71922006
- Immunologic defect71922006
- Cold urticaria74774004
- Cold-induced angio-oedema-urticaria74774004
- Cold-induced angioedema-urticaria74774004
- Urticaria caused by cold74774004
- Autoimmune leucopenia123777002
- Autoimmune leukopenia123777002
- Immunoglobulin-associated molecule deficiency234553005
- Secretory component deficiency234554004
- Secretory piece deficiency234554004
- Defective immunoglobulin glycosylation234555003
- Deficiency of immunoglobulin secretion234555003
- Defective phagocytic cell opsonisation234578009
- Defective phagocytic cell opsonization234578009
- Mannan-binding protein deficiency234579001
- Yeast opsonisation defect234579001
- Yeast opsonization defect234579001
- Immunodeficiency with major anomalies234631003
- Immunodeficiency associated with multiple organ system abnormalities234641000
- Age-related immunodeficiency234642007
- Transient immunodeficiency of infancy234643002
- FCAS - familial cold autoinflammatory syndrome238687000
- FCU - familial cold urticaria238687000
- Familial cold autoinflammatory syndrome238687000
- Familial cold urticaria238687000
- Immuno-osseous dysplasia254067002
- Congenital immunodeficiency involving the haematopoietic system363040003
- Congenital immunodeficiency involving the hematopoietic system363040003
- T-lymphocyte deficiency398055000
- Predominantly T-cell defect398271008
- Cell-mediated immune deficiency398293003
- Cellular immune defect398293003
- Deficiency of cell mediated immunity398293003
- Deficiency of cell-mediated immunity398293003
- T-lymphocyte immunodeficiency402792003
- Heritable disorder of neutrophil function402794002
- CD4 T lymphocyte deficiency406565005
- Cryopyrin associated periodic syndrome430079001
- Interleukin-12 deficiency449853003
- MBL deficiency703538003
- MBL2 deficiency703538003
- MBP deficiency703538003
- Mannose-binding lectin deficiency703538003
- Mannose-binding lectin protein deficiency703538003
- Mannose-binding protein deficiency703538003
- Phagocytic immunodeficiency707152007
- APDS - activated PI3K-delta syndrome711480000
- Activated PI3K-delta syndrome711480000
- Activated phosphoinositide 3-kinase delta syndrome711480000
- Autosomal dominant immunodeficiency due to activated p110-delta syndrome711480000
- Immunodeficiency 14711480000
- PASLI - p110-delta-activating mutation causing senescent T cells, lymphadenopathy, and immunodeficiency711480000
- p110-delta-activating mutation causing senescent T cells, lymphadenopathy and immunodeficiency711480000
- Pyogenic bacterial infection due to MyD88 deficiency718232007
- Pyogenic bacterial infection due to deficiency of myeloid differentiation primary response 88718232007
- Absent thumb with short stature and immunodeficiency syndrome719685004
- Mendelian susceptibility to mycobacterial disease due to complete IFNgammaR2 deficiency721876004
- Mendelian susceptibility to mycobacterial disease due to complete interferon gamma receptor 2 deficiency721876004
- FADD (FAS-associated protein with death domain) related immunodeficiency723334006
- FADD-related immunodeficiency723334006
- Immunodeficiency due to mutation of FAS-associated protein with death domain gene723334006
- Mendelian susceptibility to mycobacterial disease due to complete ISG15 (interferon stimulated gene 15) deficiency723384004
- Mendelian susceptibility to mycobacterial disease due to complete ISG15 deficiency723384004
- Mendelian susceptibility to mycobacterial disease due to complete interferon stimulated gene 15 deficiency723384004
- Mendelian susceptibility to mycobacterial disease due to partial IRF8 (interferon regulatory factor 8) deficiency723385003
- Mendelian susceptibility to mycobacterial disease due to partial IRF8 deficiency723385003
- Mendelian susceptibility to mycobacterial disease due to partial interferon regulatory factor 8 deficiency723385003
- Mendelian susceptibility to mycobacterial disease due to partial STAT1 (signal transducer and activator of transcription 1) deficiency723386002
- Mendelian susceptibility to mycobacterial disease due to partial STAT1 deficiency723386002
- Mendelian susceptibility to mycobacterial disease due to partial signal transducer and activator of transcription 1 deficiency723386002
- Neutrophil immunodeficiency syndrome723443003
