D76.3
BillableOther histiocytosis syndromes
Other histiocytosis syndromes
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Reticulohistiocytoma (giant-cell)
- Sinus histiocytosis with massive lymphadenopathy
- Xanthogranuloma
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- (Abt-) Letterer-Siwe disease (C96.0)
- eosinophilic granuloma (C96.6)
- Hand-Schüller-Christian disease (C96.5)
- histiocytic medullary reticulosis (C96.9)
- histiocytic sarcoma (C96.A)
- histiocytosis X, multifocal (C96.5)
- histiocytosis X, unifocal (C96.6)
- Langerhans-cell histiocytosis, multifocal (C96.5)
- Langerhans-cell histiocytosis NOS (C96.6)
- Langerhans-cell histiocytosis, unifocal (C96.6)
- leukemic reticuloendotheliosis (C91.4-)
- lipomelanotic reticulosis (I89.8)
- malignant histiocytosis (C96.A)
- malignant reticulosis (C86.0)
- nonlipid reticuloendotheliosis (C96.0)
Excludes 2
Conditions not included here, but the patient may have both
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Also Known As / Clinical Terms
SNOMED CT
- Mucinous histiocytosis of the colon6137007
- Retroperitoneal xanthogranuloma31124001
- Rosai-Dorfman disease34287003
- Rosai-Dorfman-Destombes disease34287003
- Sinus histiocytosis with massive lymphadenopathy34287003
- Sea-blue histiocyte syndrome37821003
- Sea-blue histiocytosis37821003
- Histiocytic syndrome127068004
- Histiocytosis127068004
- Xanthogranuloma189099001
- SEX - Solitary eruptive xanthogranuloma254751002
- Solitary eruptive xanthogranuloma254751002
- Juvenile xanthogranuloma of iris255013004
- Benign cephalic histiocytosis255192005
- Papular histiocytosis of head255192005
- Congenital xanthoma tuberosum400031009
- JXG - Juvenile xanthogranuloma400031009
- Juvenile giant cell granuloma400031009
- Juvenile xanthogranuloma400031009
- Juvenile xanthoma400031009
- Naevoxanthoendothelioma400031009
- Nevoxanthoendothelioma400031009
- Xanthoma multiplex400031009
- Xanthoma naeviforme400031009
- Xanthoma neviforme400031009
- Multiple eruptive juvenile xanthogranuloma400204000
- Multiple eruptive xanthoma in infancy400204000
- Panniculitis secondary to histiocytic disorder402691004
- Non-Langerhans cell histiocytic dermatosis402883006
- Cutaneous reticulohistiocytosis404161006
- Giant cell histiocytoma404162004
- Reticulohistiocytic granuloma404162004
- Solitary reticulohistiocytoma404162004
- Necrobiotic xanthogranuloma404164003
- Necrobiotic xanthogranuloma with paraproteinaemia404165002
- Necrobiotic xanthogranuloma with paraproteinemia404165002
- Malakoplakia (involving skin)404167005
- Undetermined cell histiocytosis404168000
- Juvenile xanthogranuloma of skin414552005
- Subcutaneous xanthogranulomatosis447032001
- Erdheim-Chester disease699537002
- Erdheim-Chester syndrome699537002
- Polyostotic sclerosing histiocytosis699537002
- Xanthogranuloma of choroid plexus699813007
- Periodontitis due to histiocytosis syndrome710096000
- H syndrome711159002
- Histiocytosis-lymphadenopathy plus syndrome711159002
- SLC29A3 spectrum disorder711159002
- Malakoplakia716766007
- Dermal dendritic cell histiocytosis733205009
- Histiocytosis class IIa733205009
- Progressive nodular histiocytosis765141005
- Hereditary progressive mucinous histiocytosis771300001
- Chronic histiocytosis14931000119109
UMLS
- Destombes Rosai Dorfman SyndromeC5848165
- Destombes-Rosai-Dorfman DiseaseC5848165
- Destombes-Rosai-Dorfman SyndromeC5848165
- Disease, Rosai-DorfmanC5848165
- Histiocytoses, SinusC5848165
- Histiocytosis, SinusC5848165
- RDDC5848165
- RDD - Rosai-Dorfman diseaseC5848165
- ROSAI DORFMAN DISC5848165
- Rosai Dorfman DiseaseC5848165
- Rosai-Dorfman DiseaseC5848165
- Rosai-Dorfman diseaseC5848165
- Rosai-Dorfman disease (disorder)C5848165
- Rosai-Dorfman disease (morphologic abnormality)C5848165
- Rosai-Dorfman syndromeC5848165
- Rosai-Dorfman-Destombes DiseaseC5848165
- Rosai-Dorfman-Destombes diseaseC5848165
- SHMLC5848165
- Sinus HistiocytosesC5848165
- Sinus HistiocytosisC5848165
- Sinus Histiocytosis with Massive LymphadenopathyC5848165
- Sinus histiocytosis with massive lymphadenopathyC5848165
- Syndrome, Destombes-Rosai-DorfmanC5848165
- destombes-rosai-dorfman syndromeC5848165
- disease rosai-dorfmanC5848165
- histiocytosis sinusC5848165
- rosai dorfman diseaseC5848165
- rosai-dorfman diseaseC5848165
- sinus histiocytosisC5848165
- Other histiocytosis syndromesC0477320
- Reactive XanthogranulomaC5234857
- XanthogranulomaC5234857
- Xanthogranuloma (disorder)C5234857
- Xanthogranuloma (morphologic abnormality)C5234857
- Reticulohistiocytoma (giant-cell)C2873826
Frequently Asked Questions
What is ICD-10 code D76.3?
ICD-10-CM code D76.3 represents "Other histiocytosis syndromes". It is a billable/specific code that can be used on a claim.
Is D76.3 a billable code?
Yes, D76.3 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D76.3 in?
D76.3 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D76.3?
D76.3 has Excludes1 notes indicating codes that cannot be used together with it, including: (Abt-) Letterer-Siwe disease (C96.0); eosinophilic granuloma (C96.6); Hand-Schüller-Christian disease (C96.5); and 12 more.
What SNOMED CT codes does D76.3 map to?
D76.3 maps to 30 SNOMED CT concepts: 255192005, 14931000119109, 400031009, 404161006, 733205009, and 25 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D76.3?
D76.3 is linked to 4 UMLS Concept Unique Identifiers: C5848165, C0477320, C5234857, C2873826. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.