D80.5
BillableImmunodeficiency with increased immunoglobulin M [IgM]
Immunodeficiency with increased immunoglobulin M [IgM]
Coding Notes
Includes
Conditions included under this code
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Also Known As / Clinical Terms
SNOMED CT
- Hyper IgM syndrome82286005
- Hyperimmunoglobulin M syndrome82286005
- Immunodeficiency with IgM hypergammaglobulinaemia82286005
- Immunodeficiency with IgM hypergammaglobulinemia82286005
- Hyper-IgM syndrome due to CD40 ligand deficiency403835002
- Hyper-IgM syndrome due to CD40L deficiency403835002
- Hyper-IgM syndrome type 1403835002
- X-linked hyper-IgM syndrome403835002
- X-linked hyper-immunoglobulin M syndrome403835002
- X-linked with hyper-IgM immunodeficiency403835002
- Autosomal recessive hyper- immunoglobulin M syndrome403836001
- Autosomal recessive hyper-IgM syndrome403836001
- Autosomal recessive hyperimmunoglobulin M syndrome403836001
- CMMR-D (constitutional mismatch repair deficiency) syndrome764946008
- Constitutional mismatch repair deficiency syndrome764946008
- Hyper-IgM syndrome with susceptibility to opportunistic infections783248004
- Hyperimmunoglobulin M syndrome with susceptibility to opportunistic infection783248004
- Hyper-IgM syndrome without susceptibility to opportunistic infections783249007
- Hyperimmunoglobulin M syndrome without susceptibility to opportunistic infection783249007
- Autosomal recessive hyperimmunoglobulin M syndrome due to UNG deficiency1351569004
- Autosomal recessive hyperimmunoglobulin M syndrome due to uracil DNA glycosylase deficiency1351569004
- Hyper-IgM syndrome due to UNG1351569004
- Hyper-IgM syndrome due to uracil N-glycosylase1351569004
- Hyper-IgM syndrome type 51351569004
- Autosomal dominant activation-induced cytidine deaminase deficiency1351570003
- Autosomal dominant hyper IgM syndrome due to AICDA1351570003
- Autosomal dominant hyper-IgM syndrome type 21351570003
- Autosomal dominant hyperimmunoglobulin M syndrome due to AID deficiency1351570003
- Autosomal dominant hyperimmunoglobulin M syndrome due to activation induced cytidine deaminase deficiency1351570003
- Autosomal recessive activation-induced cytidine deaminase deficiency1351572006
- Autosomal recessive hyper IgM syndrome due to AICDA1351572006
- Autosomal recessive hyper-IgM syndrome type 21351572006
- Autosomal recessive hyperimmunoglobulin M syndrome due to AID deficiency1351572006
- Autosomal recessive hyperimmunoglobulin M syndrome due to activation induced cytidine deaminase deficiency1351572006
- Autosomal recessive hyperimmunoglobulin M syndrome due to APRIL deficiency1351573001
- Hyper IgM syndrome due to TNFSF131351573001
- Autosomal recessive hyperimmunoglobulin M syndrome due to CTNNBL1 deficiency1351575008
- Autosomal recessive hyperimmunoglobulin M syndrome due to catenin beta like 1deficiency1351575008
- Hyper IgM syndrome due to CTNNBL11351575008
- Autosomal recessive hyperimmunoglobulin M syndrome due to MSH6 deficiency1351576009
- Autosomal recessive hyperimmunoglobulin M syndrome due to mutS homolog 6 deficiency1351576009
- Autosomal recessive hyperimmunoglobulin M syndrome due to mutator S homolog 6 deficiency1351576009
- Hyper IgM syndrome due to MSH61351576009
- Autosomal recessive hyperimmunoglobulin M syndrome due to INO80 complex ATPase subunit deficiency1351577000
- Autosomal recessive hyperimmunoglobulin M syndrome due to INO80 deficiency1351577000
- Hyper IgM syndrome due to INO801351577000
- Autosomal recessive combined immunodeficiency due to CD40 mutation1362020006
- HIGM3 - hyperimmunoglobulin M syndrome type 31362020006
- Hyper-IgM syndrome due to CD40 deficiency1362020006
- Hyperimmunoglobulin M syndrome type 31362020006
Frequently Asked Questions
What is ICD-10 code D80.5?
ICD-10-CM code D80.5 represents "Immunodeficiency with increased immunoglobulin M [IgM]". It is a billable/specific code that can be used on a claim.
Is D80.5 a billable code?
Yes, D80.5 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D80.5 in?
D80.5 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D80.5?
D80.5 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20).
What SNOMED CT codes does D80.5 map to?
D80.5 maps to 14 SNOMED CT concepts: 1351570003, 1351572006, 1362020006, 403836001, 1351573001, and 9 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D80.5?
D80.5 is linked to 1 UMLS Concept Unique Identifier: C0740331. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.