- Schimke immuno-osseous dysplasia723995003
- Schimke immunoosseous dysplasia723995003
- Schimke syndrome723995003
- Autosomal dominant mendelian susceptibility to mycobacterial disease due to partial IFNgammaR1 deficiency725150008
- Autosomal dominant mendelian susceptibility to mycobacterial disease due to partial interferon gamma receptor 1 deficiency725150008
- Autosomal dominant mendelian susceptibility to mycobacterial disease due to partial IFNgammaR2 deficiency725151007
- Autosomal dominant mendelian susceptibility to mycobacterial disease due to partial interferon gamma receptor 2 deficiency725151007
- Autosomal recessive mendelian susceptibility to mycobacterial disease due to partial IFNgammaR1 deficiency725431001
- Autosomal recessive mendelian susceptibility to mycobacterial disease due to partial interferon gamma receptor 1 deficiency725431001
- Autosomal recessive mendelian susceptibility to mycobacterial disease due to partial IFNgammaR2 deficiency725432008
- Autosomal recessive mendelian susceptibility to mycobacterial disease due to partial interferon gamma receptor 2 deficiency725432008
- Adult-onset immunodeficiency735536003
- Immunodeficiency due to natural-killer cell deficiency737307003
- Natural-killer cell deficiency737307003
- Lichtenstein syndrome763668009
- CMMR-D (constitutional mismatch repair deficiency) syndrome764946008
- Constitutional mismatch repair deficiency syndrome764946008
- Immunodeficiency due to ficolin 3 deficiency766705006
- Immunodeficiency due to ficolin-3 deficiency766705006
- IFIH1 (interferon induced with helicase C domain 1) deficiency768560008
- MDA5 (melanoma differentiation-associated gene 5) deficiency768560008
- MDA5 deficiency768560008
- Melanoma differentiation-associated gene 5 deficiency768560008
- T-cell immunodeficiency due to RHOH (ras homolog family member H) deficiency770785002
- T-cell immunodeficiency due to RHOH deficiency770785002
- T-cell immunodeficiency due to ras homolog family member H deficiency770785002
- T-cell immunodeficiency with epidermodysplasia verruciformis770785002
- FACU - familial atypical cold urticaria773646003
- Familial cold urticaria with common variable immunodeficiency773646003
- PLCG2 (phospholipase C gamma 2) associated antibody deficiency and immune dysregulation773646003
- PLCG2-associated antibody deficiency and immune dysregulation773646003
- Phospholipase C gamma 2 associated antibody deficiency and immune dysregulation773646003
- Immunodeficiency due to CD25 deficiency778028008
- Interleukin-2 receptor alpha chain deficiency778028008
- Adult-onset immunodeficiency with acquired anti-interferon-gamma autoantibodies784393004
- Adult-onset immunodeficiency with anti-interferon-gamma autoantibodies784393004
- Aplasia of thumb1144446007
- Lymphocyte count below reference range1156294003
- Autosomal recessive MSMD (mendelian susceptibility to mycobacterial disease) due to complete RORgamma receptor mutation1172892009
- Autosomal recessive mendelian susceptibility to mycobacterial disease due to complete RAR related orphan receptor C receptor mutation1172892009
- Autosomal recessive mendelian susceptibility to mycobacterial disease due to complete RORgamma receptor mutation1172892009
- Autosomal recessive primary immunodeficiency due to RORC mutation1172892009
- MSMD - mendelian susceptibility to mycobacterial disease1172895006
- Mendelian susceptibility to mycobacterial disease1172895006
- Mendelian susceptibility to mycobacterial infection1172895006
- IL21-related infantile inflammatory bowel disease1173999006
- Interleukin 21 related infantile inflammatory bowel disease1173999006
- Congenital progressive bone marrow failure, B-cell immunodeficiency, skeletal dysplasia syndrome1177173001
- MYSM1 (Myb like, SWIRM and MPN domains 1) deficiency1177173001
- MYSM1 deficiency1177173001
- EXTL3 (exostosin like glycosyltransferase 3) related neuro-immuno-skeletal dysplasia syndrome1177175008
- EXTL3-related neuro-immuno-skeletal dysplasia syndrome1177175008
- Neuro-immuno-skeletal dysplasia syndrome due to EXTL3 (exostosin like glycosyltransferase 3) deficiency1177175008
- Neuro-immuno-skeletal dysplasia syndrome due to EXTL3 deficiency1177175008
- Skeletal dysplasia, T-cell immunodeficiency, developmental delay syndrome1177175008
- Immune dysregulation, inflammatory bowel disease, arthritis, recurrent infection, lymphopenia syndrome1186654001
- Invasive candidiasis, deep dermatophytosis syndrome1186719000
- Predisposition to invasive fungal disease due to CARD9 deficiency1186719000
- Predisposition to invasive fungal disease due to caspase recruitment domain family member 9 deficiency1186719000
- CAIN (CEBPE-associated autoinflammation, immunodeficiency, neutrophil dysfunction) syndrome1186720006
- CCAAT enhancer binding protein epsilon-associated autoinflammation, immunodeficiency, neutrophil dysfunction syndrome1186720006
- CEBPE-associated autoinflammation, immunodeficiency, neutrophil dysfunction syndrome1186720006
- Disseminated warts, impaired cell-mediated immunity, primary lymphedema, anogenital dysplasia syndrome1186725001
- Disseminated warts, impaired cell-mediated immunity, primary lymphoedema, anogenital dysplasia syndrome1186725001
- WILD (warts, immunodeficiency, lymphedema, anogenital dysplasia) syndrome1186725001
- WILD (warts, immunodeficiency, lymphoedema, anogenital dysplasia) syndrome1186725001
- WILD syndrome1186725001
- Warts, immunodeficiency, lymphedema, anogenital dysplasia syndrome1186725001
- Warts, immunodeficiency, lymphoedema, anogenital dysplasia syndrome1186725001
- Autosomal recessive primary immunodeficiency with defective spontaneous NK (natural killer) cell cytotoxicity1197366007
- Autosomal recessive primary immunodeficiency with defective spontaneous natural killer cell cytotoxicity1197366007
- CD16 deficiency1197366007
- Autosomal recessive hyper-IgE (immunoglobulin E) syndrome due to TYK2 deficiency1197415001
- Susceptibility to infection due to TYK2 deficiency1197415001
- Susceptibility to infection due to tyrosine kinase 2 deficiency1197415001
- Griscelli syndrome type 11254946006
- Hypopigmentation-immunodeficiency disease type 11254946006
- Griscelli syndrome type 31254947002
- Hypopigmentation-immunodeficiency disease type 31254947002
- Myelodysplastic neoplasm with low blasts1260268001
- Myelodysplastic syndrome with low blasts1260268001
- Refractory neutropenia1260268001
- Predisposition to severe viral infection due to IRF7 deficiency1269234000
- Predisposition to severe viral infection due to interferon regulatory factor 7 deficiency1269234000
- Autosomal recessive mendelian susceptibility to mycobacterial disease due to partial JAK1 deficiency1279842008
- Autosomal recessive mendelian susceptibility to mycobacterial disease due to partial janus kinase 1 deficiency1279842008
- Early-onset autoimmunity, autoinflammation, immunodeficiency syndrome due to SOCS1 haploinsufficiency1351844007
- Early-onset autoimmunity, autoinflammation, immunodeficiency syndrome due to suppressor of cytokine signaling 1 haploinsufficiency1351844007
- SOCS1-related autoinflammatory syndrome1351844007
- Familial hyperinflammatory lymphoproliferative immunodeficiency1351853000
- HEM1 deficiency syndrome1351853000
- NCKAP1L-associated hyperinflammatory disorder1351853000
- Constitutional mismatch repair deficiency syndrome due to PMS1 homolog 2, mismatch repair system component mutation1356823008
- Constitutional mismatch repair deficiency syndrome due to PMS2 deficiency1356823008
- Constitutional mismatch repair deficiency syndrome due to PMS2 mutation1356823008
Frequently Asked Questions
What is the ICD-10 code for other immunodeficiencies?
The ICD-10-CM code for other immunodeficiencies is D84.89. The full clinical description is "Other immunodeficiencies". D84.89 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D84.89 mean?
ICD-10-CM code D84.89 represents "Other immunodeficiencies". It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.
Is D84.89 a billable code?
Yes, D84.89 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D84.89 in?
D84.89 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D84.89?
D84.89 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20).
What SNOMED CT codes does D84.89 map to?
D84.89 maps to 73 SNOMED CT concepts: 711480000, 719685004, 735536003, 784393004, 234642007, and 68 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D84.89?
D84.89 is linked to 1 UMLS Concept Unique Identifier: C0494264. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.